405 related articles for article (PubMed ID: 27129098)
1. Frataxin and the molecular mechanism of mitochondrial iron-loading in Friedreich's ataxia.
Chiang S; Kovacevic Z; Sahni S; Lane DJ; Merlot AM; Kalinowski DS; Huang ML; Richardson DR
Clin Sci (Lond); 2016 Jun; 130(11):853-70. PubMed ID: 27129098
[TBL] [Abstract][Full Text] [Related]
2. Fixing frataxin: 'ironing out' the metabolic defect in Friedreich's ataxia.
Anzovino A; Lane DJ; Huang ML; Richardson DR
Br J Pharmacol; 2014 Apr; 171(8):2174-90. PubMed ID: 24138602
[TBL] [Abstract][Full Text] [Related]
3. Mitochondrial dysfunction in the neuro-degenerative and cardio-degenerative disease, Friedreich's ataxia.
Chiang S; Kalinowski DS; Jansson PJ; Richardson DR; Huang ML
Neurochem Int; 2018 Jul; 117():35-48. PubMed ID: 28782591
[TBL] [Abstract][Full Text] [Related]
4. The role of frataxin in fission yeast iron metabolism: implications for Friedreich's ataxia.
Wang Y; Wang Y; Marcus S; Busenlehner LS
Biochim Biophys Acta; 2014 Oct; 1840(10):3022-33. PubMed ID: 24997422
[TBL] [Abstract][Full Text] [Related]
5. Elucidation of the mechanism of mitochondrial iron loading in Friedreich's ataxia by analysis of a mouse mutant.
Huang ML; Becker EM; Whitnall M; Suryo Rahmanto Y; Ponka P; Richardson DR
Proc Natl Acad Sci U S A; 2009 Sep; 106(38):16381-6. PubMed ID: 19805308
[TBL] [Abstract][Full Text] [Related]
6. Changes in mitochondrial glutathione levels and protein thiol oxidation in ∆yfh1 yeast cells and the lymphoblasts of patients with Friedreich's ataxia.
Bulteau AL; Planamente S; Jornea L; Dur A; Lesuisse E; Camadro JM; Auchère F
Biochim Biophys Acta; 2012 Feb; 1822(2):212-25. PubMed ID: 22200491
[TBL] [Abstract][Full Text] [Related]
7. No changes in heme synthesis in human Friedreich´s ataxia erythroid progenitor cells.
Steinkellner H; Singh HN; Muckenthaler MU; Goldenberg H; Moganty RR; Scheiber-Mojdehkar B; Sturm B
Gene; 2017 Jul; 621():5-11. PubMed ID: 28412459
[TBL] [Abstract][Full Text] [Related]
8. Targeting lipid peroxidation and mitochondrial imbalance in Friedreich's ataxia.
Abeti R; Uzun E; Renganathan I; Honda T; Pook MA; Giunti P
Pharmacol Res; 2015 Sep; 99():344-50. PubMed ID: 26141703
[TBL] [Abstract][Full Text] [Related]
9. Glutathione-dependent redox status of frataxin-deficient cells in a yeast model of Friedreich's ataxia.
Auchère F; Santos R; Planamente S; Lesuisse E; Camadro JM
Hum Mol Genet; 2008 Sep; 17(18):2790-802. PubMed ID: 18562474
[TBL] [Abstract][Full Text] [Related]
10. Deferiprone and idebenone rescue frataxin depletion phenotypes in a Drosophila model of Friedreich's ataxia.
Soriano S; Llorens JV; Blanco-Sobero L; Gutiérrez L; Calap-Quintana P; Morales MP; Moltó MD; Martínez-Sebastián MJ
Gene; 2013 Jun; 521(2):274-81. PubMed ID: 23542074
[TBL] [Abstract][Full Text] [Related]
11. Iron-sulfur cluster synthesis, iron homeostasis and oxidative stress in Friedreich ataxia.
Vaubel RA; Isaya G
Mol Cell Neurosci; 2013 Jul; 55():50-61. PubMed ID: 22917739
[TBL] [Abstract][Full Text] [Related]
12. Deferiprone for the treatment of Friedreich's ataxia.
Pandolfo M; Hausmann L
J Neurochem; 2013 Aug; 126 Suppl 1():142-6. PubMed ID: 23859349
[TBL] [Abstract][Full Text] [Related]
13. Iron metabolism and mitochondrial abnormalities in Friedreich ataxia.
Pandolfo M
Blood Cells Mol Dis; 2002; 29(3):536-47; discussion 548-52. PubMed ID: 12547248
[TBL] [Abstract][Full Text] [Related]
14. Posttranslational regulation of mitochondrial frataxin and identification of compounds that increase frataxin levels in Friedreich's ataxia.
Hackett PT; Jia X; Li L; Ward DM
J Biol Chem; 2022 Jun; 298(6):101982. PubMed ID: 35472330
[TBL] [Abstract][Full Text] [Related]
15. The ins and outs of mitochondrial iron-loading: the metabolic defect in Friedreich's ataxia.
Richardson DR; Huang ML; Whitnall M; Becker EM; Ponka P; Suryo Rahmanto Y
J Mol Med (Berl); 2010 Apr; 88(4):323-9. PubMed ID: 19997898
[TBL] [Abstract][Full Text] [Related]
16. Ferroptosis as a Novel Therapeutic Target for Friedreich's Ataxia.
Cotticelli MG; Xia S; Lin D; Lee T; Terrab L; Wipf P; Huryn DM; Wilson RB
J Pharmacol Exp Ther; 2019 Apr; 369(1):47-54. PubMed ID: 30635474
[TBL] [Abstract][Full Text] [Related]
17. Quantitative proteomics in Friedreich's ataxia B-lymphocytes: A valuable approach to decipher the biochemical events responsible for pathogenesis.
Télot L; Rousseau E; Lesuisse E; Garcia C; Morlet B; Léger T; Camadro JM; Serre V
Biochim Biophys Acta Mol Basis Dis; 2018 Apr; 1864(4 Pt A):997-1009. PubMed ID: 29329987
[TBL] [Abstract][Full Text] [Related]
18. Friedreich's ataxia.
Alper G; Narayanan V
Pediatr Neurol; 2003 May; 28(5):335-41. PubMed ID: 12878293
[TBL] [Abstract][Full Text] [Related]
19. Adding a temporal dimension to the study of Friedreich's ataxia: the effect of frataxin overexpression in a human cell model.
Vannocci T; Notario Manzano R; Beccalli O; Bettegazzi B; Grohovaz F; Cinque G; de Riso A; Quaroni L; Codazzi F; Pastore A
Dis Model Mech; 2018 Jun; 11(6):. PubMed ID: 29794127
[TBL] [Abstract][Full Text] [Related]
20. Mitochondrial pathophysiology in Friedreich's ataxia.
González-Cabo P; Palau F
J Neurochem; 2013 Aug; 126 Suppl 1():53-64. PubMed ID: 23859341
[TBL] [Abstract][Full Text] [Related]
[Next] [New Search]
