203 related articles for article (PubMed ID: 27131785)
1. Loss of the mitochondrial protein-only ribonuclease P complex causes aberrant tRNA processing and lethality in Drosophila.
Sen A; Karasik A; Shanmuganathan A; Mirkovic E; Koutmos M; Cox RT
Nucleic Acids Res; 2016 Jul; 44(13):6409-22. PubMed ID: 27131785
[TBL] [Abstract][Full Text] [Related]
2. The MRPP1/MRPP2 complex is a tRNA-maturation platform in human mitochondria.
Reinhard L; Sridhara S; Hällberg BM
Nucleic Acids Res; 2017 Dec; 45(21):12469-12480. PubMed ID: 29040705
[TBL] [Abstract][Full Text] [Related]
3. Structural insight into the human mitochondrial tRNA purine N1-methyltransferase and ribonuclease P complexes.
Oerum S; Roovers M; Rambo RP; Kopec J; Bailey HJ; Fitzpatrick F; Newman JA; Newman WG; Amberger A; Zschocke J; Droogmans L; Oppermann U; Yue WW
J Biol Chem; 2018 Aug; 293(33):12862-12876. PubMed ID: 29880640
[TBL] [Abstract][Full Text] [Related]
4. Novel patient missense mutations in the HSD17B10 gene affect dehydrogenase and mitochondrial tRNA modification functions of the encoded protein.
Oerum S; Roovers M; Leichsenring M; Acquaviva-Bourdain C; Beermann F; Gemperle-Britschgi C; Fouilhoux A; Korwitz-Reichelt A; Bailey HJ; Droogmans L; Oppermann U; Sass JO; Yue WW
Biochim Biophys Acta Mol Basis Dis; 2017 Dec; 1863(12):3294-3302. PubMed ID: 28888424
[TBL] [Abstract][Full Text] [Related]
5. Bi-allelic variants in the mitochondrial RNase P subunit PRORP cause mitochondrial tRNA processing defects and pleiotropic multisystem presentations.
Hochberg I; Demain LAM; Richer J; Thompson K; Urquhart JE; Rea A; Pagarkar W; Rodríguez-Palmero A; Schlüter A; Verdura E; Pujol A; Quijada-Fraile P; Amberger A; Deutschmann AJ; Demetz S; Gillespie M; Belyantseva IA; McMillan HJ; Barzik M; Beaman GM; Motha R; Ng KY; O'Sullivan J; Williams SG; Bhaskar SS; Lawrence IR; Jenkinson EM; Zambonin JL; Blumenfeld Z; Yalonetsky S; Oerum S; Rossmanith W; ; Yue WW; Zschocke J; Munro KJ; Battersby BJ; Friedman TB; Taylor RW; O'Keefe RT; Newman WG
Am J Hum Genet; 2021 Nov; 108(11):2195-2204. PubMed ID: 34715011
[TBL] [Abstract][Full Text] [Related]
6. Loss of Individual Mitochondrial Ribonuclease P Complex Proteins Differentially Affects Mitochondrial tRNA Processing In Vivo.
Saoji M; Sen A; Cox RT
Int J Mol Sci; 2021 Jun; 22(11):. PubMed ID: 34199774
[TBL] [Abstract][Full Text] [Related]
7. Interplay between substrate recognition, 5' end tRNA processing and methylation activity of human mitochondrial RNase P.
Karasik A; Fierke CA; Koutmos M
RNA; 2019 Dec; 25(12):1646-1660. PubMed ID: 31455609
[TBL] [Abstract][Full Text] [Related]
8. Reduction of
Saoji M; Petersen CE; Sen A; Tripoli BA; Smyth JT; Cox RT
Front Cell Dev Biol; 2022; 10():788516. PubMed ID: 35663400
[TBL] [Abstract][Full Text] [Related]
9. Recessive Mutations in TRMT10C Cause Defects in Mitochondrial RNA Processing and Multiple Respiratory Chain Deficiencies.
