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5. Promoterless, Nuclease-Free Genome Editing Confers a Growth Advantage for Corrected Hepatocytes in Mice With Methylmalonic Acidemia. Chandler RJ; Venturoni LE; Liao J; Hubbard BT; Schneller JL; Hoffmann V; Gordo S; Zang S; Ko CW; Chau N; Chiang K; Kay MA; Barzel A; Venditti CP Hepatology; 2021 Jun; 73(6):2223-2237. PubMed ID: 32976669 [TBL] [Abstract][Full Text] [Related]
6. Tricarboxylic acid cycle enzyme activities in a mouse model of methylmalonic aciduria. Wongkittichote P; Cunningham G; Summar ML; Pumbo E; Forny P; Baumgartner MR; Chapman KA Mol Genet Metab; 2019 Dec; 128(4):444-451. PubMed ID: 31648943 [TBL] [Abstract][Full Text] [Related]
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8. Growth advantage of corrected hepatocytes in a juvenile model of methylmalonic acidemia following liver directed adeno-associated viral mediated nuclease-free genome editing. Venturoni LE; Chandler RJ; Liao J; Hoffmann V; Ramesh N; Gordo S; Chau N; Venditti CP Mol Genet Metab; 2022; 137(1-2):1-8. PubMed ID: 35868241 [TBL] [Abstract][Full Text] [Related]
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10. Long-term rescue of a lethal murine model of methylmalonic acidemia using adeno-associated viral gene therapy. Chandler RJ; Venditti CP Mol Ther; 2010 Jan; 18(1):11-6. PubMed ID: 19861951 [TBL] [Abstract][Full Text] [Related]
11. Correction of methylmalonic aciduria in vivo using a codon-optimized lentiviral vector. Wong ES; McIntyre C; Peters HL; Ranieri E; Anson DS; Fletcher JM Hum Gene Ther; 2014 Jun; 25(6):529-38. PubMed ID: 24568291 [TBL] [Abstract][Full Text] [Related]
12. Neutralizing Antibodies Against Adeno-Associated Viral Capsids in Patients with mut Methylmalonic Acidemia. Harrington EA; Sloan JL; Manoli I; Chandler RJ; Schneider M; McGuire PJ; Calcedo R; Wilson JM; Venditti CP Hum Gene Ther; 2016 May; 27(5):345-53. PubMed ID: 26790480 [TBL] [Abstract][Full Text] [Related]
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17. Systematic literature review and meta-analysis on the epidemiology of methylmalonic acidemia (MMA) with a focus on MMA caused by methylmalonyl-CoA mutase (mut) deficiency. Almási T; Guey LT; Lukacs C; Csetneki K; Vokó Z; Zelei T Orphanet J Rare Dis; 2019 Apr; 14(1):84. PubMed ID: 31023387 [TBL] [Abstract][Full Text] [Related]