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3. POLG mutations cause decreased mitochondrial DNA repopulation rates following induced depletion in human fibroblasts. Stewart JD; Schoeler S; Sitarz KS; Horvath R; Hallmann K; Pyle A; Yu-Wai-Man P; Taylor RW; Samuels DC; Kunz WS; Chinnery PF Biochim Biophys Acta; 2011 Mar; 1812(3):321-5. PubMed ID: 21138766 [TBL] [Abstract][Full Text] [Related]
4. Mammalian ribonucleotide reductase subunit p53R2 is required for mitochondrial DNA replication and DNA repair in quiescent cells. Pontarin G; Ferraro P; Bee L; Reichard P; Bianchi V Proc Natl Acad Sci U S A; 2012 Aug; 109(33):13302-7. PubMed ID: 22847445 [TBL] [Abstract][Full Text] [Related]
5. Association of novel POLG mutations and multiple mitochondrial DNA deletions with variable clinical phenotypes in a Spanish population. González-Vioque E; Blázquez A; Fernández-Moreira D; Bornstein B; Bautista J; Arpa J; Navarro C; Campos Y; Fernández-Moreno MA; Garesse R; Arenas J; Martín MA Arch Neurol; 2006 Jan; 63(1):107-11. PubMed ID: 16401742 [TBL] [Abstract][Full Text] [Related]
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9. Combined use of Saccharomyces cerevisiae, Caenorhabditis elegans and patient fibroblasts leads to the identification of clofilium tosylate as a potential therapeutic chemical against POLG-related diseases. Pitayu L; Baruffini E; Rodier C; Rötig A; Lodi T; Delahodde A Hum Mol Genet; 2016 Feb; 25(4):715-27. PubMed ID: 26692522 [TBL] [Abstract][Full Text] [Related]
10. The molecular characterisation of mitochondrial DNA deficient oocytes using a pig model. Tsai TS; Tyagi S; St John JC Hum Reprod; 2018 May; 33(5):942-953. PubMed ID: 29546367 [TBL] [Abstract][Full Text] [Related]
11. No correlation between mtDNA amount and methylation levels at the CpG island of Steffann J; Pouliet A; Adjal H; Bole C; Fourrage C; Martinovic J; Rolland-Galmiche L; Rotig A; Tores F; Munnich A; Bonnefont JP J Med Genet; 2017 May; 54(5):324-329. PubMed ID: 28069933 [TBL] [Abstract][Full Text] [Related]
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13. In vivo functional analysis of the human mitochondrial DNA polymerase POLG expressed in cultured human cells. Spelbrink JN; Toivonen JM; Hakkaart GA; Kurkela JM; Cooper HM; Lehtinen SK; Lecrenier N; Back JW; Speijer D; Foury F; Jacobs HT J Biol Chem; 2000 Aug; 275(32):24818-28. PubMed ID: 10827171 [TBL] [Abstract][Full Text] [Related]
14. Depletion of the other genome-mitochondrial DNA depletion syndromes in humans. Elpeleg O; Mandel H; Saada A J Mol Med (Berl); 2002 Jul; 80(7):389-96. PubMed ID: 12110944 [TBL] [Abstract][Full Text] [Related]
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18. Mitochondrial DNA depletion and fatal infantile hepatic failure due to mutations in the mitochondrial polymerase γ (POLG) gene: a combined morphological/enzyme histochemical and immunocytochemical/biochemical and molecular genetic study. Müller-Höcker J; Horvath R; Schäfer S; Hessel H; Müller-Felber W; Kühr J; Copeland WC; Seibel P J Cell Mol Med; 2011 Feb; 15(2):445-56. PubMed ID: 19538466 [TBL] [Abstract][Full Text] [Related]
19. Increased burden of mitochondrial DNA deletions and point mutations in early-onset age-related hearing loss in mitochondrial mutator mice. Kim MJ; Haroon S; Chen GD; Ding D; Wanagat J; Liu L; Zhang Y; White K; Park HJ; Han C; Boyd K; Caicedo I; Evans K; Linser PJ; Tanokura M; Prolla T; Salvi R; Vermulst M; Someya S Exp Gerontol; 2019 Oct; 125():110675. PubMed ID: 31344454 [TBL] [Abstract][Full Text] [Related]
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