Metodiev MD; Thompson K; Alston CL; Morris AAM; He L; Assouline Z; Rio M; Bahi-Buisson N; Pyle A; Griffin H; Siira S; Filipovska A; Munnich A; Chinnery PF; McFarland R; Rötig A; Taylor RW
Am J Hum Genet; 2016 May; 98(5):993-1000. PubMed ID: 27132592
[TBL] [Abstract][Full Text] [Related]
10. Mutation or knock-down of 17β-hydroxysteroid dehydrogenase type 10 cause loss of MRPP1 and impaired processing of mitochondrial heavy strand transcripts.
Deutschmann AJ; Amberger A; Zavadil C; Steinbeisser H; Mayr JA; Feichtinger RG; Oerum S; Yue WW; Zschocke J
Hum Mol Genet; 2014 Jul; 23(13):3618-28. PubMed ID: 24549042
[TBL] [Abstract][Full Text] [Related]
11. Involvement of human ELAC2 gene product in 3' end processing of mitochondrial tRNAs.
Brzezniak LK; Bijata M; Szczesny RJ; Stepien PP
RNA Biol; 2011; 8(4):616-26. PubMed ID: 21593607
[TBL] [Abstract][Full Text] [Related]
12. Molecular insights into HSD10 disease: impact of SDR5C1 mutations on the human mitochondrial RNase P complex.
Vilardo E; Rossmanith W
Nucleic Acids Res; 2015 May; 43(10):5112-9. PubMed ID: 25925575
[TBL] [Abstract][Full Text] [Related]
13. Cytonuclear Interactions in the Evolution of Animal Mitochondrial tRNA Metabolism.
Pett W; Lavrov DV
Genome Biol Evol; 2015 Jun; 7(8):2089-101. PubMed ID: 26116918
[TBL] [Abstract][Full Text] [Related]
14. RNA processing in human mitochondria.
Sanchez MI; Mercer TR; Davies SM; Shearwood AM; Nygård KK; Richman TR; Mattick JS; Rackham O; Filipovska A
Cell Cycle; 2011 Sep; 10(17):2904-16. PubMed ID: 21857155
[TBL] [Abstract][Full Text] [Related]
15. A novel HSD17B10 mutation impairing the activities of the mitochondrial RNase P complex causes X-linked intractable epilepsy and neurodevelopmental regression.
Falk MJ; Gai X; Shigematsu M; Vilardo E; Takase R; McCormick E; Christian T; Place E; Pierce EA; Consugar M; Gamper HB; Rossmanith W; Hou YM
RNA Biol; 2016 May; 13(5):477-85. PubMed ID: 26950678
[TBL] [Abstract][Full Text] [Related]
16. Of P and Z: mitochondrial tRNA processing enzymes.
Rossmanith W
Biochim Biophys Acta; 2012; 1819(9-10):1017-26. PubMed ID: 22137969
[TBL] [Abstract][Full Text] [Related]
17. Disease-associated mutations in mitochondrial precursor tRNAs affect binding, m1R9 methylation, and tRNA processing by mtRNase P.
Karasik A; Wilhelm CA; Fierke CA; Koutmos M
RNA; 2021 Apr; 27(4):420-432. PubMed ID: 33380464
[TBL] [Abstract][Full Text] [Related]
18. Structural basis for human mitochondrial tRNA maturation.
Meynier V; Hardwick SW; Catala M; Roske JJ; Oerum S; Chirgadze DY; Barraud P; Yue WW; Luisi BF; Tisné C
Nat Commun; 2024 Jun; 15(1):4683. PubMed ID: 38824131
[TBL] [Abstract][Full Text] [Related]
19. Structure of the nuclease subunit of human mitochondrial RNase P.
Reinhard L; Sridhara S; Hällberg BM
Nucleic Acids Res; 2015 Jun; 43(11):5664-72. PubMed ID: 25953853
[TBL] [Abstract][Full Text] [Related]
20. Drosophila RNase Z processes mitochondrial and nuclear pre-tRNA 3' ends in vivo.
Dubrovsky EB; Dubrovskaya VA; Levinger L; Schiffer S; Marchfelder A
Nucleic Acids Res; 2004; 32(1):255-62. PubMed ID: 14715923
[TBL] [Abstract][Full Text] [Related]
[Next] [New Search]
