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7. Senataxin helicase, the causal gene defect in ALS4, is a significant modifier of C9orf72 ALS G4C2 and arginine-containing dipeptide repeat toxicity. Bennett CL; Dastidar S; Arnold FJ; McKinstry SU; Stockford C; Freibaum BD; Sopher BL; Wu M; Seidner G; Joiner W; Taylor JP; West RJH; La Spada AR Acta Neuropathol Commun; 2023 Oct; 11(1):164. PubMed ID: 37845749 [TBL] [Abstract][Full Text] [Related]
8. Impaired ribosome-associated quality control of C9orf72 arginine-rich dipeptide-repeat proteins. Viera Ortiz AP; Cajka G; Olatunji OA; Mikytuck B; Shalem O; Lee EB Brain; 2023 Jul; 146(7):2897-2912. PubMed ID: 36516294 [TBL] [Abstract][Full Text] [Related]
9. C9orf72 Dipeptide Repeats Cause Selective Neurodegeneration and Cell-Autonomous Excitotoxicity in Xu W; Xu J J Neurosci; 2018 Aug; 38(35):7741-7752. PubMed ID: 30037833 [TBL] [Abstract][Full Text] [Related]
10. Sense-encoded poly-GR dipeptide repeat proteins correlate to neurodegeneration and uniquely co-localize with TDP-43 in dendrites of repeat-expanded C9orf72 amyotrophic lateral sclerosis. Saberi S; Stauffer JE; Jiang J; Garcia SD; Taylor AE; Schulte D; Ohkubo T; Schloffman CL; Maldonado M; Baughn M; Rodriguez MJ; Pizzo D; Cleveland D; Ravits J Acta Neuropathol; 2018 Mar; 135(3):459-474. PubMed ID: 29196813 [TBL] [Abstract][Full Text] [Related]
11. Expression of C9orf72 hexanucleotide repeat expansion leads to formation of RNA foci and dipeptide repeat proteins but does not influence autophagy or proteasomal function in neuronal cells. Leskelä S; Huber N; Hoffmann D; Rostalski H; Remes AM; Takalo M; Hiltunen M; Haapasalo A Biochim Biophys Acta Mol Cell Res; 2021 Jun; 1868(7):119021. PubMed ID: 33775797 [TBL] [Abstract][Full Text] [Related]
12. Sense and antisense RNA are not toxic in Drosophila models of C9orf72-associated ALS/FTD. Moens TG; Mizielinska S; Niccoli T; Mitchell JS; Thoeng A; Ridler CE; Grönke S; Esser J; Heslegrave A; Zetterberg H; Partridge L; Isaacs AM Acta Neuropathol; 2018 Mar; 135(3):445-457. PubMed ID: 29380049 [TBL] [Abstract][Full Text] [Related]
13. Evidence that C9ORF72 Dipeptide Repeat Proteins Associate with U2 snRNP to Cause Mis-splicing in ALS/FTD Patients. Yin S; Lopez-Gonzalez R; Kunz RC; Gangopadhyay J; Borufka C; Gygi SP; Gao FB; Reed R Cell Rep; 2017 Jun; 19(11):2244-2256. PubMed ID: 28614712 [TBL] [Abstract][Full Text] [Related]
14. C9orf72 arginine-rich dipeptide proteins interact with ribosomal proteins in vivo to induce a toxic translational arrest that is rescued by eIF1A. Moens TG; Niccoli T; Wilson KM; Atilano ML; Birsa N; Gittings LM; Holbling BV; Dyson MC; Thoeng A; Neeves J; Glaria I; Yu L; Bussmann J; Storkebaum E; Pardo M; Choudhary JS; Fratta P; Partridge L; Isaacs AM Acta Neuropathol; 2019 Mar; 137(3):487-500. PubMed ID: 30604225 [TBL] [Abstract][Full Text] [Related]
15. Proline-arginine poly-dipeptide encoded by the C9orf72 repeat expansion inhibits adenosine deaminase acting on RNA. Suzuki H; Matsuoka M J Neurochem; 2021 Aug; 158(3):753-765. PubMed ID: 34081786 [TBL] [Abstract][Full Text] [Related]
16. Sulfated disaccharide protects membrane and DNA damages from arginine-rich dipeptide repeats in ALS. Chang YJ; Lin KT; Shih O; Yang CH; Chuang CY; Fang MH; Lai WB; Lee YC; Kuo HC; Hung SC; Yao CK; Jeng US; Chen YR Sci Adv; 2024 Feb; 10(8):eadj0347. PubMed ID: 38394210 [TBL] [Abstract][Full Text] [Related]
17. C9orf72-associated dipeptide protein repeats form A11-positive oligomers in amyotrophic lateral sclerosis and frontotemporal dementia. Bhatt N; Puangmalai N; Sengupta U; Jerez C; Kidd M; Gandhi S; Kayed R J Biol Chem; 2024 Feb; 300(2):105628. PubMed ID: 38295729 [TBL] [Abstract][Full Text] [Related]
18. DDX3X overexpression decreases dipeptide repeat proteins in a mouse model of C9ORF72-ALS/FTD. Fu X; Zhang Z; Hayes LR; Wright N; Asbury J; Li S; Ye Y; Sun S Exp Neurol; 2024 Jun; 376():114768. PubMed ID: 38556190 [TBL] [Abstract][Full Text] [Related]