208 related articles for article (PubMed ID: 31513782)
1. Establishment of ornithine transcarbamylase deficiency-derived primary human hepatocyte with hepatic functions.
Su S; Di Poto C; Kroemer AH; Cui W; Roy R; Liu X; Ressom HW
Exp Cell Res; 2019 Nov; 384(1):111621. PubMed ID: 31513782
[TBL] [Abstract][Full Text] [Related]
2. Frequency and Pathophysiology of Acute Liver Failure in Ornithine Transcarbamylase Deficiency (OTCD).
Laemmle A; Gallagher RC; Keogh A; Stricker T; Gautschi M; Nuoffer JM; Baumgartner MR; Häberle J
PLoS One; 2016; 11(4):e0153358. PubMed ID: 27070778
[TBL] [Abstract][Full Text] [Related]
3. Aquaporin 9 induction in human iPSC-derived hepatocytes facilitates modeling of ornithine transcarbamylase deficiency.
Laemmle A; Poms M; Hsu B; Borsuk M; Rüfenacht V; Robinson J; Sadowski MC; Nuoffer JM; Häberle J; Willenbring H
Hepatology; 2022 Sep; 76(3):646-659. PubMed ID: 34786702
[TBL] [Abstract][Full Text] [Related]
4. Humanized liver mouse model with transplanted human hepatocytes from patients with ornithine transcarbamylase deficiency.
Sugahara G; Yamasaki C; Yanagi A; Furukawa S; Ogawa Y; Fukuda A; Enosawa S; Umezawa A; Ishida Y; Tateno C
J Inherit Metab Dis; 2021 May; 44(3):618-628. PubMed ID: 33336822
[TBL] [Abstract][Full Text] [Related]
5. Novel liver findings in ornithine transcarbamylase deficiency due to Xp11.4-p21.1 microdeletion.
Gallant NM; Gui D; Lassman CR; Yong WH; Teitell M; Mandelker D; Lorey F; Martinez-Agosto JA; Quintero-Rivera F
Gene; 2015 Feb; 556(2):249-53. PubMed ID: 25434494
[TBL] [Abstract][Full Text] [Related]
6. An Exon-Specific Small Nuclear U1 RNA (ExSpeU1) Improves Hepatic OTC Expression in a Splicing-Defective
Balestra D; Ferrarese M; Lombardi S; Ziliotto N; Branchini A; Petersen N; Bosma P; Pinotti M; van de Graaf SFJ
Int J Mol Sci; 2020 Nov; 21(22):. PubMed ID: 33228018
[No Abstract] [Full Text] [Related]
7. Explanted diseased livers - a possible source of metabolic competent primary human hepatocytes.
Kleine M; Riemer M; Krech T; DeTemple D; Jäger MD; Lehner F; Manns MP; Klempnauer J; Borlak J; Bektas H; Vondran FW
PLoS One; 2014; 9(7):e101386. PubMed ID: 24999631
[TBL] [Abstract][Full Text] [Related]
8. Comparison of commercially available media for hepatic differentiation and hepatocyte maintenance.
Toba Y; Deguchi S; Mimura N; Sakamoto A; Harada K; Hirata K; Takayama K; Mizuguchi H
PLoS One; 2020; 15(2):e0229654. PubMed ID: 32106262
[TBL] [Abstract][Full Text] [Related]
9. Significant hepatic involvement in patients with ornithine transcarbamylase deficiency.
Gallagher RC; Lam C; Wong D; Cederbaum S; Sokol RJ
J Pediatr; 2014 Apr; 164(4):720-725.e6. PubMed ID: 24485820
[TBL] [Abstract][Full Text] [Related]
10. A Cell Culture Platform to Maintain Long-term Phenotype of Primary Human Hepatocytes and Endothelial Cells.
Ware BR; Durham MJ; Monckton CP; Khetani SR
Cell Mol Gastroenterol Hepatol; 2018 Mar; 5(3):187-207. PubMed ID: 29379855
[TBL] [Abstract][Full Text] [Related]
11. Targeted mRNA Therapy for Ornithine Transcarbamylase Deficiency.
Prieve MG; Harvie P; Monahan SD; Roy D; Li AG; Blevins TL; Paschal AE; Waldheim M; Bell EC; Galperin A; Ella-Menye JR; Houston ME
Mol Ther; 2018 Mar; 26(3):801-813. PubMed ID: 29433939
[TBL] [Abstract][Full Text] [Related]
12. Differential utilization of systemic and enteral ammonia for urea synthesis in control subjects and ornithine transcarbamylase deficiency carriers.
