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2. Novel CNS malformations and skeletal anomalies in a patient with Beaulieu-boycott-Innes syndrome. Accogli A; Scala M; Calcagno A; Castello R; Torella A; Musacchia F; Allegri AME; Mancardi MM; Maghnie M; Severino M; ; Nigro V; Capra V Am J Med Genet A; 2018 Dec; 176(12):2835-2840. PubMed ID: 30238602 [TBL] [Abstract][Full Text] [Related]
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7. Biallelic THOC6 pathogenic variants: Prenatal phenotype and review of the literature. Ruaud L; Roux N; Boutaud L; Bessières B; Ageorges F; Achaiaa A; Bole C; Nitschke P; Masson C; Vekemans M; Verloes A; Attie-Bitach T Birth Defects Res; 2022 Jun; 114(10):499-504. PubMed ID: 35426486 [TBL] [Abstract][Full Text] [Related]
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9. Genotype-phenotype evaluation of MED13L defects in the light of a novel truncating and a recurrent missense mutation. Asadollahi R; Zweier M; Gogoll L; Schiffmann R; Sticht H; Steindl K; Rauch A Eur J Med Genet; 2017 Sep; 60(9):451-464. PubMed ID: 28645799 [TBL] [Abstract][Full Text] [Related]
10. The first reported case of Beaulieu-Boycott-Innes syndrome caused by two novel mutations in THOC6 gene in a Chinese infant. Zhang Q; Chen S; Qin Z; Zheng H; Fan X Medicine (Baltimore); 2020 Apr; 99(15):e19751. PubMed ID: 32282736 [TBL] [Abstract][Full Text] [Related]
11. Heterozygous mutations affecting the protein kinase domain of Hamilton MJ; Caswell RC; Canham N; Cole T; Firth HV; Foulds N; Heimdal K; Hobson E; Houge G; Joss S; Kumar D; Lampe AK; Maystadt I; McKay V; Metcalfe K; Newbury-Ecob R; Park SM; Robert L; Rustad CF; Wakeling E; Wilkie AOM; Study TDDD; Twigg SRF; Suri M J Med Genet; 2018 Jan; 55(1):28-38. PubMed ID: 29021403 [TBL] [Abstract][Full Text] [Related]
12. TREX tetramer disruption alters RNA processing necessary for corticogenesis in THOC6 Intellectual Disability Syndrome. Werren EA; LaForce GR; Srivastava A; Perillo DR; Li S; Johnson K; Baris S; Berger B; Regan SL; Pfennig CD; de Munnik S; Pfundt R; Hebbar M; Jimenez-Heredia R; Karakoc-Aydiner E; Ozen A; Dmytrus J; Krolo A; Corning K; Prijoles EJ; Louie RJ; Lebel RR; Le TL; Amiel J; Gordon CT; Boztug K; Girisha KM; Shukla A; Bielas SL; Schaffer AE Nat Commun; 2024 Feb; 15(1):1640. PubMed ID: 38388531 [TBL] [Abstract][Full Text] [Related]
13. Mutations in EXOSC2 are associated with a novel syndrome characterised by retinitis pigmentosa, progressive hearing loss, premature ageing, short stature, mild intellectual disability and distinctive gestalt. Di Donato N; Neuhann T; Kahlert AK; Klink B; Hackmann K; Neuhann I; Novotna B; Schallner J; Krause C; Glass IA; Parnell SE; Benet-Pages A; Nissen AM; Berger W; Altmüller J; Thiele H; Weber BH; Schrock E; Dobyns WB; Bier A; Rump A J Med Genet; 2016 Jun; 53(6):419-25. PubMed ID: 26843489 [TBL] [Abstract][Full Text] [Related]
14. Proteinuria in Two Sisters with Beaulieu-Boycott-Innes Syndrome, A Case Report. Hassanvand Amouzadeh M; Akhavan Sepahi M; Abasi E Iran J Kidney Dis; 2020 Jul; 14(4):312-314. PubMed ID: 32655027 [TBL] [Abstract][Full Text] [Related]
15. Missense variants in AIMP1 gene are implicated in autosomal recessive intellectual disability without neurodegeneration. Iqbal Z; Püttmann L; Musante L; Razzaq A; Zahoor MY; Hu H; Wienker TF; Garshasbi M; Fattahi Z; Gilissen C; Vissers LE; de Brouwer AP; Veltman JA; Pfundt R; Najmabadi H; Ropers HH; Riazuddin S; Kahrizi K; van Bokhoven H Eur J Hum Genet; 2016 Mar; 24(3):392-9. PubMed ID: 26173967 [TBL] [Abstract][Full Text] [Related]
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17. Eight further individuals with intellectual disability and epilepsy carrying bi-allelic CNTNAP2 aberrations allow delineation of the mutational and phenotypic spectrum. Smogavec M; Cleall A; Hoyer J; Lederer D; Nassogne MC; Palmer EE; Deprez M; Benoit V; Maystadt I; Noakes C; Leal A; Shaw M; Gecz J; Raymond L; Reis A; Shears D; Brockmann K; Zweier C J Med Genet; 2016 Dec; 53(12):820-827. PubMed ID: 27439707 [TBL] [Abstract][Full Text] [Related]
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19. SLC1A4 mutations cause a novel disorder of intellectual disability, progressive microcephaly, spasticity and thin corpus callosum. Heimer G; Marek-Yagel D; Eyal E; Barel O; Oz Levi D; Hoffmann C; Ruzzo EK; Ganelin-Cohen E; Lancet D; Pras E; Rechavi G; Nissenkorn A; Anikster Y; Goldstein DB; Ben Zeev B Clin Genet; 2015 Oct; 88(4):327-35. PubMed ID: 26138499 [TBL] [Abstract][Full Text] [Related]