BIOMARKERS

Molecular Biopsy of Human Tumors

- a resource for Precision Medicine *

201 related articles for article (PubMed ID: 30485852)

  • 1. Syntaxin 8 and the Endoplasmic Reticulum Processing of ΔF508-CFTR.
    Sabirzhanova I; Boinot C; Guggino WB; Cebotaru L
    Cell Physiol Biochem; 2018; 51(3):1489-1499. PubMed ID: 30485852
    [TBL] [Abstract][Full Text] [Related]  

  • 2. Human heat shock protein 105/110 kDa (Hsp105/110) regulates biogenesis and quality control of misfolded cystic fibrosis transmembrane conductance regulator at multiple levels.
    Saxena A; Banasavadi-Siddegowda YK; Fan Y; Bhattacharya S; Roy G; Giovannucci DR; Frizzell RA; Wang X
    J Biol Chem; 2012 Jun; 287(23):19158-70. PubMed ID: 22505710
    [TBL] [Abstract][Full Text] [Related]  

  • 3. Control of cystic fibrosis transmembrane conductance regulator membrane trafficking: not just from the endoplasmic reticulum to the Golgi.
    Farinha CM; Matos P; Amaral MD
    FEBS J; 2013 Sep; 280(18):4396-406. PubMed ID: 23773658
    [TBL] [Abstract][Full Text] [Related]  

  • 4. AAV exploits subcellular stress associated with inflammation, endoplasmic reticulum expansion, and misfolded proteins in models of cystic fibrosis.
    Johnson JS; Gentzsch M; Zhang L; Ribeiro CM; Kantor B; Kafri T; Pickles RJ; Samulski RJ
    PLoS Pathog; 2011 May; 7(5):e1002053. PubMed ID: 21625534
    [TBL] [Abstract][Full Text] [Related]  

  • 5. The CFTR-Associated Ligand Arrests the Trafficking of the Mutant ΔF508 CFTR Channel in the ER Contributing to Cystic Fibrosis.
    Bergbower E; Boinot C; Sabirzhanova I; Guggino W; Cebotaru L
    Cell Physiol Biochem; 2018; 45(2):639-655. PubMed ID: 29402832
    [TBL] [Abstract][Full Text] [Related]  

  • 6. Ribosomal Stalk Protein Silencing Partially Corrects the ΔF508-CFTR Functional Expression Defect.
    Veit G; Oliver K; Apaja PM; Perdomo D; Bidaud-Meynard A; Lin ST; Guo J; Icyuz M; Sorscher EJ; Hartman JL; Lukacs GL
    PLoS Biol; 2016 May; 14(5):e1002462. PubMed ID: 27168400
    [TBL] [Abstract][Full Text] [Related]  

  • 7. ERp29 regulates DeltaF508 and wild-type cystic fibrosis transmembrane conductance regulator (CFTR) trafficking to the plasma membrane in cystic fibrosis (CF) and non-CF epithelial cells.
    Suaud L; Miller K; Alvey L; Yan W; Robay A; Kebler C; Kreindler JL; Guttentag S; Hubbard MJ; Rubenstein RC
    J Biol Chem; 2011 Jun; 286(24):21239-53. PubMed ID: 21525008
    [TBL] [Abstract][Full Text] [Related]  

  • 8. Coupling cystic fibrosis to endoplasmic reticulum stress: Differential role of Grp78 and ATF6.
    Kerbiriou M; Le Drévo MA; Férec C; Trouvé P
    Biochim Biophys Acta; 2007 Dec; 1772(11-12):1236-49. PubMed ID: 18022401
    [TBL] [Abstract][Full Text] [Related]  

  • 9. Mechanistic Approaches to Improve Correction of the Most Common Disease-Causing Mutation in Cystic Fibrosis.
    Bali V; Lazrak A; Guroji P; Matalon S; Bebok Z
    PLoS One; 2016; 11(5):e0155882. PubMed ID: 27214033
    [TBL] [Abstract][Full Text] [Related]  

  • 10. Diffusional mobility of the cystic fibrosis transmembrane conductance regulator mutant, delta F508-CFTR, in the endoplasmic reticulum measured by photobleaching of GFP-CFTR chimeras.
    Haggie PM; Stanton BA; Verkman AS
    J Biol Chem; 2002 May; 277(19):16419-25. PubMed ID: 11877404
    [TBL] [Abstract][Full Text] [Related]  

