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3. Lesch-Nyhan syndrome: mRNA expression of HPRT in patients with enzyme proven deficiency of HPRT and normal HPRT coding region of the DNA. Nguyen KV; Naviaux RK; Paik KK; Nyhan WL Mol Genet Metab; 2012 Aug; 106(4):498-501. PubMed ID: 22766437 [TBL] [Abstract][Full Text] [Related]
4. Amphetamine-induced behavioral phenotype in a hypoxanthine-guanine phosphoribosyltransferase-deficient mouse model of Lesch-Nyhan syndrome. Jinnah HA; Gage FH; Friedmann T Behav Neurosci; 1991 Dec; 105(6):1004-12. PubMed ID: 1777100 [TBL] [Abstract][Full Text] [Related]
9. Hypoxanthine-guanine phosphoribosyltransferase deficiency in a patient with a Madrid II mutation. Sapag A; Frischling E; Laborde H Joint Bone Spine; 2013 Jan; 80(1):93-5. PubMed ID: 22999896 [TBL] [Abstract][Full Text] [Related]
10. HPRT deficiency in a two-month-old child presenting acute renal failure and gout with a new deletion of two bases in exon 3 of the HPRT gene. Zamora A; Escárcega RO; Vazquez R; Zamora A; O'Neill JP Arch Med Res; 2007 May; 38(4):460-2. PubMed ID: 17416296 [TBL] [Abstract][Full Text] [Related]
11. Lesch Nyhan syndrome: a novel complex mutation in a Tunisian child. Rebai I; Kraoua I; Benrhouma H; Rouissi A; Turki I; Ceballos-Picot I; Gouider-Khouja N Brain Dev; 2014 Nov; 36(10):921-3. PubMed ID: 24503445 [TBL] [Abstract][Full Text] [Related]
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13. The spectrum of hypoxanthine-guanine phosphoribosyltransferase (HPRT) deficiency. Clinical experience based on 22 patients from 18 Spanish families. Puig JG; Torres RJ; Mateos FA; Ramos TH; Arcas JM; Buño AS; O'Neill P Medicine (Baltimore); 2001 Mar; 80(2):102-12. PubMed ID: 11307586 [TBL] [Abstract][Full Text] [Related]
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15. Lesch-Nyhan syndrome due to a single nucleotide change in the hypoxanthine-guanine phosphoribosyltransferase gene (HPRTYale). Fujimori S; Davidson BL; Kelley WN; Palella TD Adv Exp Med Biol; 1989; 253A():135-8. PubMed ID: 2624182 [TBL] [Abstract][Full Text] [Related]
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18. Production of a model for Lesch-Nyhan syndrome in hypoxanthine phosphoribosyltransferase-deficient mice. Wu CL; Melton DW Nat Genet; 1993 Mar; 3(3):235-40. PubMed ID: 8485579 [TBL] [Abstract][Full Text] [Related]
20. Lesch-Nyhan syndrome and HPRT variants: study of heterogeneity at the gene level. Singh S; Willers I; Held K; Goedde W Adv Exp Med Biol; 1989; 253A():145-50. PubMed ID: 2624184 [No Abstract] [Full Text] [Related] [Next] [New Search]