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7. Females with Cystic Fibrosis Demonstrate a Differential Response Profile to Ivacaftor Compared with Males. Secunda KE; Guimbellot JS; Jovanovic B; Heltshe SL; Sagel SD; Rowe SM; Jain M Am J Respir Crit Care Med; 2020 Apr; 201(8):996-998. PubMed ID: 31841644 [No Abstract] [Full Text] [Related]
8. Cystic Fibrosis-related Diabetes Is Associated with Worse Lung Function Trajectory despite Ivacaftor Use. Bengtson CD; He J; Kim MD; Salathe MA Am J Respir Crit Care Med; 2021 Dec; 204(11):1343-1345. PubMed ID: 34469275 [No Abstract] [Full Text] [Related]
9. Ivacaftor for the p.Ser549Arg (S549R) gating mutation - The Israeli experience. Dagan A; Cohen-Cymberknoh M; Shteinberg M; Levine H; Vilozni D; Bezalel Y; Bar Aluma BE; Sarouk I; Ashkenazi M; Lavie M; Tsabari R; Blau H; Kerem E; Bentur L; Efrati O; Livnat G Respir Med; 2017 Oct; 131():225-228. PubMed ID: 28947035 [TBL] [Abstract][Full Text] [Related]
11. Assessment of clinical response to ivacaftor with lung clearance index in cystic fibrosis patients with a G551D-CFTR mutation and preserved spirometry: a randomised controlled trial. Davies J; Sheridan H; Bell N; Cunningham S; Davis SD; Elborn JS; Milla CE; Starner TD; Weiner DJ; Lee PS; Ratjen F Lancet Respir Med; 2013 Oct; 1(8):630-638. PubMed ID: 24461666 [TBL] [Abstract][Full Text] [Related]
12. Efficacy and safety of ivacaftor in patients with cystic fibrosis who have an Arg117His-CFTR mutation: a double-blind, randomised controlled trial. Moss RB; Flume PA; Elborn JS; Cooke J; Rowe SM; McColley SA; Rubenstein RC; Higgins M; Lancet Respir Med; 2015 Jul; 3(7):524-33. PubMed ID: 26070913 [TBL] [Abstract][Full Text] [Related]
13. CORK Study in Cystic Fibrosis: Sustained Improvements in Ultra-Low-Dose Chest CT Scores After CFTR Modulation With Ivacaftor. Ronan NJ; Einarsson GG; Twomey M; Mooney D; Mullane D; NiChroinin M; O'Callaghan G; Shanahan F; Murphy DM; O'Connor OJ; Shortt CA; Tunney MM; Eustace JA; Maher MM; Elborn JS; Plant BJ Chest; 2018 Feb; 153(2):395-403. PubMed ID: 29037527 [TBL] [Abstract][Full Text] [Related]
14. Effects of Ivacaftor in Three Pediatric Siblings With Cystic Fibrosis Carrying the Mutations G551D And F508del. Mainz JG; Arnold C; Hentschel J; Tabori H Arch Bronconeumol (Engl Ed); 2018 Apr; 54(4):232-234. PubMed ID: 29103672 [No Abstract] [Full Text] [Related]
15. Lumacaftor/Ivacaftor Treatment of Patients with Cystic Fibrosis Heterozygous for F508del-CFTR. Rowe SM; McColley SA; Rietschel E; Li X; Bell SC; Konstan MW; Marigowda G; Waltz D; Boyle MP; Ann Am Thorac Soc; 2017 Feb; 14(2):213-219. PubMed ID: 27898234 [TBL] [Abstract][Full Text] [Related]
16. In vivo and in vitro ivacaftor response in cystic fibrosis patients with residual CFTR function: N-of-1 studies. McGarry ME; Illek B; Ly NP; Zlock L; Olshansky S; Moreno C; Finkbeiner WE; Nielson DW Pediatr Pulmonol; 2017 Apr; 52(4):472-479. PubMed ID: 28068001 [TBL] [Abstract][Full Text] [Related]
17. Elexacaftor/tezacaftor/ivacaftor (Trikafta) for cystic fibrosis. Med Lett Drugs Ther; 2020 Jan; 62(1589):5-7. PubMed ID: 31999662 [No Abstract] [Full Text] [Related]
18. Positive clinical outcomes following ivacaftor treatment in a cystic fibrosis patient with the genotype 3272-26A > G/Q493X. Pallin M; Daley CP J Cyst Fibros; 2020 Jan; 19(1):e3-e4. PubMed ID: 31771899 [No Abstract] [Full Text] [Related]
19. Forecasting US ivacaftor outcomes and cost in cystic fibrosis patients with the G551D mutation. Dilokthornsakul P; Hansen RN; Campbell JD Eur Respir J; 2016 Jun; 47(6):1697-705. PubMed ID: 27126691 [TBL] [Abstract][Full Text] [Related]
20. The U.S. Food and Drug Administration's Experience with Ivacaftor in Cystic Fibrosis. Establishing Efficacy Using In Vitro Data in Lieu of a Clinical Trial. Durmowicz AG; Lim R; Rogers H; Rosebraugh CJ; Chowdhury BA Ann Am Thorac Soc; 2018 Jan; 15(1):1-2. PubMed ID: 29020455 [TBL] [Abstract][Full Text] [Related] [Next] [New Search]