  • 11. Role of calnexin in the ER quality control and productive folding of CFTR; differential effect of calnexin knockout on wild-type and DeltaF508 CFTR.
    Okiyoneda T; Niibori A; Harada K; Kohno T; Michalak M; Duszyk M; Wada I; Ikawa M; Shuto T; Suico MA; Kai H
    Biochim Biophys Acta; 2008 Sep; 1783(9):1585-94. PubMed ID: 18457676
    [TBL] [Abstract][Full Text] [Related]  

  • 12. The DeltaF508 mutation results in loss of CFTR function and mature protein in native human colon.
    Mall M; Kreda SM; Mengos A; Jensen TJ; Hirtz S; Seydewitz HH; Yankaskas J; Kunzelmann K; Riordan JR; Boucher RC
    Gastroenterology; 2004 Jan; 126(1):32-41. PubMed ID: 14699484
    [TBL] [Abstract][Full Text] [Related]  

  • 13. Selective inhibition of endoplasmic reticulum-associated degradation rescues DeltaF508-cystic fibrosis transmembrane regulator and suppresses interleukin-8 levels: therapeutic implications.
    Vij N; Fang S; Zeitlin PL
    J Biol Chem; 2006 Jun; 281(25):17369-17378. PubMed ID: 16621797
    [TBL] [Abstract][Full Text] [Related]  

  • 14. Protein processing and inflammatory signaling in Cystic Fibrosis: challenges and therapeutic strategies.
    Belcher CN; Vij N
    Curr Mol Med; 2010 Feb; 10(1):82-94. PubMed ID: 20205681
    [TBL] [Abstract][Full Text] [Related]  

  • 15. Functional cystic fibrosis transmembrane conductance regulator tagged with an epitope of the vesicular stomatis virus glycoprotein can be addressed to the apical domain of polarized cells.
    Costa de Beauregard MA; Edelman A; Chesnoy-Marchais D; Tondelier D; Lapillonne A; El Marjou F; Robine S; Louvard D
    Eur J Cell Biol; 2000 Nov; 79(11):795-802. PubMed ID: 11139142
    [TBL] [Abstract][Full Text] [Related]  

  • 16. Processing and function of CFTR-DeltaF508 are species-dependent.
    Ostedgaard LS; Rogers CS; Dong Q; Randak CO; Vermeer DW; Rokhlina T; Karp PH; Welsh MJ
    Proc Natl Acad Sci U S A; 2007 Sep; 104(39):15370-5. PubMed ID: 17873061
    [TBL] [Abstract][Full Text] [Related]  

  • 17. Syntaxin 6 and CAL mediate the degradation of the cystic fibrosis transmembrane conductance regulator.
    Cheng J; Cebotaru V; Cebotaru L; Guggino WB
    Mol Biol Cell; 2010 Apr; 21(7):1178-87. PubMed ID: 20130090
    [TBL] [Abstract][Full Text] [Related]  

  • 18. Ubiquitination and degradation of CFTR by the E3 ubiquitin ligase MARCH2 through its association with adaptor proteins CAL and STX6.
    Cheng J; Guggino W
    PLoS One; 2013; 8(6):e68001. PubMed ID: 23818989
    [TBL] [Abstract][Full Text] [Related]  

  • 19. Endogenous surface expression of ΔF508-CFTR mediates cAMP-stimulated Cl(-) current in CFTR(ΔF508/ΔF508) pig thyroid epithelial cells.
    Li Y; Ganta S; Fong P
    Exp Physiol; 2012 Jan; 97(1):115-24. PubMed ID: 21948195
    [TBL] [Abstract][Full Text] [Related]  

  • 20. Rescuing cystic fibrosis transmembrane conductance regulator (CFTR)-processing mutants by transcomplementation.
    Cormet-Boyaka E; Jablonsky M; Naren AP; Jackson PL; Muccio DD; Kirk KL
    Proc Natl Acad Sci U S A; 2004 May; 101(21):8221-6. PubMed ID: 15141088
    [TBL] [Abstract][Full Text] [Related]  

    [Next]    [New Search]
    of 11.