216 related articles for article (PubMed ID: 31022638)
1. The therapeutic effect of stiripentol in Gabrg2
Warner TA; Smith NK; Kang JQ
Epilepsy Res; 2019 Aug; 154():8-12. PubMed ID: 31022638
[TBL] [Abstract][Full Text] [Related]
2. Overexpressing wild-type γ2 subunits rescued the seizure phenotype in Gabrg2
Huang X; Zhou C; Tian M; Kang JQ; Shen W; Verdier K; Pimenta A; MacDonald RL
Epilepsia; 2017 Aug; 58(8):1451-1461. PubMed ID: 28586508
[TBL] [Abstract][Full Text] [Related]
3. 4-Phenylbutyrate promoted wild-type γ-aminobutyric acid type A receptor trafficking, reduced endoplasmic reticulum stress, and mitigated seizures in Gabrg2
Shen W; Flamm C; Delahanty AJ; Casteel E; Biven M; DeLeeuw MB; Poliquin S; Nwosu G; Randhave K; Kang JQ
Epilepsia; 2024 Jan; 65(1):204-217. PubMed ID: 37746768
[TBL] [Abstract][Full Text] [Related]
4. Altered GABAA receptor expression in brainstem nuclei and SUDEP in Gabrg2(+/Q390X) mice associated with epileptic encephalopathy.
Xia G; P Pourali S; Warner TA; Zhang CQ; L Macdonald R; Kang JQ
Epilepsy Res; 2016 Jul; 123():50-4. PubMed ID: 27131289
[TBL] [Abstract][Full Text] [Related]
5. Heat induced temperature dysregulation and seizures in Dravet Syndrome/GEFS+ Gabrg2
Warner TA; Liu Z; Macdonald RL; Kang JQ
Epilepsy Res; 2017 Aug; 134():1-8. PubMed ID: 28505490
[TBL] [Abstract][Full Text] [Related]
6. Sleep slow-wave oscillations trigger seizures in a genetic epilepsy model of Dravet syndrome.
Catron MA; Howe RK; Besing GK; St John EK; Potesta CV; Gallagher MJ; Macdonald RL; Zhou C
Brain Commun; 2023; 5(1):fcac332. PubMed ID: 36632186
[TBL] [Abstract][Full Text] [Related]
7. The effects of stiripentol on GABA(A) receptors.
Fisher JL
Epilepsia; 2011 Apr; 52 Suppl 2(0 2):76-8. PubMed ID: 21463286
[TBL] [Abstract][Full Text] [Related]
8. Modulating Endoplasmic Reticulum Chaperones and Mutant Protein Degradation in GABRG2(Q390X) Associated with Genetic Epilepsy with Febrile Seizures Plus and Dravet Syndrome.
Poliquin S; Nwosu G; Randhave K; Shen W; Flamm C; Kang JQ
Int J Mol Sci; 2024 Apr; 25(9):. PubMed ID: 38731820
[TBL] [Abstract][Full Text] [Related]
9. Stiripentol: A Novel Antiseizure Medication for the Management of Dravet Syndrome.
Buck ML; Goodkin HP
Ann Pharmacother; 2019 Nov; 53(11):1136-1144. PubMed ID: 31167540
[No Abstract] [Full Text] [Related]
10. Do children with Dravet syndrome continue to benefit from stiripentol for long through adulthood?
Chiron C; Helias M; Kaminska A; Laroche C; de Toffol B; Dulac O; Nabbout R; An I
Epilepsia; 2018 Sep; 59(9):1705-1717. PubMed ID: 30132836
[TBL] [Abstract][Full Text] [Related]
11. Development of an antiseizure drug screening platform for Dravet syndrome at the NINDS contract site for the Epilepsy Therapy Screening Program.
Pernici CD; Mensah JA; Dahle EJ; Johnson KJ; Handy L; Buxton L; Smith MD; West PJ; Metcalf CS; Wilcox KS
Epilepsia; 2021 Jul; 62(7):1665-1676. PubMed ID: 34002394
[TBL] [Abstract][Full Text] [Related]
12. Audit of use of stiripentol in adults with Dravet syndrome.
Balestrini S; Sisodiya SM
Acta Neurol Scand; 2017 Jan; 135(1):73-79. PubMed ID: 27231140
[TBL] [Abstract][Full Text] [Related]
13. Dynamic changes of depolarizing GABA in a computational model of epileptogenic brain: Insight for Dravet syndrome.
Kurbatova P; Wendling F; Kaminska A; Rosati A; Nabbout R; Guerrini R; Dulac O; Pons G; Cornu C; Nony P; ; Chiron C; Benquet P
Exp Neurol; 2016 Sep; 283(Pt A):57-72. PubMed ID: 27246997
[TBL] [Abstract][Full Text] [Related]
14. Extending the use of stiripentol to other epileptic syndromes: a case of PCDH19-related epilepsy.
Trivisano M; Specchio N; Vigevano F
Eur J Paediatr Neurol; 2015 Mar; 19(2):248-50. PubMed ID: 25510386
[TBL] [Abstract][Full Text] [Related]
15. Efficacy of Stiripentol and the Clinical Outcome in Dravet Syndrome.
Yıldız EP; Ozkan MU; Uzunhan TA; Bektaş G; Tatlı B; Aydınlı N; Çalışkan M; Özmen M
J Child Neurol; 2019 Jan; 34(1):33-37. PubMed ID: 30362398
[TBL] [Abstract][Full Text] [Related]
16. Efficacy of stiripentol in hyperthermia-induced seizures in a mouse model of Dravet syndrome.
Cao D; Ohtani H; Ogiwara I; Ohtani S; Takahashi Y; Yamakawa K; Inoue Y
Epilepsia; 2012 Jul; 53(7):1140-5. PubMed ID: 22578034
[TBL] [Abstract][Full Text] [Related]
17. Stiripentol for the treatment of seizures associated with Dravet syndrome.
Chiron C
Expert Rev Neurother; 2019 Apr; 19(4):301-310. PubMed ID: 30900478
[TBL] [Abstract][Full Text] [Related]
18. Patients with dravet syndrome in the era of stiripentol: A French cohort cross-sectional study.
De Liso P; Chemaly N; Laschet J; Barnerias C; Hully M; Leunen D; Desguerre I; Chiron C; Dulac O; Nabbout R
Epilepsy Res; 2016 Sep; 125():42-6. PubMed ID: 27389706
[TBL] [Abstract][Full Text] [Related]
19. Endoplasmic reticulum stress increases inflammatory cytokines in an epilepsy mouse model Gabrg2
Shen W; Poliquin S; Macdonald RL; Dong M; Kang JQ
Epilepsia; 2020 Oct; 61(10):2301-2312. PubMed ID: 32944937
[TBL] [Abstract][Full Text] [Related]
20. Stiripentol efficacy and safety in Dravet syndrome: a 12-year observational study.
Myers KA; Lightfoot P; Patil SG; Cross JH; Scheffer IE
Dev Med Child Neurol; 2018 Jun; 60(6):574-578. PubMed ID: 29473155
[TBL] [Abstract][Full Text] [Related]
[Next] [New Search]
