186 related articles for article (PubMed ID: 26526358)
1. A small molecule neutrophil elastase inhibitor, KRP-109, inhibits cystic fibrosis mucin degradation.
Chillappagari S; Müller C; Mahavadi P; Guenther A; Nährlich L; Rosenblum J; Rubin BK; Henke MO
J Cyst Fibros; 2016 May; 15(3):325-31. PubMed ID: 26526358
[TBL] [Abstract][Full Text] [Related]
2. Altered protease and antiprotease balance during a COPD exacerbation contributes to mucus obstruction.
Chillappagari S; Preuss J; Licht S; Müller C; Mahavadi P; Sarode G; Vogelmeier C; Guenther A; Nahrlich L; Rubin BK; Henke MO
Respir Res; 2015 Jul; 16(1):85. PubMed ID: 26169056
[TBL] [Abstract][Full Text] [Related]
3. Neutrophil elastase correlates with increased sphingolipid content in cystic fibrosis sputum.
Karandashova S; Kummarapurugu A; Zheng S; Kang L; Sun S; Rubin BK; Voynow JA
Pediatr Pulmonol; 2018 Jul; 53(7):872-880. PubMed ID: 29624923
[TBL] [Abstract][Full Text] [Related]
4. Prolastin aerosol therapy and sputum taurine in cystic fibrosis.
Cantin AM; Berthiaume Y; Cloutier D; Martel M
Clin Invest Med; 2006 Aug; 29(4):201-7. PubMed ID: 16986483
[TBL] [Abstract][Full Text] [Related]
5. Inhibition of neutrophil elastase in CF sputum by L-658,758.
Rees DD; Brain JD; Wohl ME; Humes JL; Mumford RA
J Pharmacol Exp Ther; 1997 Dec; 283(3):1201-6. PubMed ID: 9399994
[TBL] [Abstract][Full Text] [Related]
6. Elafin, an elastase-specific inhibitor, is cleaved by its cognate enzyme neutrophil elastase in sputum from individuals with cystic fibrosis.
Guyot N; Butler MW; McNally P; Weldon S; Greene CM; Levine RL; O'Neill SJ; Taggart CC; McElvaney NG
J Biol Chem; 2008 Nov; 283(47):32377-85. PubMed ID: 18799464
[TBL] [Abstract][Full Text] [Related]
7. Cystic fibrosis airway secretions exhibit mucin hyperconcentration and increased osmotic pressure.
Henderson AG; Ehre C; Button B; Abdullah LH; Cai LH; Leigh MW; DeMaria GC; Matsui H; Donaldson SH; Davis CW; Sheehan JK; Boucher RC; Kesimer M
J Clin Invest; 2014 Jul; 124(7):3047-60. PubMed ID: 24892808
[TBL] [Abstract][Full Text] [Related]
8. Aerosolized prolastin suppresses bacterial proliferation in a model of chronic Pseudomonas aeruginosa lung infection.
Cantin AM; Woods DE
Am J Respir Crit Care Med; 1999 Oct; 160(4):1130-5. PubMed ID: 10508798
[TBL] [Abstract][Full Text] [Related]
9. Lack of neutrophil elastase reduces inflammation, mucus hypersecretion, and emphysema, but not mucus obstruction, in mice with cystic fibrosis-like lung disease.
Gehrig S; Duerr J; Weitnauer M; Wagner CJ; Graeber SY; Schatterny J; Hirtz S; Belaaouaj A; Dalpke AH; Schultz C; Mall MA
Am J Respir Crit Care Med; 2014 May; 189(9):1082-92. PubMed ID: 24678594
[TBL] [Abstract][Full Text] [Related]
10. Evidence for the in vivo degradation of human respiratory mucins during Pseudomonas aeruginosa infection.
Houdret N; Ramphal R; Scharfman A; Perini JM; Filliat M; Lamblin G; Roussel P
Biochim Biophys Acta; 1989 Jul; 992(1):96-105. PubMed ID: 2752044
[TBL] [Abstract][Full Text] [Related]
