424 related articles for article (PubMed ID: 28247063)
21. The accumulation of enzymatically inactive cuproenzymes is a CNS-specific phenomenon of the SOD1
Hilton JB; Kysenius K; White AR; Crouch PJ
Exp Neurol; 2018 Sep; 307():118-128. PubMed ID: 29906423
[TBL] [Abstract][Full Text] [Related]
22. SOD1 in neurotoxicity and its controversial roles in SOD1 mutation-negative ALS.
Hayashi Y; Homma K; Ichijo H
Adv Biol Regul; 2016 Jan; 60():95-104. PubMed ID: 26563614
[TBL] [Abstract][Full Text] [Related]
23. Misfolded SOD1 inclusions in patients with mutations in
Forsberg K; Graffmo K; Pakkenberg B; Weber M; Nielsen M; Marklund S; Brännström T; Andersen PM
J Neurol Neurosurg Psychiatry; 2019 Aug; 90(8):861-869. PubMed ID: 30992335
[TBL] [Abstract][Full Text] [Related]
24. The Timing and Extent of Motor Neuron Vulnerability in ALS Correlates with Accumulation of Misfolded SOD1 Protein in the Cortex and in the Spinal Cord.
Genc B; Gozutok O; Kocak N; Ozdinler PH
Cells; 2020 Feb; 9(2):. PubMed ID: 32098365
[TBL] [Abstract][Full Text] [Related]
25. HtrA2/Omi-immunoreactive intraneuronal inclusions in the anterior horn of patients with sporadic and Cu/Zn superoxide dismutase (SOD1) mutant amyotrophic lateral sclerosis.
Kawamoto Y; Ito H; Kobayashi Y; Suzuki Y; Akiguchi I; Fujimura H; Sakoda S; Kusaka H; Hirano A; Takahashi R
Neuropathol Appl Neurobiol; 2010 Jun; 36(4):331-44. PubMed ID: 20202124
[TBL] [Abstract][Full Text] [Related]
26. ERp57 is protective against mutant SOD1-induced cellular pathology in amyotrophic lateral sclerosis.
Parakh S; Jagaraj CJ; Vidal M; Ragagnin AMG; Perri ER; Konopka A; Toth RP; Galper J; Blair IP; Thomas CJ; Walker AK; Yang S; Spencer DM; Atkin JD
Hum Mol Genet; 2018 Apr; 27(8):1311-1331. PubMed ID: 29409023
[TBL] [Abstract][Full Text] [Related]
27. [Prion-like Properties of Misfolded Cu/Zn-superoxide Dismutase in Amyotrophic Lateral Sclerosis: Update and Perspectives].
Tokuda E; Marklund SL; Furukawa Y
Yakugaku Zasshi; 2019; 139(7):1015-1019. PubMed ID: 31257248
[TBL] [Abstract][Full Text] [Related]
28. Does wild-type Cu/Zn-superoxide dismutase have pathogenic roles in amyotrophic lateral sclerosis?
Furukawa Y; Tokuda E
Transl Neurodegener; 2020 Aug; 9(1):33. PubMed ID: 32811540
[TBL] [Abstract][Full Text] [Related]
29. Proteins that bind to misfolded mutant superoxide dismutase-1 in spinal cords from transgenic amyotrophic lateral sclerosis (ALS) model mice.
Zetterström P; Graffmo KS; Andersen PM; Brännström T; Marklund SL
J Biol Chem; 2011 Jun; 286(23):20130-6. PubMed ID: 21493711
[TBL] [Abstract][Full Text] [Related]
30. TNF receptor-associated factor 6 interacts with ALS-linked misfolded superoxide dismutase 1 and promotes aggregation.
Semmler S; Gagné M; Garg P; Pickles SR; Baudouin C; Hamon-Keromen E; Destroismaisons L; Khalfallah Y; Chaineau M; Caron E; Bayne AN; Trempe JF; Cashman NR; Star AT; Haqqani AS; Durcan TM; Meiering EM; Robertson J; Grandvaux N; Plotkin SS; McBride HM; Vande Velde C
J Biol Chem; 2020 Mar; 295(12):3808-3825. PubMed ID: 32029478
[TBL] [Abstract][Full Text] [Related]
31. Pathological TDP-43 distinguishes sporadic amyotrophic lateral sclerosis from amyotrophic lateral sclerosis with SOD1 mutations.
