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2. The Cx26-G45E mutation displays increased hemichannel activity in a mouse model of the lethal form of keratitis-ichthyosis-deafness syndrome. Mese G; Sellitto C; Li L; Wang HZ; Valiunas V; Richard G; Brink PR; White TW Mol Biol Cell; 2011 Dec; 22(24):4776-86. PubMed ID: 22031297 [TBL] [Abstract][Full Text] [Related]
3. The connexin26 S17F mouse mutant represents a model for the human hereditary keratitis-ichthyosis-deafness syndrome. Schütz M; Auth T; Gehrt A; Bosen F; Körber I; Strenzke N; Moser T; Willecke K Hum Mol Genet; 2011 Jan; 20(1):28-39. PubMed ID: 20926451 [TBL] [Abstract][Full Text] [Related]
4. Aberrant hemichannel properties of Cx26 mutations causing skin disease and deafness. Gerido DA; DeRosa AM; Richard G; White TW Am J Physiol Cell Physiol; 2007 Jul; 293(1):C337-45. PubMed ID: 17428836 [TBL] [Abstract][Full Text] [Related]
5. trans-dominant inhibition of connexin-43 by mutant connexin-26: implications for dominant connexin disorders affecting epidermal differentiation. Rouan F; White TW; Brown N; Taylor AM; Lucke TW; Paul DL; Munro CS; Uitto J; Hodgins MB; Richard G J Cell Sci; 2001 Jun; 114(Pt 11):2105-13. PubMed ID: 11493646 [TBL] [Abstract][Full Text] [Related]
6. Altered epidermal lipid processing and calcium distribution in the KID syndrome mouse model Cx26S17F. Bosen F; Celli A; Crumrine D; vom Dorp K; Ebel P; Jastrow H; Dörmann P; Winterhager E; Mauro T; Willecke K FEBS Lett; 2015 Jul; 589(15):1904-10. PubMed ID: 26070424 [TBL] [Abstract][Full Text] [Related]
7. A novel N14Y mutation in Connexin26 in keratitis-ichthyosis-deafness syndrome: analyses of altered gap junctional communication and molecular structure of N terminus of mutated Connexin26. Arita K; Akiyama M; Aizawa T; Umetsu Y; Segawa I; Goto M; Sawamura D; Demura M; Kawano K; Shimizu H Am J Pathol; 2006 Aug; 169(2):416-23. PubMed ID: 16877344 [TBL] [Abstract][Full Text] [Related]
8. The human Cx26-D50A and Cx26-A88V mutations causing keratitis-ichthyosis-deafness syndrome display increased hemichannel activity. Mhaske PV; Levit NA; Li L; Wang HZ; Lee JR; Shuja Z; Brink PR; White TW Am J Physiol Cell Physiol; 2013 Jun; 304(12):C1150-8. PubMed ID: 23447037 [TBL] [Abstract][Full Text] [Related]
9. Differentiation of organotypic epidermis in the presence of skin disease-linked dominant-negative Cx26 mutants and knockdown Cx26. Thomas T; Shao Q; Laird DW J Membr Biol; 2007 Jun; 217(1-3):93-104. PubMed ID: 17638039 [TBL] [Abstract][Full Text] [Related]
10. Overexpression of connexin26 in the basal keratinocytes reduces sensitivity to tumor promoter TPA. Wang X; Ramirez A; Budunova I Exp Dermatol; 2010 Jul; 19(7):633-40. PubMed ID: 20002174 [TBL] [Abstract][Full Text] [Related]
11. The effects of a mutant connexin 26 on epidermal differentiation. Bakirtzis G; Jamieson S; Aasen T; Bryson S; Forrow S; Tetley L; Finbow M; Greenhalgh D; Hodgins M Cell Commun Adhes; 2003; 10(4-6):359-64. PubMed ID: 14681042 [TBL] [Abstract][Full Text] [Related]
12. Connexin-26 mutations in deafness and skin disease. Lee JR; White TW Expert Rev Mol Med; 2009 Nov; 11():e35. PubMed ID: 19939300 [TBL] [Abstract][Full Text] [Related]
13. Palmoplantar keratoderma with deafness phenotypic variability in a patient with an inherited GJB2 frameshift variant and novel missense variant. Bedoukian EC; Rentas S; Skraban C; Shao Q; Treat J; Laird DW; Sullivan KE Mol Genet Genomic Med; 2021 Feb; 9(2):e1574. PubMed ID: 33443819 [TBL] [Abstract][Full Text] [Related]
14. Connexins: sensors of epidermal integrity that are therapeutic targets. Martin PE; Easton JA; Hodgins MB; Wright CS FEBS Lett; 2014 Apr; 588(8):1304-14. PubMed ID: 24607543 [TBL] [Abstract][Full Text] [Related]
15. Connexin26 Mutations Causing Palmoplantar Keratoderma and Deafness Interact with Connexin43, Modifying Gap Junction and Hemichannel Properties. Shuja Z; Li L; Gupta S; Meşe G; White TW J Invest Dermatol; 2016 Jan; 136(1):225-235. PubMed ID: 26763442 [TBL] [Abstract][Full Text] [Related]
16. Differential susceptibility of Cx26 mutations associated with epidermal dysplasias to peptidoglycan derived from Staphylococcus aureus and Staphylococcus epidermidis. Donnelly S; English G; de Zwart-Storm EA; Lang S; van Steensel MA; Martin PE Exp Dermatol; 2012 Aug; 21(8):592-8. PubMed ID: 22643125 [TBL] [Abstract][Full Text] [Related]
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18. Keratitis-ichthyosis-deafness syndrome-associated Cx26 mutants produce nonfunctional gap junctions but hyperactive hemichannels when co-expressed with wild type Cx43. García IE; Maripillán J; Jara O; Ceriani R; Palacios-Muñoz A; Ramachandran J; Olivero P; Perez-Acle T; González C; Sáez JC; Contreras JE; Martínez AD J Invest Dermatol; 2015 May; 135(5):1338-1347. PubMed ID: 25625422 [TBL] [Abstract][Full Text] [Related]
19. A deafness mechanism of digenic Cx26 (GJB2) and Cx30 (GJB6) mutations: Reduction of endocochlear potential by impairment of heterogeneous gap junctional function in the cochlear lateral wall. Mei L; Chen J; Zong L; Zhu Y; Liang C; Jones RO; Zhao HB Neurobiol Dis; 2017 Dec; 108():195-203. PubMed ID: 28823936 [TBL] [Abstract][Full Text] [Related]
20. Transport and function of cx26 mutants involved in skin and deafness disorders. Thomas T; Aasen T; Hodgins M; Laird DW Cell Commun Adhes; 2003; 10(4-6):353-8. PubMed ID: 14681041 [TBL] [Abstract][Full Text] [Related] [Next] [New Search]