397 related articles for article (PubMed ID: 27026396)
1. New insights into the structure, assembly and biological roles of 10-12 nm connective tissue microfibrils from fibrillin-1 studies.
Jensen SA; Handford PA
Biochem J; 2016 Apr; 473(7):827-38. PubMed ID: 27026396
[TBL] [Abstract][Full Text] [Related]
2. A microfibril assembly assay identifies different mechanisms of dominance underlying Marfan syndrome, stiff skin syndrome and acromelic dysplasias.
Jensen SA; Iqbal S; Bulsiewicz A; Handford PA
Hum Mol Genet; 2015 Aug; 24(15):4454-63. PubMed ID: 25979247
[TBL] [Abstract][Full Text] [Related]
3. Microfibrils: a cornerstone of extracellular matrix and a key to understand Marfan syndrome.
Bonetti MI
Ital J Anat Embryol; 2009; 114(4):201-24. PubMed ID: 20578676
[TBL] [Abstract][Full Text] [Related]
4. Fibrillin-rich microfibrils: Structural determinants of morphogenetic and homeostatic events.
Ramirez F; Dietz HC
J Cell Physiol; 2007 Nov; 213(2):326-30. PubMed ID: 17708531
[TBL] [Abstract][Full Text] [Related]
5. Fibrillin in Marfan syndrome and tight skin mice provides new insights into transforming growth factor-beta regulation and systemic sclerosis.
Lemaire R; Bayle J; Lafyatis R
Curr Opin Rheumatol; 2006 Nov; 18(6):582-7. PubMed ID: 17053502
[TBL] [Abstract][Full Text] [Related]
6. Basic components of connective tissues and extracellular matrix: elastin, fibrillin, fibulins, fibrinogen, fibronectin, laminin, tenascins and thrombospondins.
Halper J; Kjaer M
Adv Exp Med Biol; 2014; 802():31-47. PubMed ID: 24443019
[TBL] [Abstract][Full Text] [Related]
7. Basic Components of Connective Tissues and Extracellular Matrix: Fibronectin, Fibrinogen, Laminin, Elastin, Fibrillins, Fibulins, Matrilins, Tenascins and Thrombospondins.
Halper J
Adv Exp Med Biol; 2021; 1348():105-126. PubMed ID: 34807416
[TBL] [Abstract][Full Text] [Related]
8. Fell-Muir Lecture: Fibrillin microfibrils: structural tensometers of elastic tissues?
Kielty CM
Int J Exp Pathol; 2017 Aug; 98(4):172-190. PubMed ID: 28905442
[TBL] [Abstract][Full Text] [Related]
9. Adamtsl2 deletion results in bronchial fibrillin microfibril accumulation and bronchial epithelial dysplasia--a novel mouse model providing insights into geleophysic dysplasia.
Hubmacher D; Wang LW; Mecham RP; Reinhardt DP; Apte SS
Dis Model Mech; 2015 May; 8(5):487-99. PubMed ID: 25762570
[TBL] [Abstract][Full Text] [Related]
10. The fibrillin microfibril scaffold: A niche for growth factors and mechanosensation?
Sengle G; Sakai LY
Matrix Biol; 2015 Sep; 47():3-12. PubMed ID: 25957947
[TBL] [Abstract][Full Text] [Related]
11. Genetic and functional linkage between ADAMTS superfamily proteins and fibrillin-1: a novel mechanism influencing microfibril assembly and function.
Hubmacher D; Apte SS
Cell Mol Life Sci; 2011 Oct; 68(19):3137-48. PubMed ID: 21858451
[TBL] [Abstract][Full Text] [Related]
12. Mutations in the human gene for fibrillin-1 (FBN1) in the Marfan syndrome and related disorders.
Dietz HC; Pyeritz RE
Hum Mol Genet; 1995; 4 Spec No():1799-809. PubMed ID: 8541880
[TBL] [Abstract][Full Text] [Related]
13. Microenvironmental regulation by fibrillin-1.
Sengle G; Tsutsui K; Keene DR; Tufa SF; Carlson EJ; Charbonneau NL; Ono RN; Sasaki T; Wirtz MK; Samples JR; Fessler LI; Fessler JH; Sekiguchi K; Hayflick SJ; Sakai LY
PLoS Genet; 2012 Jan; 8(1):e1002425. PubMed ID: 22242013
[TBL] [Abstract][Full Text] [Related]
14. ADAMTSL6β protein rescues fibrillin-1 microfibril disorder in a Marfan syndrome mouse model through the promotion of fibrillin-1 assembly.
Saito M; Kurokawa M; Oda M; Oshima M; Tsutsui K; Kosaka K; Nakao K; Ogawa M; Manabe RI; Suda N; Ganjargal G; Hada Y; Noguchi T; Teranaka T; Sekiguchi K; Yoneda T; Tsuji T
J Biol Chem; 2011 Nov; 286(44):38602-38613. PubMed ID: 21880733
[TBL] [Abstract][Full Text] [Related]
15. In vivo studies of mutant fibrillin-1 microfibrils.
Charbonneau NL; Carlson EJ; Tufa S; Sengle G; Manalo EC; Carlberg VM; Ramirez F; Keene DR; Sakai LY
J Biol Chem; 2010 Aug; 285(32):24943-55. PubMed ID: 20529844
[TBL] [Abstract][Full Text] [Related]
16. Fibrillin-1, a calcium binding protein of extracellular matrix.
Handford PA
Biochim Biophys Acta; 2000 Dec; 1498(2-3):84-90. PubMed ID: 11108952
[TBL] [Abstract][Full Text] [Related]
17. The fibrillin-Marfan syndrome connection.
Ramirez F; Pereira L; Zhang H; Lee B
Bioessays; 1993 Sep; 15(9):589-94. PubMed ID: 8240311
[TBL] [Abstract][Full Text] [Related]
18. Fibrillin: from microfibril assembly to biomechanical function.
Kielty CM; Baldock C; Lee D; Rock MJ; Ashworth JL; Shuttleworth CA
Philos Trans R Soc Lond B Biol Sci; 2002 Feb; 357(1418):207-17. PubMed ID: 11911778
[TBL] [Abstract][Full Text] [Related]
19. Fibrillin microfibrils.
Kielty CM; Sherratt MJ; Marson A; Baldock C
Adv Protein Chem; 2005; 70():405-36. PubMed ID: 15837522
[TBL] [Abstract][Full Text] [Related]
20. Biogenesis and function of fibrillin assemblies.
Ramirez F; Sakai LY
Cell Tissue Res; 2010 Jan; 339(1):71-82. PubMed ID: 19513754
[TBL] [Abstract][Full Text] [Related]
[Next] [New Search]
