290 related articles for article (PubMed ID: 28988989)
1. FUS Mutant Human Motoneurons Display Altered Transcriptome and microRNA Pathways with Implications for ALS Pathogenesis.
De Santis R; Santini L; Colantoni A; Peruzzi G; de Turris V; Alfano V; Bozzoni I; Rosa A
Stem Cell Reports; 2017 Nov; 9(5):1450-1462. PubMed ID: 28988989
[TBL] [Abstract][Full Text] [Related]
2. Mutant FUS and ELAVL4 (HuD) Aberrant Crosstalk in Amyotrophic Lateral Sclerosis.
De Santis R; Alfano V; de Turris V; Colantoni A; Santini L; Garone MG; Antonacci G; Peruzzi G; Sudria-Lopez E; Wyler E; Anink JJ; Aronica E; Landthaler M; Pasterkamp RJ; Bozzoni I; Rosa A
Cell Rep; 2019 Jun; 27(13):3818-3831.e5. PubMed ID: 31242416
[TBL] [Abstract][Full Text] [Related]
3. ALS-related FUS mutations alter axon growth in motoneurons and affect HuD/ELAVL4 and FMRP activity.
Garone MG; Birsa N; Rosito M; Salaris F; Mochi M; de Turris V; Nair RR; Cunningham TJ; Fisher EMC; Morlando M; Fratta P; Rosa A
Commun Biol; 2021 Sep; 4(1):1025. PubMed ID: 34471224
[TBL] [Abstract][Full Text] [Related]
4. A Regulatory Circuitry Between Gria2, miR-409, and miR-495 Is Affected by ALS FUS Mutation in ESC-Derived Motor Neurons.
Capauto D; Colantoni A; Lu L; Santini T; Peruzzi G; Biscarini S; Morlando M; Shneider NA; Caffarelli E; Laneve P; Bozzoni I
Mol Neurobiol; 2018 Oct; 55(10):7635-7651. PubMed ID: 29430619
[TBL] [Abstract][Full Text] [Related]
5. Proteomics analysis of FUS mutant human motoneurons reveals altered regulation of cytoskeleton and other ALS-linked proteins via 3'UTR binding.
Garone MG; Alfano V; Salvatori B; Braccia C; Peruzzi G; Colantoni A; Bozzoni I; Armirotti A; Rosa A
Sci Rep; 2020 Jul; 10(1):11827. PubMed ID: 32678235
[TBL] [Abstract][Full Text] [Related]
6. Aberrant axon branching via Fos-B dysregulation in FUS-ALS motor neurons.
Akiyama T; Suzuki N; Ishikawa M; Fujimori K; Sone T; Kawada J; Funayama R; Fujishima F; Mitsuzawa S; Ikeda K; Ono H; Shijo T; Osana S; Shirota M; Nakagawa T; Kitajima Y; Nishiyama A; Izumi R; Morimoto S; Okada Y; Kamei T; Nishida M; Nogami M; Kaneda S; Ikeuchi Y; Mitsuhashi H; Nakayama K; Fujii T; Warita H; Okano H; Aoki M
EBioMedicine; 2019 Jul; 45():362-378. PubMed ID: 31262712
[TBL] [Abstract][Full Text] [Related]
7. The fused in sarcoma protein forms cytoplasmic aggregates in motor neurons derived from integration-free induced pluripotent stem cells generated from a patient with familial amyotrophic lateral sclerosis carrying the FUS-P525L mutation.
Liu X; Chen J; Liu W; Li X; Chen Q; Liu T; Gao S; Deng M
Neurogenetics; 2015 Jul; 16(3):223-31. PubMed ID: 25912081
[TBL] [Abstract][Full Text] [Related]
8. ALS mutant FUS proteins are recruited into stress granules in induced pluripotent stem cell-derived motoneurons.
Lenzi J; De Santis R; de Turris V; Morlando M; Laneve P; Calvo A; Caliendo V; Chiò A; Rosa A; Bozzoni I
Dis Model Mech; 2015 Jul; 8(7):755-66. PubMed ID: 26035390
[TBL] [Abstract][Full Text] [Related]
9. Altered calcium dynamics and glutamate receptor properties in iPSC-derived motor neurons from ALS patients with C9orf72, FUS, SOD1 or TDP43 mutations.
Bursch F; Kalmbach N; Naujock M; Staege S; Eggenschwiler R; Abo-Rady M; Japtok J; Guo W; Hensel N; Reinhardt P; Boeckers TM; Cantz T; Sterneckert J; Van Den Bosch L; Hermann A; Petri S; Wegner F
Hum Mol Genet; 2019 Sep; 28(17):2835-2850. PubMed ID: 31108504
[TBL] [Abstract][Full Text] [Related]
10. Directly converted patient-specific induced neurons mirror the neuropathology of FUS with disrupted nuclear localization in amyotrophic lateral sclerosis.
Lim SM; Choi WJ; Oh KW; Xue Y; Choi JY; Kim SH; Nahm M; Kim YE; Lee J; Noh MY; Lee S; Hwang S; Ki CS; Fu XD; Kim SH
Mol Neurodegener; 2016 Jan; 11():8. PubMed ID: 26795035
[TBL] [Abstract][Full Text] [Related]
11. Homozygous ALS-linked FUS P525L mutations cell- autonomously perturb transcriptome profile and chemoreceptor signaling in human iPSC microglia.
