256 related articles for article (PubMed ID: 31547314)
1. Global Proteome of
Key J; Kohli A; Bárcena C; López-Otín C; Heidler J; Wittig I; Auburger G
Int J Mol Sci; 2019 Sep; 20(18):. PubMed ID: 31547314
[TBL] [Abstract][Full Text] [Related]
2. CLPP coordinates mitoribosomal assembly through the regulation of ERAL1 levels.
Szczepanowska K; Maiti P; Kukat A; Hofsetz E; Nolte H; Senft K; Becker C; Ruzzenente B; Hornig-Do HT; Wibom R; Wiesner RJ; Krüger M; Trifunovic A
EMBO J; 2016 Dec; 35(23):2566-2583. PubMed ID: 27797820
[TBL] [Abstract][Full Text] [Related]
3. Inactivity of Peptidase ClpP Causes Primary Accumulation of Mitochondrial Disaggregase ClpX with Its Interacting Nucleoid Proteins, and of mtDNA.
Key J; Torres-Odio S; Bach NC; Gispert S; Koepf G; Reichlmeir M; West AP; Prokisch H; Freisinger P; Newman WG; Shalev S; Sieber SA; Wittig I; Auburger G
Cells; 2021 Nov; 10(12):. PubMed ID: 34943861
[TBL] [Abstract][Full Text] [Related]
4. The biology of Lonp1: More than a mitochondrial protease.
Gibellini L; De Gaetano A; Mandrioli M; Van Tongeren E; Bortolotti CA; Cossarizza A; Pinti M
Int Rev Cell Mol Biol; 2020; 354():1-61. PubMed ID: 32475470
[TBL] [Abstract][Full Text] [Related]
5. CODAS syndrome is associated with mutations of LONP1, encoding mitochondrial AAA+ Lon protease.
Strauss KA; Jinks RN; Puffenberger EG; Venkatesh S; Singh K; Cheng I; Mikita N; Thilagavathi J; Lee J; Sarafianos S; Benkert A; Koehler A; Zhu A; Trovillion V; McGlincy M; Morlet T; Deardorff M; Innes AM; Prasad C; Chudley AE; Lee IN; Suzuki CK
Am J Hum Genet; 2015 Jan; 96(1):121-35. PubMed ID: 25574826
[TBL] [Abstract][Full Text] [Related]
6. Loss of mitochondrial ClpP, Lonp1, and Tfam triggers transcriptional induction of Rnf213, a susceptibility factor for moyamoya disease.
Key J; Maletzko A; Kohli A; Gispert S; Torres-Odio S; Wittig I; Heidler J; Bárcena C; López-Otín C; Lei Y; West AP; Münch C; Auburger G
Neurogenetics; 2020 Jul; 21(3):187-203. PubMed ID: 32342250
[TBL] [Abstract][Full Text] [Related]
7. Proteomic analysis demonstrates the role of the quality control protease LONP1 in mitochondrial protein aggregation.
Pollecker K; Sylvester M; Voos W
J Biol Chem; 2021 Oct; 297(4):101134. PubMed ID: 34461102
[TBL] [Abstract][Full Text] [Related]
8. MitoRibo-Tag Mice Provide a Tool for In Vivo Studies of Mitoribosome Composition.
Busch JD; Cipullo M; Atanassov I; Bratic A; Silva Ramos E; Schöndorf T; Li X; Pearce SF; Milenkovic D; Rorbach J; Larsson NG
Cell Rep; 2019 Nov; 29(6):1728-1738.e9. PubMed ID: 31693908
[TBL] [Abstract][Full Text] [Related]
9. Roles of LonP1 in Oral-Maxillofacial Developmental Defects and Tumors: A Novel Insight.
Ma H; Chen W; Fan W; He H; Huang F
Int J Mol Sci; 2022 Nov; 23(21):. PubMed ID: 36362158
[TBL] [Abstract][Full Text] [Related]
10. Mutations in LONP1, a mitochondrial matrix protease, cause CODAS syndrome.
Dikoglu E; Alfaiz A; Gorna M; Bertola D; Chae JH; Cho TJ; Derbent M; Alanay Y; Guran T; Kim OH; Llerenar JC; Yamamoto G; Superti-Furga G; Reymond A; Xenarios I; Stevenson B; Campos-Xavier B; Bonafé L; Superti-Furga A; Unger S
Am J Med Genet A; 2015 Jul; 167(7):1501-9. PubMed ID: 25808063
[TBL] [Abstract][Full Text] [Related]
11. LONP1 Is Required for Maturation of a Subset of Mitochondrial Proteins, and Its Loss Elicits an Integrated Stress Response.
