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7. Effects of triheptanoin (UX007) in patients with long-chain fatty acid oxidation disorders: Results from an open-label, long-term extension study. Vockley J; Burton B; Berry G; Longo N; Phillips J; Sanchez-Valle A; Chapman K; Tanpaiboon P; Grunewald S; Murphy E; Lu X; Cataldo J J Inherit Metab Dis; 2021 Jan; 44(1):253-263. PubMed ID: 32885845 [TBL] [Abstract][Full Text] [Related]
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14. Deregulation of mitochondrial functions provoked by long-chain fatty acid accumulating in long-chain 3-hydroxyacyl-CoA dehydrogenase and mitochondrial permeability transition deficiencies in rat heart--mitochondrial permeability transition pore opening as a potential contributing pathomechanism of cardiac alterations in these disorders. Cecatto C; Hickmann FH; Rodrigues MD; Amaral AU; Wajner M FEBS J; 2015 Dec; 282(24):4714-26. PubMed ID: 26408230 [TBL] [Abstract][Full Text] [Related]
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