11. Desulfurization of mucin by Pseudomonas aeruginosa: influence of sulfate in the lungs of cystic fibrosis patients.
Robinson CV; Elkins MR; Bialkowski KM; Thornton DJ; Kertesz MA
J Med Microbiol; 2012 Dec; 61(Pt 12):1644-1653. PubMed ID: 22918866
[TBL] [Abstract][Full Text] [Related]
12. Alpha 1-proteinase inhibitor abrogates proteolytic and secretagogue activity of cystic fibrosis sputum.
Hansen G; Schuster A; Zubrod C; Wahn V
Respiration; 1995; 62(3):117-24. PubMed ID: 7569330
[TBL] [Abstract][Full Text] [Related]
13. Molecular principles for heparin oligosaccharide-based inhibition of neutrophil elastase in cystic fibrosis.
Kummarapurugu AB; Afosah DK; Sankaranarayanan NV; Navaz Gangji R; Zheng S; Kennedy T; Rubin BK; Voynow JA; Desai UR
J Biol Chem; 2018 Aug; 293(32):12480-12490. PubMed ID: 29903912
[TBL] [Abstract][Full Text] [Related]
14. Serine proteases degrade airway mucins in cystic fibrosis.
Henke MO; John G; Rheineck C; Chillappagari S; Naehrlich L; Rubin BK
Infect Immun; 2011 Aug; 79(8):3438-44. PubMed ID: 21646446
[TBL] [Abstract][Full Text] [Related]
15. Neutrophil elastase-mediated increase in airway temperature during inflammation.
Schmidt A; Belaaouaj A; Bissinger R; Koller G; Malleret L; D'Orazio C; Facchinelli M; Schulte-Hubbert B; Molinaro A; Holst O; Hammermann J; Schniederjans M; Meyer KC; Damkiaer S; Piacentini G; Assael B; Bruce K; Häußler S; LiPuma JJ; Seelig J; Worlitzsch D; Döring G
J Cyst Fibros; 2014 Dec; 13(6):623-31. PubMed ID: 24713593
[TBL] [Abstract][Full Text] [Related]
16. Host inflammatory responses to first isolation of Pseudomonas aeruginosa from sputum in cystic fibrosis.
Elborn JS; Cordon SM; Shale DJ
Pediatr Pulmonol; 1993 May; 15(5):287-91. PubMed ID: 8327287
[TBL] [Abstract][Full Text] [Related]
17. Evaluation of active neutrophil elastase in sputum of bronchiectasis and cystic fibrosis patients: A comparison among different techniques.
Oriano M; Terranova L; Sotgiu G; Saderi L; Bellofiore A; Retucci M; Marotta C; Gramegna A; Miglietta D; Carnini C; Marchisio P; Chalmers JD; Aliberti S; Blasi F
Pulm Pharmacol Ther; 2019 Dec; 59():101856. PubMed ID: 31626976
[TBL] [Abstract][Full Text] [Related]
18. NET formation induced by Pseudomonas aeruginosa cystic fibrosis isolates measured as release of myeloperoxidase-DNA and neutrophil elastase-DNA complexes.
Yoo DG; Floyd M; Winn M; Moskowitz SM; Rada B
Immunol Lett; 2014 Aug; 160(2):186-94. PubMed ID: 24670966
[TBL] [Abstract][Full Text] [Related]
19. Aerosol treatment with MNEI suppresses bacterial proliferation in a model of chronic Pseudomonas aeruginosa lung infection.
Woods DE; Cantin A; Cooley J; Kenney DM; Remold-O'Donnell E
Pediatr Pulmonol; 2005 Feb; 39(2):141-9. PubMed ID: 15633200
[TBL] [Abstract][Full Text] [Related]
20. Effect of recombinant human DNase on alpha1-proteinase inhibitor function: an experimental approach to the combined clinical use of rhDNase and alpha1-PI in CF patients.
Hansen G; Hoffjan S; Mosler K; Schuster A
Lung; 2001; 179(3):185-94. PubMed ID: 11891608
[TBL] [Abstract][Full Text] [Related]
[Next] [New Search]