239 related articles for article (PubMed ID: 3094585)
1. Metabolism of galactosylceramide in the twitcher mouse, an animal model of human globoid cell leukodystrophy.
Kobayashi T; Shinnoh N; Kuroiwa Y
Biochim Biophys Acta; 1986 Nov; 879(2):215-20. PubMed ID: 3094585
[TBL] [Abstract][Full Text] [Related]
2. Hydrolysis of galactosylceramide is catalyzed by two genetically distinct acid beta-galactosidases.
Kobayashi T; Shinnoh N; Goto I; Kuroiwa Y
J Biol Chem; 1985 Dec; 260(28):14982-7. PubMed ID: 3934152
[TBL] [Abstract][Full Text] [Related]
3. Hematopoietic cell transplantation in murine globoid cell leukodystrophy (the twitcher mouse): effects on levels of galactosylceramidase, psychosine, and galactocerebrosides.
Ichioka T; Kishimoto Y; Brennan S; Santos GW; Yeager AM
Proc Natl Acad Sci U S A; 1987 Jun; 84(12):4259-63. PubMed ID: 2884662
[TBL] [Abstract][Full Text] [Related]
4. Galactosylceramide- and lactosylceramide-loading studies in cultured fibroblasts from normal individuals and patients with globoid cell leukodystrophy (Krabbe's disease) and GM1-gangliosidosis.
Kobayashi T; Shinnoh N; Goto I; Kuroiwa Y; Okawauchi M; Sugihara G; Tanaka M
Biochim Biophys Acta; 1985 Jul; 835(3):456-64. PubMed ID: 3926002
[TBL] [Abstract][Full Text] [Related]
5. Globoid cell leukodystrophy (Krabbe's disease). Metabolic studies with cultured fibroblasts.
Tanaka H; Suzuki K
J Neurol Sci; 1978 Oct; 38(3):409-19. PubMed ID: 731265
[TBL] [Abstract][Full Text] [Related]
6. Specificity of galactosylceramidase activation by phosphatidylserine.
Hanada E; Suzuki K
Biochim Biophys Acta; 1980 Aug; 619(2):396-402. PubMed ID: 6773584
[TBL] [Abstract][Full Text] [Related]
7. Abnormal accumulation of galactosylceramide in the kidney of twitcher mouse.
Igisu H; Takahashi H; Suzuki K; Suzuki K
Biochem Biophys Res Commun; 1983 Feb; 110(3):940-4. PubMed ID: 6838562
[TBL] [Abstract][Full Text] [Related]
8. [The origin of renal galactosylceramide in the twitcher mouse, an animal model of human globoid cell leukodystrophy].
Katayama M
Fukuoka Igaku Zasshi; 1988 Jul; 79(7):529-36. PubMed ID: 3235022
[No Abstract] [Full Text] [Related]
9. Sphingolipid profile in the CNS of the twitcher (globoid cell leukodystrophy) mouse: a lipidomics approach.
Esch SW; Williams TD; Biswas S; Chakrabarty A; LeVine SM
Cell Mol Biol (Noisy-le-grand); 2003 Jul; 49(5):779-87. PubMed ID: 14528915
[TBL] [Abstract][Full Text] [Related]
10. Enzyme replacement with liposomes containing beta-galactosidase from Charonia lumpas in murine globoid cell leukodystrophy (twitcher).
Umezawa F; Eto Y; Tokoro T; Ito F; Maekawa K
Biochem Biophys Res Commun; 1985 Mar; 127(2):663-7. PubMed ID: 3919736
[TBL] [Abstract][Full Text] [Related]
11. An accumulation of galactocerebroside in kidney from mouse globoid cell leukodystrophy (twitcher).
Ida H; Umezawa F; Kasai E; Eto Y; Maekawa K
Biochem Biophys Res Commun; 1982 Dec; 109(3):634-8. PubMed ID: 7159437
[No Abstract] [Full Text] [Related]
12. The Twitcher mouse: an enzymatically authentic model of human globoid cell leukodystrophy (Krabbe disease).
Kobayashi T; Yamanaka T; Jacobs JM; Teixeira F; Suzuki K
Brain Res; 1980 Dec; 202(2):479-83. PubMed ID: 7437911
[TBL] [Abstract][Full Text] [Related]
13. Biochemistry and neuropathology of mice doubly deficient in synthesis and degradation of galactosylceramide.
Ezoe T; Vanier MT; Oya Y; Popko B; Tohyama J; Matsuda J; Suzuki K; Suzuki K
J Neurosci Res; 2000 Jan; 59(2):170-8. PubMed ID: 10650875
[TBL] [Abstract][Full Text] [Related]
14. Somatic cell genetic analysis of the galactocerebrosidase gene: lack of complementation in human Krabbe disease/twitcher mouse cell hybrids.
Skiba MC; Lyerla TA; Konola JT; Raghavan S
J Neurosci Res; 1990 Dec; 27(4):472-8. PubMed ID: 2079710
[TBL] [Abstract][Full Text] [Related]
15. Infantile and fetal globoid cell leukodystrophy: analysis of galactosylceramide and galactosylsphingosine.
Kobayashi T; Goto I; Yamanaka T; Suzuki Y; Nakano T; Suzuki K
Ann Neurol; 1988 Oct; 24(4):517-22. PubMed ID: 3239954
[TBL] [Abstract][Full Text] [Related]
16. Saposins (sphingolipid activator proteins) in the twitcher mutant mouse.
Shigematsu H; Morimoto S; Kishimoto Y; Weiler S; Tomich J; Barranger J; Shinohara M; Yeager AM; O'Brien JS
J Neurochem; 1990 Nov; 55(5):1659-62. PubMed ID: 2120388
[TBL] [Abstract][Full Text] [Related]
17. Clinical and biochemical heterogeneity of globoid cell leukodystrophy.
Farrell DF; Swedberg K
Ann Neurol; 1981 Oct; 10(4):364-8. PubMed ID: 7316489
[TBL] [Abstract][Full Text] [Related]
18. Galactosylceramide and galactosylsphingosine loading studies in cultured skin fibroblasts in human and murine globoid cell leukodystrophy.
Ida H; Kusano K; Suzuki H; Tokoro T; Eto Y
Biochem Biophys Res Commun; 1990 Jan; 166(2):1053-60. PubMed ID: 2302222
[TBL] [Abstract][Full Text] [Related]
19. IL-6 deficiency allows for enhanced therapeutic value after bone marrow transplantation across a minor histocompatibility barrier in the twitcher (globoid cell leukodystrophy) mouse.
Biswas S; Pinson DM; Bronshteyn IG; LeVine SM
J Neurosci Res; 2001 Aug; 65(4):298-307. PubMed ID: 11494365
[TBL] [Abstract][Full Text] [Related]
20. Lipids of developing brain of twitcher mouse. An authentic murine model of human Krabbe disease.
Igisu H; Shimomura K; Kishimoto Y; Suzuki K
Brain; 1983 Jun; 106 (Pt 2)():405-17. PubMed ID: 6850275
[TBL] [Abstract][Full Text] [Related]
[Next] [New Search]