These tools will no longer be maintained as of December 31, 2024. Archived website can be found here. PubMed4Hh GitHub repository can be found here. Contact NLM Customer Service if you have questions.
191 related articles for article (PubMed ID: 30928643)
1. Upregulation of tripeptidyl-peptidase 1 by 3-hydroxy-(2,2)-dimethyl butyrate, a brain endogenous ligand of PPARα: Implications for late-infantile Batten disease therapy. Chakrabarti S; Chandra S; Roy A; Dasarathi S; Kundu M; Pahan K Neurobiol Dis; 2019 Jul; 127():362-373. PubMed ID: 30928643 [TBL] [Abstract][Full Text] [Related]
2. Gemfibrozil and fenofibrate, Food and Drug Administration-approved lipid-lowering drugs, up-regulate tripeptidyl-peptidase 1 in brain cells via peroxisome proliferator-activated receptor α: implications for late infantile Batten disease therapy. Ghosh A; Corbett GT; Gonzalez FJ; Pahan K J Biol Chem; 2012 Nov; 287(46):38922-35. PubMed ID: 22989886 [TBL] [Abstract][Full Text] [Related]
3. Gemfibrozil, food and drug administration-approved lipid-lowering drug, increases longevity in mouse model of late infantile neuronal ceroid lipofuscinosis. Ghosh A; Rangasamy SB; Modi KK; Pahan K J Neurochem; 2017 May; 141(3):423-435. PubMed ID: 28199020 [TBL] [Abstract][Full Text] [Related]
4. Lysosomal protein thermal stability does not correlate with cellular half-life: global observations and a case study of tripeptidyl-peptidase 1. Collier AM; Nemtsova Y; Kuber N; Banach-Petrosky W; Modak A; Sleat DE; Nanda V; Lobel P Biochem J; 2020 Feb; 477(3):727-745. PubMed ID: 31957806 [TBL] [Abstract][Full Text] [Related]
5. A novel CLN2/TPP1 mutation in a patient with late infantile neuronal ceroid lipofuscinosis. Yu F; Liu XM; Chen YH; Zhang SQ; Wang K Neurol Sci; 2015 Oct; 36(10):1917-9. PubMed ID: 26032578 [No Abstract] [Full Text] [Related]
6. Enzyme replacement therapy attenuates disease progression in a canine model of late-infantile neuronal ceroid lipofuscinosis (CLN2 disease). Katz ML; Coates JR; Sibigtroth CM; Taylor JD; Carpentier M; Young WM; Wininger FA; Kennedy D; Vuillemenot BR; O'Neill CA J Neurosci Res; 2014 Nov; 92(11):1591-8. PubMed ID: 24938720 [TBL] [Abstract][Full Text] [Related]
12. Diagnosis of neuronal ceroid lipofuscinosis type 2 (CLN2 disease): Expert recommendations for early detection and laboratory diagnosis. Fietz M; AlSayed M; Burke D; Cohen-Pfeffer J; Cooper JD; Dvořáková L; Giugliani R; Izzo E; Jahnová H; Lukacs Z; Mole SE; Noher de Halac I; Pearce DA; Poupetova H; Schulz A; Specchio N; Xin W; Miller N Mol Genet Metab; 2016 Sep; 119(1-2):160-7. PubMed ID: 27553878 [TBL] [Abstract][Full Text] [Related]
13. Intrathecal tripeptidyl-peptidase 1 reduces lysosomal storage in a canine model of late infantile neuronal ceroid lipofuscinosis. Vuillemenot BR; Katz ML; Coates JR; Kennedy D; Tiger P; Kanazono S; Lobel P; Sohar I; Xu S; Cahayag R; Keve S; Koren E; Bunting S; Tsuruda LS; O'Neill CA Mol Genet Metab; 2011 Nov; 104(3):325-37. PubMed ID: 21784683 [TBL] [Abstract][Full Text] [Related]
14. Intraventricular enzyme replacement improves disease phenotypes in a mouse model of late infantile neuronal ceroid lipofuscinosis. Chang M; Cooper JD; Sleat DE; Cheng SH; Dodge JC; Passini MA; Lobel P; Davidson BL Mol Ther; 2008 Apr; 16(4):649-56. PubMed ID: 18362923 [TBL] [Abstract][Full Text] [Related]
15. Neuronal ceroid lipofuscinosis type CLN2: a new rationale for the construction of phenotypic subgroups based on a survey of 25 cases in South America. Kohan R; Carabelos MN; Xin W; Sims K; Guelbert N; Cismondi IA; Pons P; Alonso GI; Troncoso M; Witting S; Pearce DA; Dodelson de Kremer R; Oller-Ramírez AM; Noher de Halac I Gene; 2013 Mar; 516(1):114-21. PubMed ID: 23266810 [TBL] [Abstract][Full Text] [Related]
17. Glial fibrillary acidic protein is elevated in the lysosomal storage disease classical late-infantile neuronal ceroid lipofuscinosis, but is not a component of the storage material. Xu S; Sleat DE; Jadot M; Lobel P Biochem J; 2010 May; 428(3):355-62. PubMed ID: 20370715 [TBL] [Abstract][Full Text] [Related]
18. Intraventricular Cerliponase Alfa Treatment in a Patient with Advanced Neuronal Ceroid Lipofuscinosis Type 2. Nakashima S; Hamada M; Kimura T; Tanifuji S; Takahashi A; Yashita D; Kakimoto Y; Matsukawa T; Ishiura H; Toda T Intern Med; 2024 Jun; 63(12):1807-1812. PubMed ID: 37926545 [TBL] [Abstract][Full Text] [Related]
19. TPP1 Delivery to Lysosomes with Extracellular Vesicles and their Enhanced Brain Distribution in the Animal Model of Batten Disease. Haney MJ; Klyachko NL; Harrison EB; Zhao Y; Kabanov AV; Batrakova EV Adv Healthc Mater; 2019 Jun; 8(11):e1801271. PubMed ID: 30997751 [TBL] [Abstract][Full Text] [Related]
20. Large-volume intrathecal enzyme delivery increases survival of a mouse model of late infantile neuronal ceroid lipofuscinosis. Xu S; Wang L; El-Banna M; Sohar I; Sleat DE; Lobel P Mol Ther; 2011 Oct; 19(10):1842-8. PubMed ID: 21730969 [TBL] [Abstract][Full Text] [Related] [Next] [New Search]