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4. A 45-year-old man with sudden cardiac death, cutaneous abnormalities and a rare desmoplakin mutation: a case report and literature review. Santos-Ferreira C; Baptista R; Teixeira T; Gonçalves L BMC Cardiovasc Disord; 2022 Feb; 22(1):41. PubMed ID: 35151254 [TBL] [Abstract][Full Text] [Related]
5. Novel desmoplakin mutation: juvenile biventricular cardiomyopathy with left ventricular non-compaction and acantholytic palmoplantar keratoderma. Williams T; Machann W; Kühler L; Hamm H; Müller-Höcker J; Zimmer M; Ertl G; Ritter O; Beer M; Schönberger J Clin Res Cardiol; 2011 Dec; 100(12):1087-93. PubMed ID: 21789513 [TBL] [Abstract][Full Text] [Related]
6. Arrhythmogenic dilated cardiomyopathy due to a novel mutation in the desmoplakin gene. Krishnamurthy S; Adhisivam B; Hamilton RM; Baskin B; Biswal N; Kumar M Indian J Pediatr; 2011 Jul; 78(7):866-9. PubMed ID: 21193976 [TBL] [Abstract][Full Text] [Related]
8. Case report of a Spanish patient with arrhythmogenic right ventricular cardiomyopathy and palmoplantar keratoderma without plakoglobin and desmoplakin gene modifications. Alonso-Orgaz S; Zamorano-León JJ; Fernandez-Arquero M; Villacastín J; Perez-Castellanos N; García-Torrent MJ; Macaya C; López Farré AJ Int J Cardiol; 2007 May; 118(2):275-7. PubMed ID: 17045679 [TBL] [Abstract][Full Text] [Related]
9. Early death from cardiomyopathy in a family with autosomal dominant striate palmoplantar keratoderma and woolly hair associated with a novel insertion mutation in desmoplakin. Norgett EE; Lucke TW; Bowers B; Munro CS; Leigh IM; Kelsell DP J Invest Dermatol; 2006 Jul; 126(7):1651-4. PubMed ID: 16628197 [No Abstract] [Full Text] [Related]
10. Loss of desmoplakin isoform I causes early onset cardiomyopathy and heart failure in a Naxos-like syndrome. Uzumcu A; Norgett EE; Dindar A; Uyguner O; Nisli K; Kayserili H; Sahin SE; Dupont E; Severs NJ; Leigh IM; Yuksel-Apak M; Kelsell DP; Wollnik B J Med Genet; 2006 Feb; 43(2):e5. PubMed ID: 16467215 [TBL] [Abstract][Full Text] [Related]
11. Palmoplantar Keratoderma and Woolly Hair Revealing Asymptomatic Arrhythmogenic Cardiomyopathy. Guerra L; Magliozzi M; Baban A; Di Mambro C; Di Zenzo G; Novelli A; El Hachem M; Zambruno G; Castiglia D Acta Derm Venereol; 2019 Jul; 99(9):831-832. PubMed ID: 31073624 [No Abstract] [Full Text] [Related]
12. Combination of palmoplantar keratoderma and hair shaft anomalies, the warning signal of severe arrhythmogenic cardiomyopathy: a systematic review on genetic desmosomal diseases. Polivka L; Bodemer C; Hadj-Rabia S J Med Genet; 2016 May; 53(5):289-95. PubMed ID: 26399581 [TBL] [Abstract][Full Text] [Related]
13. Novel homozygous mutation in DSP causing skin fragility-woolly hair syndrome: report of a large family and review of the desmoplakin-related phenotypes. Al-Owain M; Wakil S; Shareef F; Al-Fatani A; Hamadah E; Haider M; Al-Hindi H; Awaji A; Khalifa O; Baz B; Ramadhan R; Meyer B Clin Genet; 2011 Jul; 80(1):50-8. PubMed ID: 20738328 [TBL] [Abstract][Full Text] [Related]
14. De novo heterozygous desmoplakin mutations leading to Naxos-Carvajal disease. Keller DI; Stepowski D; Balmer C; Simon F; Guenthard J; Bauer F; Itin P; David N; Drouin-Garraud V; Fressart V Swiss Med Wkly; 2012; 142():w13670. PubMed ID: 22949226 [TBL] [Abstract][Full Text] [Related]
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16. A novel desmoplakin mutation causes dilated cardiomyopathy with palmoplantar keratoderma as an early clinical sign. Karvonen V; Harjama L; Heliö K; Kettunen K; Elomaa O; Koskenvuo JW; Kere J; Weckström S; Holmström M; Saarela J; Ranki A; Heliö T; Hannula-Jouppi K J Eur Acad Dermatol Venereol; 2022 Aug; 36(8):1349-1358. PubMed ID: 35445468 [TBL] [Abstract][Full Text] [Related]
17. Identification of a deletion in plakoglobin in arrhythmogenic right ventricular cardiomyopathy with palmoplantar keratoderma and woolly hair (Naxos disease). McKoy G; Protonotarios N; Crosby A; Tsatsopoulou A; Anastasakis A; Coonar A; Norman M; Baboonian C; Jeffery S; McKenna WJ Lancet; 2000 Jun; 355(9221):2119-24. PubMed ID: 10902626 [TBL] [Abstract][Full Text] [Related]
18. Left-Dominant Arrhythmogenic Cardiomyopathy, Palmoplantar Keratoderma, and Curly Hair Associated With a Rare Autosomal Dominant Truncating Variant in Desmoplakin. Reza N; Hoffman-Andrews L; Chowns JL; Marzolf A; Shields BE; Owens AT Circ Genom Precis Med; 2020 Oct; 13(5):557-559. PubMed ID: 33079602 [No Abstract] [Full Text] [Related]