These tools will no longer be maintained as of December 31, 2024. Archived website can be found here. PubMed4Hh GitHub repository can be found here. Contact NLM Customer Service if you have questions.
265 related articles for article (PubMed ID: 29135436)
1. Defective synaptic transmission causes disease signs in a mouse model of juvenile neuronal ceroid lipofuscinosis. Grünewald B; Lange MD; Werner C; O'Leary A; Weishaupt A; Popp S; Pearce DA; Wiendl H; Reif A; Pape HC; Toyka KV; Sommer C; Geis C Elife; 2017 Nov; 6():. PubMed ID: 29135436 [TBL] [Abstract][Full Text] [Related]
2. Age-dependent alterations in neuronal activity in the hippocampus and visual cortex in a mouse model of Juvenile Neuronal Ceroid Lipofuscinosis (CLN3). Burkovetskaya M; Karpuk N; Kielian T Neurobiol Dis; 2017 Apr; 100():19-29. PubMed ID: 28042098 [TBL] [Abstract][Full Text] [Related]
3. Cerebellar defects in a mouse model of juvenile neuronal ceroid lipofuscinosis. Weimer JM; Benedict JW; Getty AL; Pontikis CC; Lim MJ; Cooper JD; Pearce DA Brain Res; 2009 Apr; 1266():93-107. PubMed ID: 19230832 [TBL] [Abstract][Full Text] [Related]
4. Altered Cerebellar Short-Term Plasticity but No Change in Postsynaptic AMPA-Type Glutamate Receptors in a Mouse Model of Juvenile Batten Disease. Studniarczyk D; Needham EL; Mitchison HM; Farrant M; Cull-Candy SG eNeuro; 2018; 5(2):. PubMed ID: 29780879 [TBL] [Abstract][Full Text] [Related]
5. Transcript and in silico analysis of CLN3 in juvenile neuronal ceroid lipofuscinosis and associated mouse models. Chan CH; Mitchison HM; Pearce DA Hum Mol Genet; 2008 Nov; 17(21):3332-9. PubMed ID: 18678598 [TBL] [Abstract][Full Text] [Related]
6. Late onset neurodegeneration in the Cln3-/- mouse model of juvenile neuronal ceroid lipofuscinosis is preceded by low level glial activation. Pontikis CC; Cella CV; Parihar N; Lim MJ; Chakrabarti S; Mitchison HM; Mobley WC; Rezaie P; Pearce DA; Cooper JD Brain Res; 2004 Oct; 1023(2):231-42. PubMed ID: 15374749 [TBL] [Abstract][Full Text] [Related]
7. Retinal pathology and function in a Cln3 knockout mouse model of juvenile Neuronal Ceroid Lipofuscinosis (batten disease). Seigel GM; Lotery A; Kummer A; Bernard DJ; Greene ND; Turmaine M; Derksen T; Nussbaum RL; Davidson B; Wagner J; Mitchison HM Mol Cell Neurosci; 2002 Apr; 19(4):515-27. PubMed ID: 11988019 [TBL] [Abstract][Full Text] [Related]
8. Glial cells are functionally impaired in juvenile neuronal ceroid lipofuscinosis and detrimental to neurons. Parviainen L; Dihanich S; Anderson GW; Wong AM; Brooks HR; Abeti R; Rezaie P; Lalli G; Pope S; Heales SJ; Mitchison HM; Williams BP; Cooper JD Acta Neuropathol Commun; 2017 Oct; 5(1):74. PubMed ID: 29041969 [TBL] [Abstract][Full Text] [Related]
9. Alterations in striatal dopamine catabolism precede loss of substantia nigra neurons in a mouse model of juvenile neuronal ceroid lipofuscinosis. Weimer JM; Benedict JW; Elshatory YM; Short DW; Ramirez-Montealegre D; Ryan DA; Alexander NA; Federoff HJ; Cooper JD; Pearce DA Brain Res; 2007 Aug; 1162():98-112. PubMed ID: 17617387 [TBL] [Abstract][Full Text] [Related]
