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3. A fluorometric assay using 4-methylumbelliferyl alpha-L-iduronide for the estimation of alpha-L-iduronidase activity and the detection of Hurler and Scheie syndromes. Hopwood JJ; Muller V; Smithson A; Baggett N Clin Chim Acta; 1979 Mar; 92(2):257-65. PubMed ID: 114339 [TBL] [Abstract][Full Text] [Related]
4. Diagnostic enzymology of alpha-L-iduronidase with special reference to a sulphated disaccharide derived from heparin. Hopwood JJ; Muller V Clin Sci (Lond); 1982 Feb; 62(2):193-201. PubMed ID: 6895615 [TBL] [Abstract][Full Text] [Related]
5. Use of 4-trifluoromethylumbelliferyl-alpha-L-iduronide as a new substrate for detection of alpha-L-iduronidase deficiency in human tissues and for rapid prenatal diagnosis of Hurler disease. Tsvetkova IV; Karpova EA; Voznyi YV; Zolotukhina TV; Biryukov VV; Semyachkina AN J Inherit Metab Dis; 1991; 14(2):134-9. PubMed ID: 1909400 [TBL] [Abstract][Full Text] [Related]
6. Comparison of the substrate 4-methylumbelliferyl-alpha-l-iduronide with phenyl-alpha-L-iduronide for the diagnosis of Hurler's disease in cultured cells. Butterworth J; Broadhead DM J Inherit Metab Dis; 1980; 2(3):71-4. PubMed ID: 6796763 [TBL] [Abstract][Full Text] [Related]
7. [Use of 4-methylumbelliferryl-alpha-L-iduronide and 4-trifluoromethylumbelliferryl-alpha-L-iduronide for detecting alpha-L-iduronidase deficiencies in human tissue and for rapid prenatal diagnosis of Hurler disease]. Tsvetkova IV; Karpova EA; Voznyĭ IaV; Zolotukhina TV; Biriukov VB; Semiachkina AN Vopr Med Khim; 1991; 37(1):74-7. PubMed ID: 1907053 [TBL] [Abstract][Full Text] [Related]
8. alpha-L-iduronidase activity in leukocytes: diagnosis of homozygotes and heterozygotes of the Hurler syndrome. Omura K; Higami S; Tada K Eur J Pediatr; 1976 May; 122(2):103-5. PubMed ID: 817912 [TBL] [Abstract][Full Text] [Related]
9. Microtest for determination of alpha-L-iduronidase in plasma and leucocytes and its potential for diagnosing alpha-L-iduronidase deficiency. Den Tandt WR; Scharpe S; Giesberts M; Poorthuis BJ Lancet; 1984 Apr; 1(8380):794. PubMed ID: 6143109 [No Abstract] [Full Text] [Related]
10. The use of alpha-L-iduronidase activity determinations in leucocytes for the detection of Hurler and Scheie syndromes. Liem KO; Hooghwinkel GJ Clin Chim Acta; 1975 Apr; 60(2):259-62. PubMed ID: 805007 [No Abstract] [Full Text] [Related]
11. Properties of alpha-L-iduronidase in cultured skin fibroblasts from alpha-L-iduronidase-deficient patients. Fujibayashi S; Minami R; Ishikawa Y; Wagatsuma K; Nakao T; Tsugawa S Hum Genet; 1984; 65(3):268-72. PubMed ID: 6421718 [TBL] [Abstract][Full Text] [Related]
12. Fluorometric measurement of urinary alpha-L-iduronidase activity. Isemura M; Kosaka H; Ikenaka T; Kido R; Yoshimura T J Biochem; 1978 Sep; 84(3):627-32. PubMed ID: 102641 [TBL] [Abstract][Full Text] [Related]
13. Residual α-L-iduronidase activity in fibroblasts of mild to severe Mucopolysaccharidosis type I patients. Oussoren E; Keulemans J; van Diggelen OP; Oemardien LF; Timmermans RG; van der Ploeg AT; Ruijter GJ Mol Genet Metab; 2013 Aug; 109(4):377-81. PubMed ID: 23786846 [TBL] [Abstract][Full Text] [Related]
14. Simplied assay method of alpha-L-iduronidase activity in leukocytes for detection of Hurler syndrome and its carriers. Momoi T; Sudo M; Tanioka KI; Kushida H Clin Chim Acta; 1977 Dec; 81(3):311-3. PubMed ID: 411615 [No Abstract] [Full Text] [Related]
15. Human alpha-L-iduronidase. II. Comparative biochemical and immunologic properties of the purified low and high uptake forms. Schuchman EH; Guzman NA; Takada G; Desnick RJ Enzyme; 1984; 31(3):166-75. PubMed ID: 6734578 [TBL] [Abstract][Full Text] [Related]
16. [Fluorometric determination of alpha-L-iduronidase activity in leukocytes and blood plasma in Hurler's disease]. Gusina NB; Tsukerman GL Lab Delo; 1988; (7):46-9. PubMed ID: 2460681 [No Abstract] [Full Text] [Related]
18. Detection of mucopolysaccharidosis type I heterozygotes based on the biochemical characteristics of leukocyte alpha-L-iduronidase. Mandelli J; Wajner A; Pires RF; Giugliani R; Coelho JC Arch Med Res; 2002; 33(1):20-4. PubMed ID: 11825626 [TBL] [Abstract][Full Text] [Related]
19. Detection of mucopolysaccharidosis type I heterozygotes on the basis of the biochemical properties of plasma alpha-L-iduronidase. Mandelli J; Wajner A; Pires R; Giugliani R; Coelho JC Clin Chim Acta; 2001 Oct; 312(1-2):81-6. PubMed ID: 11580912 [TBL] [Abstract][Full Text] [Related]
20. The Hurler syndrome: detection of patients and heterozygotes using a microassay for alpha-L-iduronidase in fibroblasts. Kleijer WJ; Hensing-Wolffers GM; Thompson EJ; Niermeijer MF Clin Chim Acta; 1981 Oct; 116(1):47-54. PubMed ID: 6797759 [TBL] [Abstract][Full Text] [Related] [Next] [New Search]