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2. Lumacaftor (VX-809) restores the ability of CF macrophages to phagocytose and kill Pseudomonas aeruginosa. Barnaby R; Koeppen K; Nymon A; Hampton TH; Berwin B; Ashare A; Stanton BA Am J Physiol Lung Cell Mol Physiol; 2018 Mar; 314(3):L432-L438. PubMed ID: 29146575 [TBL] [Abstract][Full Text] [Related]
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9. The use of lumacaftor/ivacaftor to treat acute deterioration in paediatric cystic fibrosis. Hammond JA; Connett GJ Paediatr Respir Rev; 2018 Jun; 27():16-17. PubMed ID: 29914743 [TBL] [Abstract][Full Text] [Related]
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13. Two Small Molecules Restore Stability to a Subpopulation of the Cystic Fibrosis Transmembrane Conductance Regulator with the Predominant Disease-causing Mutation. Meng X; Wang Y; Wang X; Wrennall JA; Rimington TL; Li H; Cai Z; Ford RC; Sheppard DN J Biol Chem; 2017 Mar; 292(9):3706-3719. PubMed ID: 28087700 [TBL] [Abstract][Full Text] [Related]
14. Metabolomic responses to lumacaftor/ivacaftor in cystic fibrosis. Kopp BT; McCulloch S; Shrestha CL; Zhang S; Sarzynski L; Woodley FW; Hayes D Pediatr Pulmonol; 2018 May; 53(5):583-591. PubMed ID: 29461009 [TBL] [Abstract][Full Text] [Related]
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