466 related articles for article (PubMed ID: 31365319)
1. Hyperexcitability precedes motoneuron loss in the
Quinlan KA; Reedich EJ; Arnold WD; Puritz AC; Cavarsan CF; Heckman CJ; DiDonato CJ
J Neurophysiol; 2019 Oct; 122(4):1297-1311. PubMed ID: 31365319
[TBL] [Abstract][Full Text] [Related]
2. Compensatory axon sprouting for very slow axonal die-back in a transgenic model of spinal muscular atrophy type III.
Udina E; Putman CT; Harris LR; Tyreman N; Cook VE; Gordon T
J Physiol; 2017 Mar; 595(5):1815-1829. PubMed ID: 27891608
[TBL] [Abstract][Full Text] [Related]
3. Spinal motor neuron loss occurs through a p53-and-p21-independent mechanism in the Smn
Reedich EJ; Kalski M; Armijo N; Cox GA; DiDonato CJ
Exp Neurol; 2021 Mar; 337():113587. PubMed ID: 33382987
[TBL] [Abstract][Full Text] [Related]
4. Motor transmission defects with sex differences in a new mouse model of mild spinal muscular atrophy.
Deguise MO; De Repentigny Y; Tierney A; Beauvais A; Michaud J; Chehade L; Thabet M; Paul B; Reilly A; Gagnon S; Renaud JM; Kothary R
EBioMedicine; 2020 May; 55():102750. PubMed ID: 32339936
[TBL] [Abstract][Full Text] [Related]
5. A large animal model of spinal muscular atrophy and correction of phenotype.
Duque SI; Arnold WD; Odermatt P; Li X; Porensky PN; Schmelzer L; Meyer K; Kolb SJ; Schümperli D; Kaspar BK; Burghes AH
Ann Neurol; 2015 Mar; 77(3):399-414. PubMed ID: 25516063
[TBL] [Abstract][Full Text] [Related]
6. HuD and the Survival Motor Neuron Protein Interact in Motoneurons and Are Essential for Motoneuron Development, Function, and mRNA Regulation.
Hao le T; Duy PQ; An M; Talbot J; Iyer CC; Wolman M; Beattie CE
J Neurosci; 2017 Nov; 37(48):11559-11571. PubMed ID: 29061699
[TBL] [Abstract][Full Text] [Related]
7. Chronic treatment with lithium does not improve neuromuscular phenotype in a mouse model of severe spinal muscular atrophy.
Dachs E; Piedrafita L; Hereu M; Esquerda JE; Calderó J
Neuroscience; 2013 Oct; 250():417-33. PubMed ID: 23876328
[TBL] [Abstract][Full Text] [Related]
8. A critical smn threshold in mice dictates onset of an intermediate spinal muscular atrophy phenotype associated with a distinct neuromuscular junction pathology.
Bowerman M; Murray LM; Beauvais A; Pinheiro B; Kothary R
Neuromuscul Disord; 2012 Mar; 22(3):263-76. PubMed ID: 22071333
[TBL] [Abstract][Full Text] [Related]
9. Calpain Inhibition Increases SMN Protein in Spinal Cord Motoneurons and Ameliorates the Spinal Muscular Atrophy Phenotype in Mice.
de la Fuente S; Sansa A; Periyakaruppiah A; Garcera A; Soler RM
Mol Neurobiol; 2019 Jun; 56(6):4414-4427. PubMed ID: 30327977
[TBL] [Abstract][Full Text] [Related]
10. Impairment of the neurotrophic signaling hub B-Raf contributes to motoneuron degeneration in spinal muscular atrophy.
Hensel N; Cieri F; Santonicola P; Tapken I; Schüning T; Taiana M; Pagliari E; Joseph A; Fischer S; Heidrich N; Brinkmann H; Kubinski S; Bergmann AK; Richter MF; Jung K; Corti S; Di Schiavi E; Claus P
Proc Natl Acad Sci U S A; 2021 May; 118(18):. PubMed ID: 33931501
[TBL] [Abstract][Full Text] [Related]
11. SMN expression is required in motor neurons to rescue electrophysiological deficits in the SMNΔ7 mouse model of SMA.
McGovern VL; Iyer CC; Arnold WD; Gombash SE; Zaworski PG; Blatnik AJ; Foust KD; Burghes AH
Hum Mol Genet; 2015 Oct; 24(19):5524-41. PubMed ID: 26206889
[TBL] [Abstract][Full Text] [Related]
12. The neuromuscular impact of symptomatic SMN restoration in a mouse model of spinal muscular atrophy.
Arnold W; McGovern VL; Sanchez B; Li J; Corlett KM; Kolb SJ; Rutkove SB; Burghes AH
Neurobiol Dis; 2016 Mar; 87():116-23. PubMed ID: 26733414
[TBL] [Abstract][Full Text] [Related]
13. Synaptic withdrawal following nerve injury is influenced by postnatal maturity, muscle-specific properties, and the presence of underlying pathology in mice.
Mole AJ; Bell S; Thomson AK; Dissanayake KN; Ribchester RR; Murray LM
J Anat; 2020 Aug; 237(2):263-274. PubMed ID: 32311115
[TBL] [Abstract][Full Text] [Related]
14. Ciliary neurotrophic factor-induced sprouting preserves motor function in a mouse model of mild spinal muscular atrophy.
Simon CM; Jablonka S; Ruiz R; Tabares L; Sendtner M
Hum Mol Genet; 2010 Mar; 19(6):973-86. PubMed ID: 20022887
[TBL] [Abstract][Full Text] [Related]
15. Spinal muscular atrophy: present state.
Schmalbruch H; Haase G
Brain Pathol; 2001 Apr; 11(2):231-47. PubMed ID: 11303798
[TBL] [Abstract][Full Text] [Related]
16. Mechanisms of exercise-induced survival motor neuron expression in the skeletal muscle of spinal muscular atrophy-like mice.
Ng SY; Mikhail A; Ljubicic V
J Physiol; 2019 Sep; 597(18):4757-4778. PubMed ID: 31361024
[TBL] [Abstract][Full Text] [Related]
17. Motoneuron development influences dorsal root ganglia survival and Schwann cell development in a vertebrate model of spinal muscular atrophy.
Hao le T; Duy PQ; Jontes JD; Beattie CE
Hum Mol Genet; 2015 Jan; 24(2):346-60. PubMed ID: 25180019
[TBL] [Abstract][Full Text] [Related]
18. Loganin possesses neuroprotective properties, restores SMN protein and activates protein synthesis positive regulator Akt/mTOR in experimental models of spinal muscular atrophy.
Tseng YT; Chen CS; Jong YJ; Chang FR; Lo YC
Pharmacol Res; 2016 Sep; 111():58-75. PubMed ID: 27241020
[TBL] [Abstract][Full Text] [Related]
19. Transcriptional profiling of differentially vulnerable motor neurons at pre-symptomatic stage in the Smn (2b/-) mouse model of spinal muscular atrophy.
Murray LM; Beauvais A; Gibeault S; Courtney NL; Kothary R
Acta Neuropathol Commun; 2015 Sep; 3():55. PubMed ID: 26374403
[TBL] [Abstract][Full Text] [Related]
20. Nusinersen ameliorates motor function and prevents motoneuron Cajal body disassembly and abnormal poly(A) RNA distribution in a SMA mouse model.
Berciano MT; Puente-Bedia A; Medina-Samamé A; Rodríguez-Rey JC; Calderó J; Lafarga M; Tapia O
Sci Rep; 2020 Jul; 10(1):10738. PubMed ID: 32612161
[TBL] [Abstract][Full Text] [Related]
[Next] [New Search]
