These tools will no longer be maintained as of December 31, 2024. Archived website can be found here. PubMed4Hh GitHub repository can be found here. Contact NLM Customer Service if you have questions.
5. Using the C14:1/Medium-Chain Acylcarnitine Ratio Instead of C14:1 to Reduce False-Positive Results for Very-Long-Chain Acyl-CoA Dehydrogenase Deficiency in Newborn Screening in Japan. Tajima G; Aisaki J; Hara K; Tsumura M; Kagawa R; Sakura F; Sasai H; Yuasa M; Shigematsu Y; Okada S Int J Neonatal Screen; 2024 Feb; 10(1):. PubMed ID: 38390979 [TBL] [Abstract][Full Text] [Related]
6. Infants suspected to have very-long chain acyl-CoA dehydrogenase deficiency from newborn screening. Merritt JL; Vedal S; Abdenur JE; Au SM; Barshop BA; Feuchtbaum L; Harding CO; Hermerath C; Lorey F; Sesser DE; Thompson JD; Yu A Mol Genet Metab; 2014 Apr; 111(4):484-92. PubMed ID: 24503138 [TBL] [Abstract][Full Text] [Related]
7. Sequencing from dried blood spots in infants with "false positive" newborn screen for MCAD deficiency. McCandless SE; Chandrasekar R; Linard S; Kikano S; Rice L Mol Genet Metab; 2013 Jan; 108(1):51-5. PubMed ID: 23151387 [TBL] [Abstract][Full Text] [Related]
8. Diagnosis of very long chain acyl-dehydrogenase deficiency from an infant's newborn screening card. Wood JC; Magera MJ; Rinaldo P; Seashore MR; Strauss AW; Friedman A Pediatrics; 2001 Jul; 108(1):E19. PubMed ID: 11433098 [TBL] [Abstract][Full Text] [Related]
9. Clinical and biochemical outcome of patients with very long-chain acyl-CoA dehydrogenase deficiency. Rovelli V; Manzoni F; Viau K; Pasquali M; Longo N Mol Genet Metab; 2019 May; 127(1):64-73. PubMed ID: 31031081 [TBL] [Abstract][Full Text] [Related]
10. False positive cases of elevated tetradecenoyl carnitine in newborn mass screening showed significant loss of body weight. Bo R; Awano H; Nishida K; Fujioka K; Nishiyama A; Miyake O; Iijima K Mol Genet Metab Rep; 2020 Sep; 24():100634. PubMed ID: 32775213 [TBL] [Abstract][Full Text] [Related]
11. Characterization of exonic variants of uncertain significance in very long-chain acyl-CoA dehydrogenase identified through newborn screening. D'Annibale OM; Koppes EA; Sethuraman M; Bloom K; Mohsen AW; Vockley J J Inherit Metab Dis; 2022 May; 45(3):529-540. PubMed ID: 35218577 [TBL] [Abstract][Full Text] [Related]
12. Elevations of C14:1 and C14:2 Plasma Acylcarnitines in Fasted Children: A Diagnostic Dilemma. Burrage LC; Miller MJ; Wong LJ; Kennedy AD; Sutton VR; Sun Q; Elsea SH; Graham BH J Pediatr; 2016 Feb; 169():208-13.e2. PubMed ID: 26602010 [TBL] [Abstract][Full Text] [Related]
13. New Ratios for Performance Improvement for Identifying Acyl-CoA Dehydrogenase Deficiencies in Expanded Newborn Screening: A Retrospective Study. Wang B; Zhang Q; Gao A; Wang Q; Ma J; Li H; Wang T Front Genet; 2019; 10():811. PubMed ID: 31620161 [TBL] [Abstract][Full Text] [Related]
14. Very Long-Chain Acyl-CoA Dehydrogenase Deficiency: High Incidence of Detected Patients With Expanded Newborn Screening Program. Remec ZI; Groselj U; Drole Torkar A; Zerjav Tansek M; Cuk V; Perko D; Ulaga B; Lipovec N; Debeljak M; Kovac J; Battelino T; Repic Lampret B Front Genet; 2021; 12():648493. PubMed ID: 33986768 [TBL] [Abstract][Full Text] [Related]
15. Recurrent ACADVL molecular findings in individuals with a positive newborn screen for very long chain acyl-coA dehydrogenase (VLCAD) deficiency in the United States. Miller MJ; Burrage LC; Gibson JB; Strenk ME; Lose EJ; Bick DP; Elsea SH; Sutton VR; Sun Q; Graham BH; Craigen WJ; Zhang VW; Wong LJ Mol Genet Metab; 2015 Nov; 116(3):139-45. PubMed ID: 26385305 [TBL] [Abstract][Full Text] [Related]
16. Outcomes and genotype-phenotype correlations in 52 individuals with VLCAD deficiency diagnosed by NBS and enrolled in the IBEM-IS database. Pena LD; van Calcar SC; Hansen J; Edick MJ; Walsh Vockley C; Leslie N; Cameron C; Mohsen AW; Berry SA; Arnold GL; Vockley J; Mol Genet Metab; 2016 Aug; 118(4):272-81. PubMed ID: 27209629 [TBL] [Abstract][Full Text] [Related]
18. Tissue-specific strategies of the very-long chain acyl-CoA dehydrogenase-deficient (VLCAD-/-) mouse to compensate a defective fatty acid β-oxidation. Tucci S; Herebian D; Sturm M; Seibt A; Spiekerkoetter U PLoS One; 2012; 7(9):e45429. PubMed ID: 23024820 [TBL] [Abstract][Full Text] [Related]
19. Lethal Undiagnosed Very Long-Chain Acyl-CoA Dehydrogenase Deficiency with Mild C14-Acylcarnitine Abnormalities on Newborn Screening. Spiekerkoetter U; Mueller M; Sturm M; Hofmann M; Schneider DT JIMD Rep; 2012; 6():113-5. PubMed ID: 23430948 [TBL] [Abstract][Full Text] [Related]
20. A novel tandem mass spectrometry method for rapid confirmation of medium- and very long-chain acyl-CoA dehydrogenase deficiency in newborns. ter Veld F; Mueller M; Kramer S; Haussmann U; Herebian D; Mayatepek E; Laryea MD; Primassin S; Spiekerkoetter U PLoS One; 2009 Jul; 4(7):e6449. PubMed ID: 19649258 [TBL] [Abstract][Full Text] [Related] [Next] [New Search]