156 related articles for article (PubMed ID: 3116331)
1. Localization of pipecolic acid metabolism in rat liver peroxisomes: probable explanation for hyperpipecolataemia in Zellweger syndrome.
Trijbels JM; Monnens LA; Melis G; van den Broekvan Essen M; Bruckwilder M
J Inherit Metab Dis; 1987; 10(2):128-34. PubMed ID: 3116331
[TBL] [Abstract][Full Text] [Related]
2. Pipecolic acid is oxidized by renal and hepatic peroxisomes. Implications for Zellweger's cerebro-hepato-renal syndrome (CHRS).
Zaar K; Angermüller S; Völkl A; Fahimi HD
Exp Cell Res; 1986 May; 164(1):267-71. PubMed ID: 2869967
[TBL] [Abstract][Full Text] [Related]
3. Peroxisomal L-pipecolic acid oxidation is deficient in liver from Zellweger syndrome patients.
Mihalik SJ; Moser HW; Watkins PA; Danks DM; Poulos A; Rhead WJ
Pediatr Res; 1989 May; 25(5):548-52. PubMed ID: 2717271
[TBL] [Abstract][Full Text] [Related]
4. A sibship with a mild variant of Zellweger syndrome.
Barth PG; Schutgens RB; Wanders RJ; Heymans HS; Moser AE; Moser HW; Bleeker-Wagemakers EM; Jansonius-Schultheiss K; Derix M; Nelck GF
J Inherit Metab Dis; 1987; 10(3):253-9. PubMed ID: 3123783
[TBL] [Abstract][Full Text] [Related]
5. Zellweger syndrome: biochemical procedures in diagnosis, prevention and treatment.
Schutgens RB; Wanders RJ; Heymans HS; Schram AW; Tager JM; Schrakamp G; van den Bosch H
J Inherit Metab Dis; 1987; 10 Suppl 1():33-45. PubMed ID: 3119940
[TBL] [Abstract][Full Text] [Related]
6. Peroxisomal oxidation of pipecolic acid in the rat.
Kramar R; Kremser K; Schön H
J Clin Chem Clin Biochem; 1989 May; 27(5):319-21. PubMed ID: 2760567
[TBL] [Abstract][Full Text] [Related]
7. Biochemical studies in the liver and muscle of patients with Zellweger syndrome.
Trijbels JM; Berden JA; Monnens LA; Willems JL; Janssen AJ; Schutgens RB; van den Broek-Van Essen M
Pediatr Res; 1983 Jun; 17(6):514-7. PubMed ID: 6877906
[TBL] [Abstract][Full Text] [Related]
8. Biochemical studies in the cerebro-hepato-renal syndrome of Zellweger: a disturbance in the metabolism of pipecolic acid.
Trijbels JM; Monnens LA; Bakkeren JA; Van Raay-Selten AH; Corstiaensen JM
J Inherit Metab Dis; 1980; 2(2):39-42. PubMed ID: 6796759
[TBL] [Abstract][Full Text] [Related]
9. Lignoceric acid is oxidized in the peroxisome: implications for the Zellweger cerebro-hepato-renal syndrome and adrenoleukodystrophy.
Singh I; Moser AE; Goldfischer S; Moser HW
Proc Natl Acad Sci U S A; 1984 Jul; 81(13):4203-7. PubMed ID: 6588384
[TBL] [Abstract][Full Text] [Related]
10. Biosynthesis of peroxisomal membrane polypeptides in infants with Zellweger syndrome.
Suzuki Y; Shimozawa N; Orii T; Aikawa J; Tada K; Kuwabara T; Hashimoto T
J Inherit Metab Dis; 1987; 10(3):297-300. PubMed ID: 3123796
[No Abstract] [Full Text] [Related]
11. L-pipecolaturia in Zellweger syndrome.
Lam S; Hutzler J; Dancis J
Biochim Biophys Acta; 1986 Jun; 882(2):254-7. PubMed ID: 2871866
[TBL] [Abstract][Full Text] [Related]
12. Review: the cerebrohepatorenal syndrome of Zellweger, morphologic and metabolic aspects.
Kelley RI
Am J Med Genet; 1983 Dec; 16(4):503-17. PubMed ID: 6362411
[TBL] [Abstract][Full Text] [Related]
13. Peroxisomal disorders: clinical characterization.
Monnens L; Heymans H
J Inherit Metab Dis; 1987; 10 Suppl 1():23-32. PubMed ID: 2446046
[TBL] [Abstract][Full Text] [Related]
14. [Peroxisomes--in search of their function in man].
Monnens L; Trijbels F; Govaerts L
Tijdschr Kindergeneeskd; 1985 Aug; 53(4):129-36. PubMed ID: 3909510
[TBL] [Abstract][Full Text] [Related]
15. Presence of the peroxisomal 22-kDa integral membrane protein in the liver of a person lacking recognizable peroxisomes (Zellweger syndrome).
Lazarow PB; Fujiki Y; Small GM; Watkins P; Moser H
Proc Natl Acad Sci U S A; 1986 Dec; 83(23):9193-6. PubMed ID: 3538019
[TBL] [Abstract][Full Text] [Related]
16. Peroxisomal very long-chain fatty acid beta-oxidation in human skin fibroblasts: activity in Zellweger syndrome and other peroxisomal disorders.
Wanders RJ; van Roermund CW; van Wijland MJ; Heikoop J; Schutgens RB; Schram AW; Tager JM; van den Bosch H; Poll-Thé BT; Saudubray JM
Clin Chim Acta; 1987 Jul; 166(2-3):255-63. PubMed ID: 2441904
[TBL] [Abstract][Full Text] [Related]
17. Defective peroxisomal cleavage of the C27-steroid side chain in the cerebro-hepato-renal syndrome of Zellweger.
Kase BF; Björkhem I; Hågå P; Pedersen JI
J Clin Invest; 1985 Feb; 75(2):427-35. PubMed ID: 3973012
[TBL] [Abstract][Full Text] [Related]
18. Species variation in organellar location and activity of L-pipecolic acid oxidation in mammals.
Mihalik SJ; Rhead WJ
J Comp Physiol B; 1991; 160(6):671-6. PubMed ID: 2045546
[TBL] [Abstract][Full Text] [Related]
19. Peroxisomes and peroxisomal functions in hyperpipecolic acidaemia.
Wanders RJ; van Roermund CW; van Wijland MJ; Schutgens RB; Tager JM; van den Bosch H; Thomas GH
J Inherit Metab Dis; 1988; 11 Suppl 2():161-4. PubMed ID: 3141699
[No Abstract] [Full Text] [Related]
20. L-pipecolic acid metabolism in human liver: detection of L-pipecolate oxidase and identification of its reaction product.
Rao VV; Chang YF
Biochim Biophys Acta; 1990 May; 1038(3):295-9. PubMed ID: 2340290
[TBL] [Abstract][Full Text] [Related]
[Next] [New Search]
