208 related articles for article (PubMed ID: 28363799)
1. Neuroserpin polymers cause oxidative stress in a neuronal model of the dementia FENIB.
Guadagno NA; Moriconi C; Licursi V; D'Acunto E; Nisi PS; Carucci N; De Jaco A; Cacci E; Negri R; Lupo G; Miranda E
Neurobiol Dis; 2017 Jul; 103():32-44. PubMed ID: 28363799
[TBL] [Abstract][Full Text] [Related]
2. Polymerogenic neuroserpin causes mitochondrial alterations and activates NFκB but not the UPR in a neuronal model of neurodegeneration FENIB.
D'Acunto E; Gianfrancesco L; Serangeli I; D'Orsi M; Sabato V; Guadagno NA; Bhosale G; Caristi S; Failla AV; De Jaco A; Cacci E; Duchen MR; Lupo G; Galliciotti G; Miranda E
Cell Mol Life Sci; 2022 Jul; 79(8):437. PubMed ID: 35864382
[TBL] [Abstract][Full Text] [Related]
3. Sterol metabolism regulates neuroserpin polymer degradation in the absence of the unfolded protein response in the dementia FENIB.
Roussel BD; Newton TM; Malzer E; Simecek N; Haq I; Thomas SE; Burr ML; Lehner PJ; Crowther DC; Marciniak SJ; Lomas DA
Hum Mol Genet; 2013 Nov; 22(22):4616-26. PubMed ID: 23814041
[TBL] [Abstract][Full Text] [Related]
4. G392E neuroserpin causing the dementia FENIB is secreted from cells but is not synaptotoxic.
Ingwersen T; Linnenberg C; D'Acunto E; Temori S; Paolucci I; Wasilewski D; Mohammadi B; Kirchmair J; Glen RC; Miranda E; Glatzel M; Galliciotti G
Sci Rep; 2021 Apr; 11(1):8766. PubMed ID: 33888787
[TBL] [Abstract][Full Text] [Related]
5. Mutation-, aging-, and gene dosage-dependent accumulation of neuroserpin (G392E) in endoplasmic reticula and lysosomes of neurons in transgenic mice.
Takasawa A; Kato I; Takasawa K; Ishii Y; Yoshida T; Shehata MH; Kawaguchi H; Mohafez OM; Sasahara M; Hiraga K
J Biol Chem; 2008 Dec; 283(51):35606-13. PubMed ID: 18940798
[TBL] [Abstract][Full Text] [Related]
6. Lectin OS-9 delivers mutant neuroserpin to endoplasmic reticulum associated degradation in familial encephalopathy with neuroserpin inclusion bodies.
Schipanski A; Oberhauser F; Neumann M; Lange S; Szalay B; Krasemann S; van Leeuwen FW; Galliciotti G; Glatzel M
Neurobiol Aging; 2014 Oct; 35(10):2394-403. PubMed ID: 24795221
[TBL] [Abstract][Full Text] [Related]
7. The serpinopathies studying serpin polymerization in vivo.
Irving JA; Ekeowa UI; Belorgey D; Haq I; Gooptu B; Miranda E; Pérez J; Roussel BD; Ordóñez A; Dalton LE; Thomas SE; Marciniak SJ; Parfrey H; Chilvers ER; Teckman JH; Alam S; Mahadeva R; Rashid ST; Vallier L; Lomas DA
Methods Enzymol; 2011; 501():421-66. PubMed ID: 22078544
[TBL] [Abstract][Full Text] [Related]
8. Cellular Models for the Serpinopathies.
Fra A; D'Acunto E; Laffranchi M; Miranda E
Methods Mol Biol; 2018; 1826():109-121. PubMed ID: 30194596
[TBL] [Abstract][Full Text] [Related]
9. Interactions between N-linked glycosylation and polymerisation of neuroserpin within the endoplasmic reticulum.
Moriconi C; Ordoñez A; Lupo G; Gooptu B; Irving JA; Noto R; Martorana V; Manno M; Timpano V; Guadagno NA; Dalton L; Marciniak SJ; Lomas DA; Miranda E
FEBS J; 2015 Dec; 282(23):4565-79. PubMed ID: 26367528
[TBL] [Abstract][Full Text] [Related]
