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3. Cathepsin A/protective protein: an unusual lysosomal multifunctional protein. Hiraiwa M Cell Mol Life Sci; 1999 Dec; 56(11-12):894-907. PubMed ID: 11212324 [TBL] [Abstract][Full Text] [Related]
4. Human placental neuraminidase. Activation, stabilization and association with beta-galactosidase and its protective protein. Verheijen FW; Palmeri S; Hoogeveen AT; Galjaard H Eur J Biochem; 1985 Jun; 149(2):315-21. PubMed ID: 3922758 [TBL] [Abstract][Full Text] [Related]
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6. [Genetic advances in galactosialidosis]. Hirasawa M Nihon Rinsho; 1993 Sep; 51(9):2319-23. PubMed ID: 8411708 [TBL] [Abstract][Full Text] [Related]
7. Human lysosomal protective protein has cathepsin A-like activity distinct from its protective function. Galjart NJ; Morreau H; Willemsen R; Gillemans N; Bonten EJ; d'Azzo A J Biol Chem; 1991 Aug; 266(22):14754-62. PubMed ID: 1907282 [TBL] [Abstract][Full Text] [Related]
8. Stable expression of protective protein/cathepsin A-green fluorescent protein fusion genes in a fibroblastic cell line from a galactosialidosis patient. Model system for revealing the intracellular transport of normal and mutated lysosomal enzymes. Naganawa Y; Itoh K; Shimmoto M; Kamei S; Takiguchi K; Doi H; Sakuraba H Biochem J; 1999 Jun; 340 ( Pt 2)(Pt 2):467-74. PubMed ID: 10333491 [TBL] [Abstract][Full Text] [Related]
9. Association of N-acetylgalactosamine-6-sulfate sulfatase with the multienzyme lysosomal complex of beta-galactosidase, cathepsin A, and neuraminidase. Possible implication for intralysosomal catabolism of keratan sulfate. Pshezhetsky AV; Potier M J Biol Chem; 1996 Nov; 271(45):28359-65. PubMed ID: 8910459 [TBL] [Abstract][Full Text] [Related]
10. Transport of human lysosomal neuraminidase to mature lysosomes requires protective protein/cathepsin A. van der Spoel A; Bonten E; d'Azzo A EMBO J; 1998 Mar; 17(6):1588-97. PubMed ID: 9501080 [TBL] [Abstract][Full Text] [Related]
11. Purification and characterization of human lysosomal protective protein expressed in stably transformed Chinese hamster ovary cells. Itoh K; Takiyama N; Kase R; Kondoh K; Sano A; Oshima A; Sakuraba H; Suzuki Y J Biol Chem; 1993 Jan; 268(2):1180-6. PubMed ID: 8419322 [TBL] [Abstract][Full Text] [Related]
12. In vitro activation of neuraminidase in the beta-galactosidase-neuraminidase-protective protein complex by cathepsin C. D'Agrosa RM; Callahan JW Biochem Biophys Res Commun; 1988 Dec; 157(2):770-5. PubMed ID: 3144278 [TBL] [Abstract][Full Text] [Related]
13. The biochemistry and clinical features of galactosialidosis. Okamura-Oho Y; Zhang S; Callahan JW Biochim Biophys Acta; 1994 Feb; 1225(3):244-54. PubMed ID: 8312369 [TBL] [Abstract][Full Text] [Related]
14. [Galactosialidosis--protective protein and related enzymes]. Hirasawa M Nihon Rinsho; 1995 Dec; 53(12):2967-72. PubMed ID: 8577044 [TBL] [Abstract][Full Text] [Related]
15. A mutation in a mild form of galactosialidosis impairs dimerization of the protective protein and renders it unstable. Zhou XY; Galjart NJ; Willemsen R; Gillemans N; Galjaard H; d'Azzo A EMBO J; 1991 Dec; 10(13):4041-8. PubMed ID: 1756715 [TBL] [Abstract][Full Text] [Related]
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17. Alternative splicing of beta-galactosidase mRNA generates the classic lysosomal enzyme and a beta-galactosidase-related protein. Morreau H; Galjart NJ; Gillemans N; Willemsen R; van der Horst GT; d'Azzo A J Biol Chem; 1989 Dec; 264(34):20655-63. PubMed ID: 2511208 [TBL] [Abstract][Full Text] [Related]
18. Immunoelectron microscopical localization of lysosomal beta-galactosidase and its precursor forms in normal and mutant human fibroblasts. Willemsen R; Hoogeveen AT; Sips HJ; van Dongen JM; Galjaard H Eur J Cell Biol; 1986 Mar; 40(1):9-15. PubMed ID: 3084261 [TBL] [Abstract][Full Text] [Related]
19. Protective protein gene mutations in galactosialidosis. Shimmoto M; Fukuhara Y; Itoh K; Oshima A; Sakuraba H; Suzuki Y J Clin Invest; 1993 Jun; 91(6):2393-8. PubMed ID: 8514852 [TBL] [Abstract][Full Text] [Related]
20. Clinical and molecular heterogeneity in hereditary beta-galactosidase deficiency. Suzuki Y; Sakuraba H; Oshima A; Yoshida K; Shimmoto M; Takano T; Fukuhara Y Dev Neurosci; 1991; 13(4-5):299-303. PubMed ID: 1817034 [TBL] [Abstract][Full Text] [Related] [Next] [New Search]