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23. Experimental phenylketonuria: replacement of carboxyl terminal tyrosine by phenylalanine in infant rat brain tubulin. Rodriguez JA; Borisy GG Science; 1979 Oct; 206(4417):463-5. PubMed ID: 574315 [TBL] [Abstract][Full Text] [Related]
24. Free amino acid pool in the brain of mice homozygous for the gene "dilute lethal". Simler S; Essayag S; Ledig M; Koehl C; Mandel P J Neurosci Res; 1977; 3(4):281-7. PubMed ID: 566796 [TBL] [Abstract][Full Text] [Related]
25. Behavioral and biochemical correlates of diet change in phenylketonuria. Anderson VE; Siegel FS Pediatr Res; 1976 Jan; 10(1):10-7. PubMed ID: 1246460 [TBL] [Abstract][Full Text] [Related]
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29. PKU is a reversible neurodegenerative process within the nigrostriatum that begins as early as 4 weeks of age in Pah(enu2) mice. Embury JE; Charron CE; Martynyuk A; Zori AG; Liu B; Ali SF; Rowland NE; Laipis PJ Brain Res; 2007 Jan; 1127(1):136-50. PubMed ID: 17112485 [TBL] [Abstract][Full Text] [Related]
30. Event-related potential correlates of selective processing in early- and continuously-treated children with phenylketonuria: effects of concurrent phenylalanine level and dietary control. de Sonneville LM; Huijbregts SC; van Spronsen FJ; Verkerk PH; Sergeant JA; Licht R Mol Genet Metab; 2010; 99 Suppl 1():S10-7. PubMed ID: 20123462 [TBL] [Abstract][Full Text] [Related]
31. Brain imaging and proton magnetic resonance spectroscopy in patients with phenylketonuria. Möller HE; Weglage J; Bick U; Wiedermann D; Feldmann R; Ullrich K Pediatrics; 2003 Dec; 112(6 Pt 2):1580-3. PubMed ID: 14654669 [TBL] [Abstract][Full Text] [Related]
32. Long-term correction of hyperphenylalaninemia by AAV-mediated gene transfer leads to behavioral recovery in phenylketonuria mice. Mochizuki S; Mizukami H; Ogura T; Kure S; Ichinohe A; Kojima K; Matsubara Y; Kobayahi E; Okada T; Hoshika A; Ozawa K; Kume A Gene Ther; 2004 Jul; 11(13):1081-6. PubMed ID: 15057263 [TBL] [Abstract][Full Text] [Related]
33. Cognitive profile of rats exposed to lactational hyperphenylalaninemia: correspondence with human mental retardation. Strupp BJ; Himmelstein S; Bunsey M; Levitsky DA; Kesler M Dev Psychobiol; 1990 Apr; 23(3):195-214. PubMed ID: 2379759 [TBL] [Abstract][Full Text] [Related]
34. Brain phenylalanine concentrations in phenylketonuria: research and treatment of adults. Moats RA; Moseley KD; Koch R; Nelson M Pediatrics; 2003 Dec; 112(6 Pt 2):1575-9. PubMed ID: 14654668 [TBL] [Abstract][Full Text] [Related]
35. [Brain sulfatides and cerebrosides in experimental hyperphenylalaninemia]. Chaeva LS Vopr Med Khim; 1977; 23(5):646-9. PubMed ID: 563642 [TBL] [Abstract][Full Text] [Related]
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38. Cerebral glycine content and phosphoserine phosphatase activity in hyperaminoacidemias. McChesney R; Isaacs CE; Greengard O Neurochem Res; 1987 Mar; 12(3):289-95. PubMed ID: 3035402 [TBL] [Abstract][Full Text] [Related]
39. Amino acid depletion in the blood and brain tissue of hyperphenylalaninemic rats is abolished by the administration of additional lysine: a contribution to the understanding of the metabolic defects in phenylketonuria. Huether G; Kaus R; Neuhoff V Biochem Med; 1985 Jun; 33(3):334-41. PubMed ID: 3925942 [TBL] [Abstract][Full Text] [Related]