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6. Acute fatal presentation of ornithine transcarbamylase deficiency in a previously healthy male. Klein OD; Kostiner DR; Weisiger K; Moffatt E; Lindeman N; Goodman S; Tuchman M; Packman S Hepatol Int; 2008 Sep; 2(3):390-4. PubMed ID: 19669271 [TBL] [Abstract][Full Text] [Related]
7. Clinical outcomes and the mutation spectrum of the OTC gene in patients with ornithine transcarbamylase deficiency. Choi JH; Lee BH; Kim JH; Kim GH; Kim YM; Cho J; Cheon CK; Ko JM; Lee JH; Yoo HW J Hum Genet; 2015 Sep; 60(9):501-7. PubMed ID: 25994866 [TBL] [Abstract][Full Text] [Related]
8. Fatal cerebral edema from late-onset ornithine transcarbamylase deficiency in a juvenile male patient receiving valproic acid. Thakur V; Rupar CA; Ramsay DA; Singh R; Fraser DD Pediatr Crit Care Med; 2006 May; 7(3):273-6. PubMed ID: 16575347 [TBL] [Abstract][Full Text] [Related]
9. Late-onset ornithine transcarbamylase deficiency associated with hyperammonemia. Daijo K; Kawaoka T; Nakahara T; Nagaoki Y; Tsuge M; Hiramatsu A; Imamura M; Kawakami Y; Aikata H; Hara K; Tajima G; Kobayashi M; Chayama K Clin J Gastroenterol; 2017 Aug; 10(4):383-387. PubMed ID: 28597413 [TBL] [Abstract][Full Text] [Related]
10. Late-onset ornithine transcarbamylase deficiency: treatment and outcome of hyperammonemic crisis. Bergmann KR; McCabe J; Smith TR; Guillaume DJ; Sarafoglou K; Gupta S Pediatrics; 2014 Apr; 133(4):e1072-6. PubMed ID: 24616362 [TBL] [Abstract][Full Text] [Related]
11. Pathogenic variants of ornithine transcarbamylase deficiency: Nation-wide study in Japan and literature review. Kido J; Sugawara K; Sawada T; Matsumoto S; Nakamura K Front Genet; 2022; 13():952467. PubMed ID: 36303552 [TBL] [Abstract][Full Text] [Related]
12. Fatal coma in a young adult due to late-onset urea cycle deficiency presenting with a prolonged seizure: a case report. Alameri M; Shakra M; Alsaadi T J Med Case Rep; 2015 Nov; 9():267. PubMed ID: 26593089 [TBL] [Abstract][Full Text] [Related]
13. Corticosteroid suppresses urea-cycle-related gene expressions in ornithine transcarbamylase deficiency. Imoto K; Tanaka M; Goya T; Aoyagi T; Takahashi M; Kurokawa M; Tashiro S; Kato M; Kohjima M; Ogawa Y BMC Gastroenterol; 2022 Mar; 22(1):144. PubMed ID: 35346058 [TBL] [Abstract][Full Text] [Related]
14. Female heterozygotes for the hypomorphic R40H mutation can have ornithine transcarbamylase deficiency and present in early adolescence: a case report and review of the literature. Pinner JR; Freckmann ML; Kirk EP; Yoshino M J Med Case Rep; 2010 Nov; 4():361. PubMed ID: 21070677 [TBL] [Abstract][Full Text] [Related]
15. Variable disease manifestations and metabolic management within a single family affected by ornithine transcarbamylase deficiency. Baker J; Hitchins L; Vucko E; Havens K; Becker K; Arduini K Mol Genet Metab Rep; 2022 Dec; 33(Suppl 1):100906. PubMed ID: 36620388 [TBL] [Abstract][Full Text] [Related]
16. OTC gene in ornithine transcarbamylase deficiency: clinical course and mutational spectrum in seven Korean patients. Lee JH; Kim GH; Yoo HW; Cheon CK Pediatr Neurol; 2014 Sep; 51(3):354-359.e1. PubMed ID: 25011434 [TBL] [Abstract][Full Text] [Related]
17. Challenges of managing ornithine transcarbamylase deficiency in female heterozygotes. Feigenbaum A Mol Genet Metab Rep; 2022 Dec; 33(Suppl 1):100941. PubMed ID: 36620389 [TBL] [Abstract][Full Text] [Related]
18. Posterior fossa syndrome in a patient with an ornithine transcarbamylase deficiency. Nedermeijer SC; van den Hout J; Geleijns C; de Klerk H; Catsman-Berrevoets CE Eur J Paediatr Neurol; 2015 May; 19(3):364-6. PubMed ID: 25687292 [TBL] [Abstract][Full Text] [Related]
19. Ammonia and coma - a case report of late onset hemizygous ornithine carbamyltransferase deficiency in 68-year-old female. Marquetand J; Freisinger P; Lindig T; Euler S; Gasser M; Overkamp D BMC Neurol; 2020 Apr; 20(1):118. PubMed ID: 32252669 [TBL] [Abstract][Full Text] [Related]
20. Successful early management of a female patient with a metabolic stroke due to ornithine transcarbamylase deficiency. Tummolo A; Favia V; Bellantuono R; Bellino V; Ranieri A; Morrone A; De Palo T; Papadia F Pediatr Emerg Care; 2013 May; 29(5):656-8. PubMed ID: 23640148 [TBL] [Abstract][Full Text] [Related] [Next] [New Search]