These tools will no longer be maintained as of December 31, 2024. Archived website can be found here. PubMed4Hh GitHub repository can be found here. Contact NLM Customer Service if you have questions.
125 related articles for article (PubMed ID: 2868163)
1. Carnitine reduces fasting ketogenesis in patients with disorders of propionate metabolism. Wolff JA; Carroll JE; Le Phuc Thuy ; Prodanos C; Haas R; Nyhan WL Lancet; 1986 Feb; 1(8476):289-91. PubMed ID: 2868163 [TBL] [Abstract][Full Text] [Related]
2. Propionylcarnitine excretion in propionic and methylmalonic acidurias: a cause of carnitine deficiency. Di Donato S; Rimoldi M; Garavaglia B; Uziel G Clin Chim Acta; 1984 May; 139(1):13-21. PubMed ID: 6723070 [TBL] [Abstract][Full Text] [Related]
3. Urinary propionylcarnitine analysis for monitoring carnitine supplementation in inherited disorders of propionate metabolism. Sugiyama N; Matsuda I; Wada Y; Narisawa K; Kobayashi M; Kidouchi K J Inherit Metab Dis; 1994; 17(5):611-5. PubMed ID: 7837769 [No Abstract] [Full Text] [Related]
4. Oxidative stress parameters in urine from patients with disorders of propionate metabolism: a beneficial effect of L:-carnitine supplementation. Ribas GS; Biancini GB; Mescka C; Wayhs CY; Sitta A; Wajner M; Vargas CR Cell Mol Neurobiol; 2012 Jan; 32(1):77-82. PubMed ID: 21833551 [TBL] [Abstract][Full Text] [Related]
6. L-carnitine in inborn errors of metabolism: what is the evidence? Walter JH J Inherit Metab Dis; 2003; 26(2-3):181-8. PubMed ID: 12889659 [TBL] [Abstract][Full Text] [Related]
7. Stimulation of ketogenesis by propionate in isolated rat hepatocytes: an explanation for ketosis associated with propionic acidaemia and methylmalonic acidaemia? Rosario P; Medina JM J Inherit Metab Dis; 1982; 5(1):59-62. PubMed ID: 6820416 [TBL] [Abstract][Full Text] [Related]
8. Reduction of lipid and protein damage in patients with disorders of propionate metabolism under treatment: a possible protective role of L-carnitine supplementation. Ribas GS; Manfredini V; de Mari JF; Wayhs CY; Vanzin CS; Biancini GB; Sitta A; Deon M; Wajner M; Vargas CR Int J Dev Neurosci; 2010 Apr; 28(2):127-32. PubMed ID: 20100562 [TBL] [Abstract][Full Text] [Related]
9. Propionylcarnitine excretion is not affected by metronidazole administration to patients with disorders of propionate metabolism. Burns SP; Iles RA; Saudubray JM; Chalmers RA Eur J Pediatr; 1996 Jan; 155(1):31-5. PubMed ID: 8750807 [TBL] [Abstract][Full Text] [Related]
10. Direct identification of propionylcarnitine in propionic acidaemia: biochemical and clinical results of oral carnitine supplementation. Duran M; Ketting D; Beckeringh TE; Leupold D; Wadman SK J Inherit Metab Dis; 1986; 9(2):202-7. PubMed ID: 3091925 [TBL] [Abstract][Full Text] [Related]
11. The management and outcome of propionic and methylmalonic acidaemia. Leonard JV J Inherit Metab Dis; 1995; 18(4):430-4. PubMed ID: 7494401 [TBL] [Abstract][Full Text] [Related]
12. Successful pregnancy in a woman with mut- methylmalonic acidaemia. Deodato F; Rizzo C; Boenzi S; Baiocco F; Sabetta G; Dionisi-Vici C J Inherit Metab Dis; 2002 May; 25(2):133-4. PubMed ID: 12118529 [TBL] [Abstract][Full Text] [Related]
13. The effect of intravenous L-carnitine on propionic acid excretion in acute propionic acidaemia. Böhles H; Lehnert W Eur J Pediatr; 1984 Nov; 143(1):61-3. PubMed ID: 6510434 [TBL] [Abstract][Full Text] [Related]
14. Stable isotope studies in propionic and methylmalonic acidaemia. Leonard JV Eur J Pediatr; 1997 Aug; 156 Suppl 1():S67-9. PubMed ID: 9266219 [TBL] [Abstract][Full Text] [Related]
15. In vivo propionate oxidation as a prognostic indicator in disorders of propionate metabolism. Thompson GN; Walter JH; Bresson JL; Bonnefont JP; Saudubray JM; Leonard JV; Halliday D Eur J Pediatr; 1990 Mar; 149(6):408-11. PubMed ID: 2332010 [TBL] [Abstract][Full Text] [Related]
16. ESI-MS/MS study of acylcarnitine profiles in urine from patients with organic acidemias and fatty acid oxidation disorders. Kobayashi H; Hasegawa Y; Endo M; Purevsuren J; Yamaguchi S J Chromatogr B Analyt Technol Biomed Life Sci; 2007 Aug; 855(1):80-7. PubMed ID: 17301002 [TBL] [Abstract][Full Text] [Related]
17. Metabolic response to carnitine in methylmalonic aciduria. An effective strategy for elimination of propionyl groups. Roe CR; Hoppel CL; Stacey TE; Chalmers RA; Tracey BM; Millington DS Arch Dis Child; 1983 Nov; 58(11):916-20. PubMed ID: 6651329 [TBL] [Abstract][Full Text] [Related]