Mackenzie IR; Bigio EH; Ince PG; Geser F; Neumann M; Cairns NJ; Kwong LK; Forman MS; Ravits J; Stewart H; Eisen A; McClusky L; Kretzschmar HA; Monoranu CM; Highley JR; Kirby J; Siddique T; Shaw PJ; Lee VM; Trojanowski JQ
Ann Neurol; 2007 May; 61(5):427-34. PubMed ID: 17469116
[TBL] [Abstract][Full Text] [Related]
32. Identification of a misfolded region in superoxide dismutase 1 that is exposed in amyotrophic lateral sclerosis.
Rotunno MS; Auclair JR; Maniatis S; Shaffer SA; Agar J; Bosco DA
J Biol Chem; 2014 Oct; 289(41):28527-38. PubMed ID: 25164820
[TBL] [Abstract][Full Text] [Related]
33. Misfolded superoxide dismutase-1 in CSF from amyotrophic lateral sclerosis patients.
Zetterström P; Andersen PM; Brännström T; Marklund SL
J Neurochem; 2011 Apr; 117(1):91-9. PubMed ID: 21226712
[TBL] [Abstract][Full Text] [Related]
34. The molecular tweezer CLR01 inhibits aberrant superoxide dismutase 1 (SOD1) self-assembly
Malik R; Meng H; Wongkongkathep P; Corrales CI; Sepanj N; Atlasi RS; Klärner FG; Schrader T; Spencer MJ; Loo JA; Wiedau M; Bitan G
J Biol Chem; 2019 Mar; 294(10):3501-3513. PubMed ID: 30602569
[TBL] [Abstract][Full Text] [Related]
35. Targeting low levels of MIF expression as a potential therapeutic strategy for ALS.
Alfahel L; Gschwendtberger T; Kozareva V; Dumas L; Gibbs R; Kertser A; Baruch K; Zaccai S; Kahn J; Thau-Habermann N; Eggenschwiler R; Sterneckert J; Hermann A; Sundararaman N; Vaibhav V; Van Eyk JE; Rafuse VF; Fraenkel E; Cantz T; Petri S; Israelson A
Cell Rep Med; 2024 May; 5(5):101546. PubMed ID: 38703766
[TBL] [Abstract][Full Text] [Related]
36. SOD1-positive aggregate accumulation in the CNS predicts slower disease progression and increased longevity in a mutant SOD1 mouse model of ALS.
Gill C; Phelan JP; Hatzipetros T; Kidd JD; Tassinari VR; Levine B; Wang MZ; Moreno A; Thompson K; Maier M; Grimm J; Gill A; Vieira FG
Sci Rep; 2019 Apr; 9(1):6724. PubMed ID: 31040321
[TBL] [Abstract][Full Text] [Related]
37. Immunochemical characterization on pathological oligomers of mutant Cu/Zn-superoxide dismutase in amyotrophic lateral sclerosis.
Tokuda E; Anzai I; Nomura T; Toichi K; Watanabe M; Ohara S; Watanabe S; Yamanaka K; Morisaki Y; Misawa H; Furukawa Y
Mol Neurodegener; 2017 Jan; 12(1):2. PubMed ID: 28057013
[TBL] [Abstract][Full Text] [Related]
38. Overexpressed wild-type superoxide dismutase 1 exhibits amyotrophic lateral sclerosis-related misfolded conformation in induced pluripotent stem cell-derived spinal motor neurons.
Komatsu K; Imamura K; Yamashita H; Julien JP; Takahashi R; Inoue H
Neuroreport; 2018 Jan; 29(1):25-29. PubMed ID: 29140847
[TBL] [Abstract][Full Text] [Related]
39. Immunodetection of disease-associated conformers of mutant cu/zn superoxide dismutase 1 selectively expressed in degenerating neurons in amyotrophic lateral sclerosis.
Sábado J; Casanovas A; Hernández S; Piedrafita L; Hereu M; Esquerda JE
J Neuropathol Exp Neurol; 2013 Jul; 72(7):646-61. PubMed ID: 23771221
[TBL] [Abstract][Full Text] [Related]
40. Misfolded SOD1 Accumulation and Mitochondrial Association Contribute to the Selective Vulnerability of Motor Neurons in Familial ALS: Correlation to Human Disease.
Abu-Hamad S; Kahn J; Leyton-Jaimes MF; Rosenblatt J; Israelson A
ACS Chem Neurosci; 2017 Oct; 8(10):2225-2234. PubMed ID: 28715630
[TBL] [Abstract][Full Text] [Related]
[Previous] [Next] [New Search]