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5. Phase separation and toxicity of C9orf72 poly(PR) depends on alternate distribution of arginine. Chen C; Yamanaka Y; Ueda K; Li P; Miyagi T; Harada Y; Tezuka S; Narumi S; Sugimoto M; Kuroda M; Hayamizu Y; Kanekura K J Cell Biol; 2021 Nov; 220(11):. PubMed ID: 34499080 [TBL] [Abstract][Full Text] [Related]
6. The DNA damage response (DDR) is induced by the C9orf72 repeat expansion in amyotrophic lateral sclerosis. Farg MA; Konopka A; Soo KY; Ito D; Atkin JD Hum Mol Genet; 2017 Aug; 26(15):2882-2896. PubMed ID: 28481984 [TBL] [Abstract][Full Text] [Related]
7. Phase Separation of Toxic Dipeptide Repeat Proteins Related to C9orf72 ALS/FTD. Jafarinia H; van der Giessen E; Onck PR Biophys J; 2020 Aug; 119(4):843-851. PubMed ID: 32730793 [TBL] [Abstract][Full Text] [Related]
8. Arginine-rich dipeptide-repeat proteins as phase disruptors in C9-ALS/FTD. Odeh HM; Shorter J Emerg Top Life Sci; 2020 Dec; 4(3):293-305. PubMed ID: 32639008 [TBL] [Abstract][Full Text] [Related]
9. Senataxin helicase, the causal gene defect in ALS4, is a significant modifier of C9orf72 ALS G4C2 and arginine-containing dipeptide repeat toxicity. Bennett CL; Dastidar S; Arnold FJ; McKinstry SU; Stockford C; Freibaum BD; Sopher BL; Wu M; Seidner G; Joiner W; Taylor JP; West RJH; La Spada AR Acta Neuropathol Commun; 2023 Oct; 11(1):164. PubMed ID: 37845749 [TBL] [Abstract][Full Text] [Related]
10. C9orf72 Dipeptide Repeats Impair the Assembly, Dynamics, and Function of Membrane-Less Organelles. Lee KH; Zhang P; Kim HJ; Mitrea DM; Sarkar M; Freibaum BD; Cika J; Coughlin M; Messing J; Molliex A; Maxwell BA; Kim NC; Temirov J; Moore J; Kolaitis RM; Shaw TI; Bai B; Peng J; Kriwacki RW; Taylor JP Cell; 2016 Oct; 167(3):774-788.e17. PubMed ID: 27768896 [TBL] [Abstract][Full Text] [Related]
11. Soluble and insoluble dipeptide repeat protein measurements in C9orf72-frontotemporal dementia brains show regional differential solubility and correlation of poly-GR with clinical severity. Quaegebeur A; Glaria I; Lashley T; Isaacs AM Acta Neuropathol Commun; 2020 Nov; 8(1):184. PubMed ID: 33168090 [TBL] [Abstract][Full Text] [Related]
12. The proline-arginine repeat protein linked to C9-ALS/FTD causes neuronal toxicity by inhibiting the DEAD-box RNA helicase-mediated ribosome biogenesis. Suzuki H; Shibagaki Y; Hattori S; Matsuoka M Cell Death Dis; 2018 Sep; 9(10):975. PubMed ID: 30250194 [TBL] [Abstract][Full Text] [Related]
13. Proline-arginine poly-dipeptide encoded by the C9orf72 repeat expansion inhibits adenosine deaminase acting on RNA. Suzuki H; Matsuoka M J Neurochem; 2021 Aug; 158(3):753-765. PubMed ID: 34081786 [TBL] [Abstract][Full Text] [Related]
14. A Chemical Screen Identifies Compounds Limiting the Toxicity of C9ORF72 Dipeptide Repeats. Corman A; Jung B; Häggblad M; Bräutigam L; Lafarga V; Lidemalm L; Hühn D; Carreras-Puigvert J; Fernandez-Capetillo O Cell Chem Biol; 2019 Feb; 26(2):235-243.e5. PubMed ID: 30527999 [TBL] [Abstract][Full Text] [Related]
15. C9orf72 Dipeptide Repeats Cause Selective Neurodegeneration and Cell-Autonomous Excitotoxicity in Xu W; Xu J J Neurosci; 2018 Aug; 38(35):7741-7752. PubMed ID: 30037833 [TBL] [Abstract][Full Text] [Related]
16. C9orf72 poly GA RAN-translated protein plays a key role in amyotrophic lateral sclerosis via aggregation and toxicity. Lee YB; Baskaran P; Gomez-Deza J; Chen HJ; Nishimura AL; Smith BN; Troakes C; Adachi Y; Stepto A; Petrucelli L; Gallo JM; Hirth F; Rogelj B; Guthrie S; Shaw CE Hum Mol Genet; 2017 Dec; 26(24):4765-4777. PubMed ID: 28973350 [TBL] [Abstract][Full Text] [Related]
20. Sulfated disaccharide protects membrane and DNA damages from arginine-rich dipeptide repeats in ALS. Chang YJ; Lin KT; Shih O; Yang CH; Chuang CY; Fang MH; Lai WB; Lee YC; Kuo HC; Hung SC; Yao CK; Jeng US; Chen YR Sci Adv; 2024 Feb; 10(8):eadj0347. PubMed ID: 38394210 [TBL] [Abstract][Full Text] [Related] [Next] [New Search]