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5. Differential protein structural disturbances and suppression of assembly partners produced by nonsense GABRG2 epilepsy mutations: implications for disease phenotypic heterogeneity. Wang J; Shen D; Xia G; Shen W; Macdonald RL; Xu D; Kang JQ Sci Rep; 2016 Oct; 6():35294. PubMed ID: 27762395 [TBL] [Abstract][Full Text] [Related]
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8. Synaptic clustering differences due to different GABRB3 mutations cause variable epilepsy syndromes. Shi YW; Zhang Q; Cai K; Poliquin S; Shen W; Winters N; Yi YH; Wang J; Hu N; Macdonald RL; Liao WP; Kang JQ Brain; 2019 Oct; 142(10):3028-3044. PubMed ID: 31435640 [TBL] [Abstract][Full Text] [Related]
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10. Exome sequencing reveals new causal mutations in children with epileptic encephalopathies. Veeramah KR; Johnstone L; Karafet TM; Wolf D; Sprissler R; Salogiannis J; Barth-Maron A; Greenberg ME; Stuhlmann T; Weinert S; Jentsch TJ; Pazzi M; Restifo LL; Talwar D; Erickson RP; Hammer MF Epilepsia; 2013 Jul; 54(7):1270-81. PubMed ID: 23647072 [TBL] [Abstract][Full Text] [Related]
11. Overexpressing wild-type γ2 subunits rescued the seizure phenotype in Gabrg2 Huang X; Zhou C; Tian M; Kang JQ; Shen W; Verdier K; Pimenta A; MacDonald RL Epilepsia; 2017 Aug; 58(8):1451-1461. PubMed ID: 28586508 [TBL] [Abstract][Full Text] [Related]
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13. A novel GABRG2 mutation, p.R136*, in a family with GEFS+ and extended phenotypes. Johnston AJ; Kang JQ; Shen W; Pickrell WO; Cushion TD; Davies JS; Baer K; Mullins JGL; Hammond CL; Chung SK; Thomas RH; White C; Smith PEM; Macdonald RL; Rees MI Neurobiol Dis; 2014 Apr; 64():131-141. PubMed ID: 24407264 [TBL] [Abstract][Full Text] [Related]
14. Molecular Pathogenic Basis for GABRG2 Mutations Associated With a Spectrum of Epilepsy Syndromes, From Generalized Absence Epilepsy to Dravet Syndrome. Kang JQ; Macdonald RL JAMA Neurol; 2016 Aug; 73(8):1009-16. PubMed ID: 27367160 [TBL] [Abstract][Full Text] [Related]
15. Molecular basis for and chemogenetic modulation of comorbidities in GABRG2-deficient epilepsies. Zhang CQ; McMahon B; Dong H; Warner T; Shen W; Gallagher M; Macdonald RL; Kang JQ Epilepsia; 2019 Jun; 60(6):1137-1149. PubMed ID: 31087664 [TBL] [Abstract][Full Text] [Related]
16. 4-Phenylbutyrate promoted wild-type γ-aminobutyric acid type A receptor trafficking, reduced endoplasmic reticulum stress, and mitigated seizures in Gabrg2 Shen W; Flamm C; Delahanty AJ; Casteel E; Biven M; DeLeeuw MB; Poliquin S; Nwosu G; Randhave K; Kang JQ Epilepsia; 2024 Jan; 65(1):204-217. PubMed ID: 37746768 [TBL] [Abstract][Full Text] [Related]
17. De novo variants in GABRA2 and GABRA5 alter receptor function and contribute to early-onset epilepsy. Butler KM; Moody OA; Schuler E; Coryell J; Alexander JJ; Jenkins A; Escayg A Brain; 2018 Aug; 141(8):2392-2405. PubMed ID: 29961870 [TBL] [Abstract][Full Text] [Related]
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20. Spectrum of GABAA receptor variants in epilepsy. Maljevic S; Møller RS; Reid CA; Pérez-Palma E; Lal D; May P; Lerche H Curr Opin Neurol; 2019 Apr; 32(2):183-190. PubMed ID: 30664068 [TBL] [Abstract][Full Text] [Related] [Next] [New Search]