10. Loss of CLN3, the gene mutated in juvenile neuronal ceroid lipofuscinosis, leads to metabolic impairment and autophagy induction in retinal pigment epithelium. Zhong Y; Mohan K; Liu J; Al-Attar A; Lin P; Flight RM; Sun Q; Warmoes MO; Deshpande RR; Liu H; Jung KS; Mitov MI; Lin N; Butterfield DA; Lu S; Liu J; Moseley HNB; Fan TWM; Kleinman ME; Wang QJ Biochim Biophys Acta Mol Basis Dis; 2020 Oct; 1866(10):165883. PubMed ID: 32592935 [TBL] [Abstract][Full Text] [Related]
11. Batten disease (JNCL) is linked to disturbances in mitochondrial, cytoskeletal, and synaptic compartments. Luiro K; Kopra O; Blom T; Gentile M; Mitchison HM; Hovatta I; Törnquist K; Jalanko A J Neurosci Res; 2006 Oct; 84(5):1124-38. PubMed ID: 16941499 [TBL] [Abstract][Full Text] [Related]
12. Functional categorization of gene expression changes in the cerebellum of a Cln3-knockout mouse model for Batten disease. Brooks AI; Chattopadhyay S; Mitchison HM; Nussbaum RL; Pearce DA Mol Genet Metab; 2003 Jan; 78(1):17-30. PubMed ID: 12559844 [TBL] [Abstract][Full Text] [Related]
13. Regional brain atrophy in mouse models of neuronal ceroid lipofuscinosis: a new rostrocaudal perspective. Kühl TG; Dihanich S; Wong AM; Cooper JD J Child Neurol; 2013 Sep; 28(9):1117-22. PubMed ID: 24014506 [TBL] [Abstract][Full Text] [Related]
14. Phenotypic characterization of a mouse model of juvenile neuronal ceroid lipofuscinosis. Katz ML; Johnson GS; Tullis GE; Lei B Neurobiol Dis; 2008 Feb; 29(2):242-53. PubMed ID: 17962032 [TBL] [Abstract][Full Text] [Related]
15. Altered flurothyl seizure induction latency, phenotype, and subsequent mortality in a mouse model of juvenile neuronal ceroid lipofuscinosis/batten disease. Kriscenski-Perry E; Applegate CD; Serour A; Mhyre TR; Leonardo CC; Pearce DA Epilepsia; 2002 Oct; 43(10):1137-40. PubMed ID: 12366726 [TBL] [Abstract][Full Text] [Related]
16. A novel c.1135_1138delCTGT mutation in CLN3 leads to juvenile neuronal ceroid lipofuscinosis. Drack AV; Miller JN; Pearce DA J Child Neurol; 2013 Sep; 28(9):1112-6. PubMed ID: 23877479 [TBL] [Abstract][Full Text] [Related]
18. Age-dependent therapeutic effect of memantine in a mouse model of juvenile Batten disease. Kovács AD; Saje A; Wong A; Ramji S; Cooper JD; Pearce DA Neuropharmacology; 2012 Oct; 63(5):769-75. PubMed ID: 22683643 [TBL] [Abstract][Full Text] [Related]
19. Altered gene expression in the eye of a mouse model for batten disease. Chattopadhyay S; Kingsley E; Serour A; Curran TM; Brooks AI; Pearce DA Invest Ophthalmol Vis Sci; 2004 Sep; 45(9):2893-905. PubMed ID: 15326100 [TBL] [Abstract][Full Text] [Related]
20. Altered arginine metabolism in the central nervous system (CNS) of the Cln3-/- mouse model of juvenile Batten disease. Chan CH; Ramirez-Montealegre D; Pearce DA Neuropathol Appl Neurobiol; 2009 Apr; 35(2):189-207. PubMed ID: 19284480 [TBL] [Abstract][Full Text] [Related] [Next] [New Search]