These tools will no longer be maintained as of December 31, 2024. Archived website can be found here. PubMed4Hh GitHub repository can be found here. Contact NLM Customer Service if you have questions.
182 related articles for article (PubMed ID: 30797798)
1. Pathophysiological characterization of MERRF patient-specific induced neurons generated by direct reprogramming. Villanueva-Paz M; Povea-Cabello S; Villalón-García I; Suárez-Rivero JM; Álvarez-Córdoba M; de la Mata M; Talaverón-Rey M; Jackson S; Sánchez-Alcázar JA Biochim Biophys Acta Mol Cell Res; 2019 May; 1866(5):861-881. PubMed ID: 30797798 [TBL] [Abstract][Full Text] [Related]
2. Parkin-mediated mitophagy and autophagy flux disruption in cellular models of MERRF syndrome. Villanueva-Paz M; Povea-Cabello S; Villalón-García I; Álvarez-Córdoba M; Suárez-Rivero JM; Talaverón-Rey M; Jackson S; Falcón-Moya R; Rodríguez-Moreno A; Sánchez-Alcázar JA Biochim Biophys Acta Mol Basis Dis; 2020 Jun; 1866(6):165726. PubMed ID: 32061767 [TBL] [Abstract][Full Text] [Related]
3. Altered mitochondrial function in fibroblasts containing MELAS or MERRF mitochondrial DNA mutations. James AM; Wei YH; Pang CY; Murphy MP Biochem J; 1996 Sep; 318 ( Pt 2)(Pt 2):401-7. PubMed ID: 8809026 [TBL] [Abstract][Full Text] [Related]
4. Mitochondrial impairment and synaptic dysfunction are associated with neurological defects in iPSCs-derived cortical neurons of MERRF patients. Wu YT; Tay HY; Yang JT; Liao HH; Ma YS; Wei YH J Biomed Sci; 2023 Aug; 30(1):70. PubMed ID: 37605213 [TBL] [Abstract][Full Text] [Related]
5. Recovery of MERRF fibroblasts and cybrids pathophysiology by coenzyme Q10. De la Mata M; Garrido-Maraver J; Cotán D; Cordero MD; Oropesa-Ávila M; Izquierdo LG; De Miguel M; Lorite JB; Infante ER; Ybot P; Jackson S; Sánchez-Alcázar JA Neurotherapeutics; 2012 Apr; 9(2):446-63. PubMed ID: 22354625 [TBL] [Abstract][Full Text] [Related]
6. Nuclear DNA-encoded tRNAs targeted into mitochondria can rescue a mitochondrial DNA mutation associated with the MERRF syndrome in cultured human cells. Kolesnikova OA; Entelis NS; Jacquin-Becker C; Goltzene F; Chrzanowska-Lightowlers ZM; Lightowlers RN; Martin RP; Tarassov I Hum Mol Genet; 2004 Oct; 13(20):2519-34. PubMed ID: 15317755 [TBL] [Abstract][Full Text] [Related]
7. Rapamycin rescues mitochondrial dysfunction in cells carrying the m.8344A > G mutation in the mitochondrial tRNA Capristo M; Del Dotto V; Tropeano CV; Fiorini C; Caporali L; La Morgia C; Valentino ML; Montopoli M; Carelli V; Maresca A Mol Med; 2022 Aug; 28(1):90. PubMed ID: 35922766 [TBL] [Abstract][Full Text] [Related]
8. Identification of new variants in MTRNR1 and MTRNR2 genes using whole mitochondrial genome sequencing in a Taiwanese family with MERRF (myoclonic epilepsy with ragged-red fibers) syndrome. Wu YT; Huang SC; Shiao YM; Syu WC; Wei YH; Hsu YC Hear Res; 2023 Oct; 438():108876. PubMed ID: 37683310 [TBL] [Abstract][Full Text] [Related]
9. Distal weakness with respiratory insufficiency caused by the m.8344A > G "MERRF" mutation. Blakely EL; Alston CL; Lecky B; Chakrabarti B; Falkous G; Turnbull DM; Taylor RW; Gorman GS Neuromuscul Disord; 2014 Jun; 24(6):533-6. PubMed ID: 24792523 [TBL] [Abstract][Full Text] [Related]