10. Limited Unfolded Protein Response and Inflammation in Neuroserpinopathy.
López-González I; Pérez-Mediavilla A; Zamarbide M; Carmona M; Torrejón Escribano B; Glatzel M; Galliciotti G; Ferrer I
J Neuropathol Exp Neurol; 2016 Feb; 75(2):121-33. PubMed ID: 26733586
[TBL] [Abstract][Full Text] [Related]
11. Neuroserpin Inclusion Bodies in a FENIB Yeast Model.
Vapore V; Mazzaglia C; Sibilia D; Del Vecchio M; Fruhmann G; Valenti M; Miranda E; Rinaldi T; Winderickx J; Mazzoni C
Microorganisms; 2021 Jul; 9(7):. PubMed ID: 34361933
[TBL] [Abstract][Full Text] [Related]
12. Latent S49P neuroserpin forms polymers in the dementia familial encephalopathy with neuroserpin inclusion bodies.
Onda M; Belorgey D; Sharp LK; Lomas DA
J Biol Chem; 2005 Apr; 280(14):13735-41. PubMed ID: 15664988
[TBL] [Abstract][Full Text] [Related]
13. The intracellular accumulation of polymeric neuroserpin explains the severity of the dementia FENIB.
Miranda E; MacLeod I; Davies MJ; Pérez J; Römisch K; Crowther DC; Lomas DA
Hum Mol Genet; 2008 Jun; 17(11):1527-39. PubMed ID: 18267959
[TBL] [Abstract][Full Text] [Related]
14. Neuroserpin: structure, function, physiology and pathology.
D'Acunto E; Fra A; Visentin C; Manno M; Ricagno S; Galliciotti G; Miranda E
Cell Mol Life Sci; 2021 Oct; 78(19-20):6409-6430. PubMed ID: 34405255
[TBL] [Abstract][Full Text] [Related]
15. Progressive myoclonus epilepsy associated with neuroserpin inclusion bodies (neuroserpinosis).
Roussel BD; Lomas DA; Crowther DC
Epileptic Disord; 2016 Sep; 18(S2):103-110. PubMed ID: 27618835
[TBL] [Abstract][Full Text] [Related]
16. Mutants of neuroserpin that cause dementia accumulate as polymers within the endoplasmic reticulum.
Miranda E; Römisch K; Lomas DA
J Biol Chem; 2004 Jul; 279(27):28283-91. PubMed ID: 15090543
[TBL] [Abstract][Full Text] [Related]
17. Functional and dysfunctional conformers of human neuroserpin characterized by optical spectroscopies and Molecular Dynamics.
Noto R; Santangelo MG; Levantino M; Cupane A; Mangione MR; Parisi D; Ricagno S; Bolognesi M; Manno M; Martorana V
Biochim Biophys Acta; 2015 Feb; 1854(2):110-7. PubMed ID: 25450507
[TBL] [Abstract][Full Text] [Related]
18. Characterisation of serpin polymers in vitro and in vivo.
Belorgey D; Irving JA; Ekeowa UI; Freeke J; Roussel BD; Miranda E; Pérez J; Robinson CV; Marciniak SJ; Crowther DC; Michel CH; Lomas DA
Methods; 2011 Mar; 53(3):255-66. PubMed ID: 21115126
[TBL] [Abstract][Full Text] [Related]
19. The endoplasmic reticulum (ER)-associated degradation system regulates aggregation and degradation of mutant neuroserpin.
Ying Z; Wang H; Fan H; Wang G
J Biol Chem; 2011 Jun; 286(23):20835-44. PubMed ID: 21507957
[TBL] [Abstract][Full Text] [Related]
20. Endoplasmic reticulum-associated degradation (ERAD) and autophagy cooperate to degrade polymerogenic mutant serpins.
Kroeger H; Miranda E; MacLeod I; Pérez J; Crowther DC; Marciniak SJ; Lomas DA
J Biol Chem; 2009 Aug; 284(34):22793-802. PubMed ID: 19549782
[TBL] [Abstract][Full Text] [Related]
[Next] [New Search]