Kerk SY; Bai Y; Smith J; Lalgudi P; Hunt C; Kuno J; Nuara J; Yang T; Lanza K; Chan N; Coppola A; Tang Q; Espert J; Jones H; Fannell C; Zambrowicz B; Chiao E
Stem Cell Reports; 2022 Mar; 17(3):678-692. PubMed ID: 35120624
[TBL] [Abstract][Full Text] [Related]
12. Establishment of In Vitro FUS-Associated Familial Amyotrophic Lateral Sclerosis Model Using Human Induced Pluripotent Stem Cells.
Ichiyanagi N; Fujimori K; Yano M; Ishihara-Fujisaki C; Sone T; Akiyama T; Okada Y; Akamatsu W; Matsumoto T; Ishikawa M; Nishimoto Y; Ishihara Y; Sakuma T; Yamamoto T; Tsuiji H; Suzuki N; Warita H; Aoki M; Okano H
Stem Cell Reports; 2016 Apr; 6(4):496-510. PubMed ID: 26997647
[TBL] [Abstract][Full Text] [Related]
13. Adenoviral expression of TDP-43 and FUS genes and shRNAs for protein degradation pathways in rodent motoneurons in vitro and in vivo.
Watabe K; Akiyama K; Kawakami E; Ishii T; Endo K; Yanagisawa H; Sango K; Tsukamoto M
Neuropathology; 2014 Feb; 34(1):83-98. PubMed ID: 23937386
[TBL] [Abstract][Full Text] [Related]
14. lncRNA Sequencing Reveals Neurodegeneration-Associated FUS Mutations Alter Transcriptional Landscape of iPS Cells That Persists in Motor Neurons.
Provasek VE; Kodavati M; Guo W; Wang H; Boldogh I; Van Den Bosch L; Britz G; Hegde ML
Cells; 2023 Oct; 12(20):. PubMed ID: 37887305
[TBL] [Abstract][Full Text] [Related]
15. HDAC6 inhibition reverses axonal transport defects in motor neurons derived from FUS-ALS patients.
Guo W; Naujock M; Fumagalli L; Vandoorne T; Baatsen P; Boon R; Ordovás L; Patel A; Welters M; Vanwelden T; Geens N; Tricot T; Benoy V; Steyaert J; Lefebvre-Omar C; Boesmans W; Jarpe M; Sterneckert J; Wegner F; Petri S; Bohl D; Vanden Berghe P; Robberecht W; Van Damme P; Verfaillie C; Van Den Bosch L
Nat Commun; 2017 Oct; 8(1):861. PubMed ID: 29021520
[TBL] [Abstract][Full Text] [Related]
16. Novel miR-b2122 regulates several ALS-related RNA-binding proteins.
Hawley ZCE; Campos-Melo D; Strong MJ
Mol Brain; 2017 Oct; 10(1):46. PubMed ID: 28969660
[TBL] [Abstract][Full Text] [Related]
17. ALS-causing mutations differentially affect PGC-1α expression and function in the brain vs. peripheral tissues.
Bayer H; Lang K; Buck E; Higelin J; Barteczko L; Pasquarelli N; Sprissler J; Lucas T; Holzmann K; Demestre M; Lindenberg KS; Danzer KM; Boeckers T; Ludolph AC; Dupuis L; Weydt P; Witting A
Neurobiol Dis; 2017 Jan; 97(Pt A):36-45. PubMed ID: 27818323
[TBL] [Abstract][Full Text] [Related]
18. Upregulation of β-catenin due to loss of miR-139 contributes to motor neuron death in amyotrophic lateral sclerosis.
Hawkins S; Namboori SC; Tariq A; Blaker C; Flaxman C; Dey NS; Henley P; Randall A; Rosa A; Stanton LW; Bhinge A
Stem Cell Reports; 2022 Jul; 17(7):1650-1665. PubMed ID: 35750046
[TBL] [Abstract][Full Text] [Related]
19. ALS-associated mutations in FUS disrupt the axonal distribution and function of SMN.
Groen EJ; Fumoto K; Blokhuis AM; Engelen-Lee J; Zhou Y; van den Heuvel DM; Koppers M; van Diggelen F; van Heest J; Demmers JA; Kirby J; Shaw PJ; Aronica E; Spliet WG; Veldink JH; van den Berg LH; Pasterkamp RJ
Hum Mol Genet; 2013 Sep; 22(18):3690-704. PubMed ID: 23681068
[TBL] [Abstract][Full Text] [Related]
20. [The FUS protein: Physiological functions and a role in amyotrophic lateral sclerosis].
Efimova AD; Ovchinnikov RK; Roman AY; Maltsev AV; Grigoriev VV; Kovrazhkina EA; Skvortsova VI
Mol Biol (Mosk); 2017; 51(3):387-399. PubMed ID: 28707655
[TBL] [Abstract][Full Text] [Related]
[Next] [New Search]