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2. CYP46A1, the rate-limiting enzyme for cholesterol degradation, is neuroprotective in Huntington's disease. Boussicault L; Alves S; Lamazière A; Planques A; Heck N; Moumné L; Despres G; Bolte S; Hu A; Pagès C; Galvan L; Piguet F; Aubourg P; Cartier N; Caboche J; Betuing S Brain; 2016 Mar; 139(Pt 3):953-70. PubMed ID: 26912634 [TBL] [Abstract][Full Text] [Related]
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6. Downregulation of glial genes involved in synaptic function mitigates Huntington's disease pathogenesis. Onur TS; Laitman A; Zhao H; Keyho R; Kim H; Wang J; Mair M; Wang H; Li L; Perez A; de Haro M; Wan YW; Allen G; Lu B; Al-Ramahi I; Liu Z; Botas J Elife; 2021 Apr; 10():. PubMed ID: 33871358 [TBL] [Abstract][Full Text] [Related]
7. Selective reduction of striatal mature BDNF without induction of proBDNF in the zQ175 mouse model of Huntington's disease. Ma Q; Yang J; Li T; Milner TA; Hempstead BL Neurobiol Dis; 2015 Oct; 82():466-477. PubMed ID: 26282324 [TBL] [Abstract][Full Text] [Related]
8. Pramipexole reduces soluble mutant huntingtin and protects striatal neurons through dopamine D3 receptors in a genetic model of Huntington's disease. Luis-Ravelo D; Estévez-Silva H; Barroso-Chinea P; Afonso-Oramas D; Salas-Hernández J; Rodríguez-Núñez J; Acevedo-Arozena A; Marcellino D; González-Hernández T Exp Neurol; 2018 Jan; 299(Pt A):137-147. PubMed ID: 29056363 [TBL] [Abstract][Full Text] [Related]
9. Gene therapy by proteasome activator, PA28γ, improves motor coordination and proteasome function in Huntington's disease YAC128 mice. Jeon J; Kim W; Jang J; Isacson O; Seo H Neuroscience; 2016 Jun; 324():20-8. PubMed ID: 26944602 [TBL] [Abstract][Full Text] [Related]
10. Study of cholesterol metabolism in Huntington's disease. Leoni V; Caccia C Biochem Biophys Res Commun; 2014 Apr; 446(3):697-701. PubMed ID: 24525128 [TBL] [Abstract][Full Text] [Related]
11. TRiC subunits enhance BDNF axonal transport and rescue striatal atrophy in Huntington's disease. Zhao X; Chen XQ; Han E; Hu Y; Paik P; Ding Z; Overman J; Lau AL; Shahmoradian SH; Chiu W; Thompson LM; Wu C; Mobley WC Proc Natl Acad Sci U S A; 2016 Sep; 113(38):E5655-64. PubMed ID: 27601642 [TBL] [Abstract][Full Text] [Related]
12. BDNF overexpression in the forebrain rescues Huntington's disease phenotypes in YAC128 mice. Xie Y; Hayden MR; Xu B J Neurosci; 2010 Nov; 30(44):14708-18. PubMed ID: 21048129 [TBL] [Abstract][Full Text] [Related]
13. Altered anterograde axonal transport of mitochondria in cultured striatal neurons of a knock-in mouse model of Huntington's disease. Wu C; Yin H; Fu S; Yoo H; Zhang M; Park H Biochem Biophys Res Commun; 2024 Jan; 691():149246. PubMed ID: 38029540 [TBL] [Abstract][Full Text] [Related]
14. Neural stem cells derived from the developing forebrain of YAC128 mice exhibit pathological features of Huntington's disease. Li E; Park HR; Hong CP; Kim Y; Choi J; Lee S; Park HJ; Lee B; Kim TA; Kim SJ; Kim HS; Song J Cell Prolif; 2020 Oct; 53(10):e12893. PubMed ID: 32865873 [TBL] [Abstract][Full Text] [Related]
15. VGLUT3 Deletion Rescues Motor Deficits and Neuronal Loss in the zQ175 Mouse Model of Huntington's Disease. Ibrahim KS; El Mestikawy S; Abd-Elrahman KS; Ferguson SSG J Neurosci; 2023 Jun; 43(23):4365-4377. PubMed ID: 37055181 [TBL] [Abstract][Full Text] [Related]
16. Sulforaphane enhances proteasomal and autophagic activities in mice and is a potential therapeutic reagent for Huntington's disease. Liu Y; Hettinger CL; Zhang D; Rezvani K; Wang X; Wang H J Neurochem; 2014 May; 129(3):539-47. PubMed ID: 24383989 [TBL] [Abstract][Full Text] [Related]
17. Brain-derived neurotrophic factor regulates the onset and severity of motor dysfunction associated with enkephalinergic neuronal degeneration in Huntington's disease. Canals JM; Pineda JR; Torres-Peraza JF; Bosch M; Martín-Ibañez R; Muñoz MT; Mengod G; Ernfors P; Alberch J J Neurosci; 2004 Sep; 24(35):7727-39. PubMed ID: 15342740 [TBL] [Abstract][Full Text] [Related]
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