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3. Goltz-Gorlin (focal dermal hypoplasia) and the microphthalmia with linear skin defects (MLS) syndrome: no evidence of genetic overlap. Harmsen MB; Azzarello-Burri S; García González MM; Gillessen-Kaesbach G; Meinecke P; Müller D; Rauch A; Rossier E; Seemanova E; Spaich C; Steiner B; Wieczorek D; Zenker M; Kutsche K Eur J Hum Genet; 2009 Oct; 17(10):1207-15. PubMed ID: 19277062 [TBL] [Abstract][Full Text] [Related]
4. Novel and recurrent PORCN gene mutations in almost unilateral and typical focal dermal hypoplasia patients. Nakanishi G; Hasegawa K; Oono T; Koshida S; Fujimoto N; Iwatsuki K; Tanaka H; Tanaka T Eur J Dermatol; 2013; 23(1):64-7. PubMed ID: 23399492 [TBL] [Abstract][Full Text] [Related]
5. Deletion of Porcn in mice leads to multiple developmental defects and models human focal dermal hypoplasia (Goltz syndrome). Liu W; Shaver TM; Balasa A; Ljungberg MC; Wang X; Wen S; Nguyen H; Van den Veyver IB PLoS One; 2012; 7(3):e32331. PubMed ID: 22412863 [TBL] [Abstract][Full Text] [Related]
6. Implementation of high-resolution melting analysis of the porcupine (PORCN) gene for molecular diagnosis of focal dermal hypoplasia: Identification of a novel mutation. Martínez-Saucedo M; Ornelas-Fuentes C; Dedden M; Sánchez-Urbina R; Díaz-García H; Aquino-Jarquin G; Moreno-Salgado R; Granados-Riveron JT J Gene Med; 2020 May; 22(5):e3165. PubMed ID: 31984575 [TBL] [Abstract][Full Text] [Related]
7. PORCN gene mutations and the protean nature of focal dermal hypoplasia. Clements SE; Mellerio JE; Holden ST; McCauley J; McGrath JA Br J Dermatol; 2009 May; 160(5):1103-9. PubMed ID: 19292719 [TBL] [Abstract][Full Text] [Related]
8. Two new patients with focal dermal hypoplasia: A novel PORCN variant and insights on the diagnostic considerations. Elhossini RM; Abdel-Hamid MS; Ashaat E; Otaify GA; Dawoud H; Elshimy K; El Ruby M; Aglan M Congenit Anom (Kyoto); 2022 Mar; 62(2):68-77. PubMed ID: 34962003 [TBL] [Abstract][Full Text] [Related]
9. Goltz syndrome and PORCN mosaicism. Stevenson DA; Chirpich M; Contreras Y; Hanson H; Dent K Int J Dermatol; 2014 Dec; 53(12):1481-4. PubMed ID: 25040319 [TBL] [Abstract][Full Text] [Related]
10. Focal dermal hypoplasia (Goltz-Gorlin syndrome): a new case with a novel variant in the PORCN gene (c.1250T>C:p.F417S) and unusual spinal anomaly. Garavelli L; Simonte G; Rosato S; Wischmeijer A; Albertini E; Guareschi E; Longo C; Albertini G; Gelmini C; Greco C; Errico S; Savino G; Pavanello M; Happle R; Unger S; Superti-Furga A; Grzeschik KH Am J Med Genet A; 2013 Jul; 161A(7):1750-4. PubMed ID: 23696273 [TBL] [Abstract][Full Text] [Related]
11. A novel mutation in the PORCN gene underlying a case of almost unilateral focal dermal hypoplasia. Maalouf D; Mégarbané H; Chouery E; Nasr J; Badens C; Lacoste C; Grzeschik KH; Mégarbané A Arch Dermatol; 2012 Jan; 148(1):85-8. PubMed ID: 22250236 [TBL] [Abstract][Full Text] [Related]
12. Focal dermal hypoplasia resulting from a new nonsense mutation, p.E300X, in the PORCN gene. Clements SE; Wessagowit V; Lai-Cheong JE; Arita K; McGrath JA J Dermatol Sci; 2008 Jan; 49(1):39-42. PubMed ID: 17951029 [TBL] [Abstract][Full Text] [Related]
13. Phenotype and genotype in 17 patients with Goltz-Gorlin syndrome. Maas SM; Lombardi MP; van Essen AJ; Wakeling EL; Castle B; Temple IK; Kumar VK; Writzl K; Hennekam RC J Med Genet; 2009 Oct; 46(10):716-20. PubMed ID: 19586929 [TBL] [Abstract][Full Text] [Related]
14. A nonsense porcn mutation in severe focal dermal hypoplasia with natal teeth. Dias C; Basto J; Pinho O; Barbêdo C; Mártins M; Bornholdt D; Fortuna A; Grzeschik KH; Lima M Fetal Pediatr Pathol; 2010; 29(5):305-13. PubMed ID: 20704476 [TBL] [Abstract][Full Text] [Related]
16. Mosaicism due to postzygotic mutations in women with focal dermal hypoplasia. Heinz L; Bourrat E; Vabres P; Thevenon J; Hotz A; Hörer S; Küsel J; Zimmer AD; Alter S; Happle R; Fischer J Br J Dermatol; 2019 Mar; 180(3):657-661. PubMed ID: 30022487 [TBL] [Abstract][Full Text] [Related]
17. Focal Dermal Hypoplasia Due to De Novo Mutation c.1061T>C(p.Leu354Pro) in the PORCN Gene: Importance of Early Diagnosis and Multidisciplinary Follow-Up. Arias-Llorente RP; Rodriguez-Dehli C; López-Martínez A; Riaño-Galán I Fetal Pediatr Pathol; 2015; 34(6):375-82. PubMed ID: 26470739 [TBL] [Abstract][Full Text] [Related]
18. Deletion of mouse Porcn blocks Wnt ligand secretion and reveals an ectodermal etiology of human focal dermal hypoplasia/Goltz syndrome. Barrott JJ; Cash GM; Smith AP; Barrow JR; Murtaugh LC Proc Natl Acad Sci U S A; 2011 Aug; 108(31):12752-7. PubMed ID: 21768372 [TBL] [Abstract][Full Text] [Related]
19. Fragmented Elastic Fibers in Focal Dermal Hypoplasia (Goltz-Gorlin Syndrome) Without Focal Dermal Hypoplasia: Report of a Male Case and Review of the Literature. Rohdenburg C; Liersch J; Kutsche K; Schaller J Am J Dermatopathol; 2020 Sep; 42(9):653-661. PubMed ID: 31789838 [TBL] [Abstract][Full Text] [Related]
20. PORCN mutations in focal dermal hypoplasia: coping with lethality. Bornholdt D; Oeffner F; König A; Happle R; Alanay Y; Ascherman J; Benke PJ; Boente Mdel C; van der Burgt I; Chassaing N; Ellis I; Francisco CR; Della Giovanna P; Hamel B; Has C; Heinelt K; Janecke A; Kastrup W; Loeys B; Lohrisch I; Marcelis C; Mehraein Y; Nicolas ME; Pagliarini D; Paradisi M; Patrizi A; Piccione M; Piza-Katzer H; Prager B; Prescott K; Strien J; Utine GE; Zeller MS; Grzeschik KH Hum Mutat; 2009 May; 30(5):E618-28. PubMed ID: 19309688 [TBL] [Abstract][Full Text] [Related] [Next] [New Search]