These tools will no longer be maintained as of December 31, 2024. Archived website can be found here. PubMed4Hh GitHub repository can be found here. Contact NLM Customer Service if you have questions.
253 related articles for article (PubMed ID: 27812215)
1. Paradoxical Sensitivity to an Integrated Stress Response Blocking Mutation in Vanishing White Matter Cells. Sekine Y; Zyryanova A; Crespillo-Casado A; Amin-Wetzel N; Harding HP; Ron D PLoS One; 2016; 11(11):e0166278. PubMed ID: 27812215 [TBL] [Abstract][Full Text] [Related]
2. [Eukaryotic translation initiation factor 2B and leukoencephalopathy with vanishing white matter]. Pan YX; Wu Y; Niu ZP; Jiang YW Beijing Da Xue Xue Bao Yi Xue Ban; 2009 Oct; 41(5):608-10. PubMed ID: 19829687 [TBL] [Abstract][Full Text] [Related]
3. Vanishing white matter: deregulated integrated stress response as therapy target. Abbink TEM; Wisse LE; Jaku E; Thiecke MJ; Voltolini-González D; Fritsen H; Bobeldijk S; Ter Braak TJ; Polder E; Postma NL; Bugiani M; Struijs EA; Verheijen M; Straat N; van der Sluis S; Thomas AAM; Molenaar D; van der Knaap MS Ann Clin Transl Neurol; 2019 Aug; 6(8):1407-1422. PubMed ID: 31402619 [TBL] [Abstract][Full Text] [Related]
4. Different Eukaryotic Initiation Factor 2Bε Mutations Lead to Various Degrees of Intolerance to the Stress of Endoplasmic Reticulum in Oligodendrocytes. Chen N; Jiang YW; Hao HJ; Ban TT; Gao K; Zhang ZB; Wang JM; Wu Y Chin Med J (Engl); 2015 Jul; 128(13):1772-7. PubMed ID: 26112719 [TBL] [Abstract][Full Text] [Related]
5. ISRIB Blunts the Integrated Stress Response by Allosterically Antagonising the Inhibitory Effect of Phosphorylated eIF2 on eIF2B. Zyryanova AF; Kashiwagi K; Rato C; Harding HP; Crespillo-Casado A; Perera LA; Sakamoto A; Nishimoto M; Yonemochi M; Shirouzu M; Ito T; Ron D Mol Cell; 2021 Jan; 81(1):88-103.e6. PubMed ID: 33220178 [TBL] [Abstract][Full Text] [Related]
6. eIF2B: recent structural and functional insights into a key regulator of translation. Wortham NC; Proud CG Biochem Soc Trans; 2015 Dec; 43(6):1234-40. PubMed ID: 26614666 [TBL] [Abstract][Full Text] [Related]
9. Mutations linked to leukoencephalopathy with vanishing white matter impair the function of the eukaryotic initiation factor 2B complex in diverse ways. Li W; Wang X; Van Der Knaap MS; Proud CG Mol Cell Biol; 2004 Apr; 24(8):3295-306. PubMed ID: 15060152 [TBL] [Abstract][Full Text] [Related]
10. Isocaloric low protein diet in a mouse model for vanishing white matter does not impact ISR deregulation in brain, but reveals ISR deregulation in liver. Wisse LE; Visser D; Ter Braak TJ; Bakkali A; Struys EA; Morrison CD; van der Knaap MS; Abbink TEM Nutr Neurosci; 2022 Jun; 25(6):1219-1230. PubMed ID: 33236691 [No Abstract] [Full Text] [Related]
11. A yeast purification system for human translation initiation factors eIF2 and eIF2Bε and their use in the diagnosis of CACH/VWM disease. de Almeida RA; Fogli A; Gaillard M; Scheper GC; Boesflug-Tanguy O; Pavitt GD PLoS One; 2013; 8(1):e53958. PubMed ID: 23335982 [TBL] [Abstract][Full Text] [Related]
12. Biochemical effects of mutations in the gene encoding the alpha subunit of eukaryotic initiation factor (eIF) 2B associated with Vanishing White Matter disease. Wortham NC; Proud CG BMC Med Genet; 2015 Aug; 16():64. PubMed ID: 26285592 [TBL] [Abstract][Full Text] [Related]
13. eIF2B activator prevents neurological defects caused by a chronic integrated stress response. Wong YL; LeBon L; Basso AM; Kohlhaas KL; Nikkel AL; Robb HM; Donnelly-Roberts DL; Prakash J; Swensen AM; Rubinstein ND; Krishnan S; McAllister FE; Haste NV; O'Brien JJ; Roy M; Ireland A; Frost JM; Shi L; Riedmaier S; Martin K; Dart MJ; Sidrauski C Elife; 2019 Jan; 8():. PubMed ID: 30624206 [TBL] [Abstract][Full Text] [Related]
14. Mutations in each of the five subunits of translation initiation factor eIF2B can cause leukoencephalopathy with vanishing white matter. van der Knaap MS; Leegwater PA; Könst AA; Visser A; Naidu S; Oudejans CB; Schutgens RB; Pronk JC Ann Neurol; 2002 Feb; 51(2):264-70. PubMed ID: 11835386 [TBL] [Abstract][Full Text] [Related]
15. Vanishing white matter. van der Knaap MS; Bugiani M; Abbink TEM Handb Clin Neurol; 2024; 204():77-94. PubMed ID: 39322396 [TBL] [Abstract][Full Text] [Related]
16. Stress responses. Mutations in a translation initiation factor identify the target of a memory-enhancing compound. Sekine Y; Zyryanova A; Crespillo-Casado A; Fischer PM; Harding HP; Ron D Science; 2015 May; 348(6238):1027-30. PubMed ID: 25858979 [TBL] [Abstract][Full Text] [Related]
17. Mutations causing childhood ataxia with central nervous system hypomyelination reduce eukaryotic initiation factor 2B complex formation and activity. Richardson JP; Mohammad SS; Pavitt GD Mol Cell Biol; 2004 Mar; 24(6):2352-63. PubMed ID: 14993275 [TBL] [Abstract][Full Text] [Related]
18. The role of eIF2 phosphorylation in cell and organismal physiology: new roles for well-known actors. Wang X; Proud CG Biochem J; 2022 May; 479(10):1059-1082. PubMed ID: 35604373 [TBL] [Abstract][Full Text] [Related]
19. Glial pathology in a novel spontaneous mutant mouse of the Eif2b5 gene: a vanishing white matter disease model. Terumitsu-Tsujita M; Kitaura H; Miura I; Kiyama Y; Goto F; Muraki Y; Ominato S; Hara N; Simankova A; Bizen N; Kashiwagi K; Ito T; Toyoshima Y; Kakita A; Manabe T; Wakana S; Takebayashi H; Igarashi H J Neurochem; 2020 Jul; 154(1):25-40. PubMed ID: 31587290 [TBL] [Abstract][Full Text] [Related]
20. Severity of vanishing white matter disease does not correlate with deficits in eIF2B activity or the integrity of eIF2B complexes. Liu R; van der Lei HD; Wang X; Wortham NC; Tang H; van Berkel CG; Mufunde TA; Huang W; van der Knaap MS; Scheper GC; Proud CG Hum Mutat; 2011 Sep; 32(9):1036-45. PubMed ID: 21560189 [TBL] [Abstract][Full Text] [Related] [Next] [New Search]