Zurita Rendón O; Shoubridge EA
Mol Cell Biol; 2018 Oct; 38(20):. PubMed ID: 30061372
[TBL] [Abstract][Full Text] [Related]
12. Mitochondrial Lon protease is a gatekeeper for proteins newly imported into the matrix.
Matsushima Y; Takahashi K; Yue S; Fujiyoshi Y; Yoshioka H; Aihara M; Setoyama D; Uchiumi T; Fukuchi S; Kang D
Commun Biol; 2021 Aug; 4(1):974. PubMed ID: 34400774
[TBL] [Abstract][Full Text] [Related]
13. Knockout Mouse Studies Show That Mitochondrial CLPP Peptidase and CLPX Unfoldase Act in Matrix Condensates near IMM, as Fast Stress Response in Protein Assemblies for Transcript Processing, Translation, and Heme Production.
Key J; Gispert S; Auburger G
Genes (Basel); 2024 May; 15(6):. PubMed ID: 38927630
[TBL] [Abstract][Full Text] [Related]
14. LONP1 de novo dominant mutation causes mitochondrial encephalopathy with loss of LONP1 chaperone activity and excessive LONP1 proteolytic activity.
Besse A; Brezavar D; Hanson J; Larson A; Bonnen PE
Mitochondrion; 2020 Mar; 51():68-78. PubMed ID: 31923470
[TBL] [Abstract][Full Text] [Related]
15. Defective mitochondrial protease LonP1 can cause classical mitochondrial disease.
Peter B; Waddington CL; Oláhová M; Sommerville EW; Hopton S; Pyle A; Champion M; Ohlson M; Siibak T; Chrzanowska-Lightowlers ZMA; Taylor RW; Falkenberg M; Lightowlers RN
Hum Mol Genet; 2018 May; 27(10):1743-1753. PubMed ID: 29518248
[TBL] [Abstract][Full Text] [Related]
16. LONP1 Regulates Mitochondrial Accumulations of HMGB1 and Caspase-3 in CA1 and PV Neurons Following Status Epilepticus.
Kim JE; Park H; Kim TH; Kang TC
Int J Mol Sci; 2021 Feb; 22(5):. PubMed ID: 33668863
[TBL] [Abstract][Full Text] [Related]
17. LONP1 and mtHSP70 cooperate to promote mitochondrial protein folding.
Shin CS; Meng S; Garbis SD; Moradian A; Taylor RW; Sweredoski MJ; Lomenick B; Chan DC
Nat Commun; 2021 Jan; 12(1):265. PubMed ID: 33431889
[TBL] [Abstract][Full Text] [Related]
18. GTPBP8 plays a role in mitoribosome formation in human mitochondria.
Cipullo M; Valentín Gesé G; Gopalakrishna S; Krueger A; Lobo V; Pirozhkova MA; Marks J; Páleníková P; Shiriaev D; Liu Y; Misic J; Cai Y; Nguyen MD; Abdelbagi A; Li X; Minczuk M; Hafner M; Benhalevy D; Sarshad AA; Atanassov I; Hällberg BM; Rorbach J
Nat Commun; 2024 Jul; 15(1):5664. PubMed ID: 38969660
[TBL] [Abstract][Full Text] [Related]
19. Bi-allelic mutations of LONP1 encoding the mitochondrial LonP1 protease cause pyruvate dehydrogenase deficiency and profound neurodegeneration with progressive cerebellar atrophy.
Nimmo GAM; Venkatesh S; Pandey AK; Marshall CR; Hazrati LN; Blaser S; Ahmed S; Cameron J; Singh K; Ray PN; Suzuki CK; Yoon G
Hum Mol Genet; 2019 Jan; 28(2):290-306. PubMed ID: 30304514
[TBL] [Abstract][Full Text] [Related]
20. Disuse-associated loss of the protease LONP1 in muscle impairs mitochondrial function and causes reduced skeletal muscle mass and strength.
Xu Z; Fu T; Guo Q; Zhou D; Sun W; Zhou Z; Chen X; Zhang J; Liu L; Xiao L; Yin Y; Jia Y; Pang E; Chen Y; Pan X; Fang L; Zhu MS; Fei W; Lu B; Gan Z
Nat Commun; 2022 Feb; 13(1):894. PubMed ID: 35173176
[TBL] [Abstract][Full Text] [Related]
[Next] [New Search]