10. Platelet-mediated transformation of mtDNA-less human cells: analysis of phenotypic variability among clones from normal individuals--and complementation behavior of the tRNALys mutation causing myoclonic epilepsy and ragged red fibers. Chomyn A; Lai ST; Shakeley R; Bresolin N; Scarlato G; Attardi G Am J Hum Genet; 1994 Jun; 54(6):966-74. PubMed ID: 8198140 [TBL] [Abstract][Full Text] [Related]
11. Generation of an induced pluripotent stem cell (iPSC) line from a 40-year-old patient with the A8344G mutation of mitochondrial DNA and MERRF (myoclonic epilepsy with ragged red fibers) syndrome. Wu YT; Hsu YH; Huang CY; Ho MC; Cheng YC; Wen CH; Ko HW; Lu HE; Chen YC; Tsai CL; Hsu YC; Wei YH; Hsieh PCH Stem Cell Res; 2018 Mar; 27():10-14. PubMed ID: 29288969 [TBL] [Abstract][Full Text] [Related]
12. Impaired ROS Scavenging System in Human Induced Pluripotent Stem Cells Generated from Patients with MERRF Syndrome. Chou SJ; Tseng WL; Chen CT; Lai YF; Chien CS; Chang YL; Lee HC; Wei YH; Chiou SH Sci Rep; 2016 Mar; 6():23661. PubMed ID: 27025901 [TBL] [Abstract][Full Text] [Related]
13. Decreased ATP synthesis is phenotypically expressed during increased energy demand in fibroblasts containing mitochondrial tRNA mutations. James AM; Sheard PW; Wei YH; Murphy MP Eur J Biochem; 1999 Jan; 259(1-2):462-9. PubMed ID: 9914528 [TBL] [Abstract][Full Text] [Related]
14. Regionalized pathology correlates with augmentation of mtDNA copy numbers in a patient with myoclonic epilepsy with ragged-red fibers (MERRF-syndrome). Brinckmann A; Weiss C; Wilbert F; von Moers A; Zwirner A; Stoltenburg-Didinger G; Wilichowski E; Schuelke M PLoS One; 2010 Oct; 5(10):e13513. PubMed ID: 20976001 [TBL] [Abstract][Full Text] [Related]
15. Mitochondrial DNA mutation-elicited oxidative stress, oxidative damage, and altered gene expression in cultured cells of patients with MERRF syndrome. Wu SB; Ma YS; Wu YT; Chen YC; Wei YH Mol Neurobiol; 2010 Jun; 41(2-3):256-66. PubMed ID: 20411357 [TBL] [Abstract][Full Text] [Related]
16. Pathogenetic aspects of the A8344G mutation of mitochondrial DNA associated with MERRF syndrome and multiple symmetric lipomas. Larsson NG; Tulinius MH; Holme E; Oldfors A Muscle Nerve Suppl; 1995; 3():S102-6. PubMed ID: 7603509 [TBL] [Abstract][Full Text] [Related]
17. The Bacterial Protein CNF1 as a Potential Therapeutic Strategy against Mitochondrial Diseases: A Pilot Study. Fabbri A; Travaglione S; Maroccia Z; Guidotti M; Pierri CL; Primiano G; Servidei S; Loizzo S; Fiorentini C Int J Mol Sci; 2018 Jun; 19(7):. PubMed ID: 29933571 [TBL] [Abstract][Full Text] [Related]
18. [Molecular genetic analysis for myoclonus epilepsy associated with ragged-red fibers (MERRF)]. Tanno Y; Yoneda M; Tanaka K; Tsuji S Nihon Rinsho; 1993 Sep; 51(9):2379-85. PubMed ID: 8411716 [TBL] [Abstract][Full Text] [Related]
19. MERRF/MELAS overlap syndrome: a double pathogenic mutation in mitochondrial tRNA genes. Nakamura M; Yabe I; Sudo A; Hosoki K; Yaguchi H; Saitoh S; Sasaki H J Med Genet; 2010 Oct; 47(10):659-64. PubMed ID: 20610441 [TBL] [Abstract][Full Text] [Related]
20. Myoclonus epilepsy associated with ragged-red fibers: a G-to-A mutation at nucleotide pair 8363 in mitochondrial tRNA(Lys) in two families. Ozawa M; Nishino I; Horai S; Nonaka I; Goto YI Muscle Nerve; 1997 Mar; 20(3):271-8. PubMed ID: 9052804 [TBL] [Abstract][Full Text] [Related] [Next] [New Search]