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8. A novel mutation in the mitochondrial tRNA Asn gene associated with a lethal disease. Coulbault L; Herlicoviez D; Chapon F; Read MH; Penniello MJ; Reynier P; Fayet G; Lombès A; Jauzac P; Allouche S Biochem Biophys Res Commun; 2005 Apr; 329(3):1152-4. PubMed ID: 15752774 [TBL] [Abstract][Full Text] [Related]
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10. Thompson K; Mai N; Oláhová M; Scialó F; Formosa LE; Stroud DA; Garrett M; Lax NZ; Robertson FM; Jou C; Nascimento A; Ortez C; Jimenez-Mallebrera C; Hardy SA; He L; Brown GK; Marttinen P; McFarland R; Sanz A; Battersby BJ; Bonnen PE; Ryan MT; Chrzanowska-Lightowlers ZM; Lightowlers RN; Taylor RW EMBO Mol Med; 2018 Nov; 10(11):. PubMed ID: 30201738 [TBL] [Abstract][Full Text] [Related]
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12. Analysis of mouse models of cytochrome c oxidase deficiency owing to mutations in Sco2. Yang H; Brosel S; Acin-Perez R; Slavkovich V; Nishino I; Khan R; Goldberg IJ; Graziano J; Manfredi G; Schon EA Hum Mol Genet; 2010 Jan; 19(1):170-80. PubMed ID: 19837698 [TBL] [Abstract][Full Text] [Related]
13. A novel variant in the COX15 gene causing a fatal infantile cardioencephalomyopathy: A case report with clinical and molecular review. Galvão de Oliveira M; Tengan C; Micheletti C; Ramos de Macedo P; Soares Pinho Cernach MC; Cavole TR; de França Basto M; Filho JS; Virmond LA; Milanezi F; Nakano V; Falconi A; Perrone E Eur J Med Genet; 2021 May; 64(5):104195. PubMed ID: 33746038 [TBL] [Abstract][Full Text] [Related]
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15. Defects of the mitochondrial respiratory chain complexes in three pediatric cases with hypotonia and cardiac involvement. Figarella-Branger D; Pellissier JF; Scheiner C; Wernert F; Desnuelle C J Neurol Sci; 1992 Mar; 108(1):105-13. PubMed ID: 1320661 [TBL] [Abstract][Full Text] [Related]
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17. A systematic mutation screen of 10 nuclear and 25 mitochondrial candidate genes in 21 patients with cytochrome c oxidase (COX) deficiency shows tRNA(Ser)(UCN) mutations in a subgroup with syndromal encephalopathy. Jaksch M; Hofmann S; Kleinle S; Liechti-Gallati S; Pongratz DE; Müller-Höcker J; Jedele KB; Meitinger T; Gerbitz KD J Med Genet; 1998 Nov; 35(11):895-900. PubMed ID: 9832034 [TBL] [Abstract][Full Text] [Related]
18. Expression pattern of mitochondrial respiratory chain enzymes in skeletal muscle of patients with mitochondrial myopathy associated with the homoplasmic m.14674T>C variant. Roos S; Hedberg-Oldfors C; Visuttijai K; Stein M; Kollberg G; Elíasdóttir Ó; Lindberg C; Darin N; Oldfors A Brain Pathol; 2022 Jul; 32(4):e13038. PubMed ID: 34806237 [TBL] [Abstract][Full Text] [Related]
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