Scaglia F; Marini J; Rosenberger J; Henry J; Garlick P; Lee B; Reeds P
Am J Clin Nutr; 2003 Oct; 78(4):749-55. PubMed ID: 14522733
[TBL] [Abstract][Full Text] [Related]
13. Microengineered cultures containing human hepatic stellate cells and hepatocytes for drug development.
Davidson MD; Kukla DA; Khetani SR
Integr Biol (Camb); 2017 Aug; 9(8):662-677. PubMed ID: 28702667
[TBL] [Abstract][Full Text] [Related]
14. Primary-like human hepatocytes genetically engineered to obtain proliferation competence display hepatic differentiation characteristics in monolayer and organotypical spheroid cultures.
Herzog N; Hansen M; Miethbauer S; Schmidtke KU; Anderer U; Lupp A; Sperling S; Seehofer D; Damm G; Scheibner K; Küpper JH
Cell Biol Int; 2016 Mar; 40(3):341-53. PubMed ID: 26715207
[TBL] [Abstract][Full Text] [Related]
15. Hyperammonemia in ornithine transcarbamylase-deficient recipients following living donor liver transplantation from heterozygous carrier donors.
Rahayatri TH; Uchida H; Sasaki K; Shigeta T; Hirata Y; Kanazawa H; Mali V; Fukuda A; Sakamoto S; Kasahara M
Pediatr Transplant; 2017 Feb; 21(1):. PubMed ID: 27891735
[TBL] [Abstract][Full Text] [Related]
16. Correction of ureagenesis after gene transfer in an animal model and after liver transplantation in humans with ornithine transcarbamylase deficiency.
Batshaw ML; Robinson MB; Ye X; Pabin C; Daikhin Y; Burton BK; Wilson JM; Yudkoff M
Pediatr Res; 1999 Nov; 46(5):588-93. PubMed ID: 10541323
[TBL] [Abstract][Full Text] [Related]
17. HepaRG human hepatic cell line utility as a surrogate for primary human hepatocytes in drug metabolism assessment in vitro.
Lübberstedt M; Müller-Vieira U; Mayer M; Biemel KM; Knöspel F; Knobeloch D; Nüssler AK; Gerlach JC; Zeilinger K
J Pharmacol Toxicol Methods; 2011; 63(1):59-68. PubMed ID: 20460162
[TBL] [Abstract][Full Text] [Related]
18. 3D hepatic cultures simultaneously maintain primary hepatocyte and liver sinusoidal endothelial cell phenotypes.
Kim Y; Rajagopalan P
PLoS One; 2010 Nov; 5(11):e15456. PubMed ID: 21103392
[TBL] [Abstract][Full Text] [Related]
19. Ornithine transcarbamylase deficiency unmasked because of gastrointestinal bleeding.
Trivedi M; Zafar S; Spalding MJ; Jonnalagadda S
J Clin Gastroenterol; 2001 Apr; 32(4):340-3. PubMed ID: 11276280
[TBL] [Abstract][Full Text] [Related]
20. Three-Dimensional Spheroid Primary Human Hepatocytes in Monoculture and Coculture with Nonparenchymal Cells.
Baze A; Parmentier C; Hendriks DFG; Hurrell T; Heyd B; Bachellier P; Schuster C; Ingelman-Sundberg M; Richert L
Tissue Eng Part C Methods; 2018 Sep; 24(9):534-545. PubMed ID: 30101670
[TBL] [Abstract][Full Text] [Related]
[Next] [New Search]
