370 related articles for article (PubMed ID: 31640267)
1. Large Neutral Amino Acid Therapy Increases Tyrosine Levels in Adult Patients with Phenylketonuria: A Long-Term Study.
Burlina AP; Cazzorla C; Massa P; Polo G; Loro C; Gueraldi D; Burlina AB
Nutrients; 2019 Oct; 11(10):. PubMed ID: 31640267
[TBL] [Abstract][Full Text] [Related]
2. The Impact of a Slow-Release Large Neutral Amino Acids Supplement on Treatment Adherence in Adult Patients with Phenylketonuria.
Burlina AP; Cazzorla C; Massa P; Loro C; Gueraldi D; Burlina AB
Nutrients; 2020 Jul; 12(7):. PubMed ID: 32674279
[TBL] [Abstract][Full Text] [Related]
3. The effects of large neutral amino acid supplements in PKU: an MRS and neuropsychological study.
Schindeler S; Ghosh-Jerath S; Thompson S; Rocca A; Joy P; Kemp A; Rae C; Green K; Wilcken B; Christodoulou J
Mol Genet Metab; 2007 May; 91(1):48-54. PubMed ID: 17368065
[TBL] [Abstract][Full Text] [Related]
4. Beneficial Effects of Slow-Release Large Neutral Amino Acids after a Phenylalanine Oral Load in Patients with Phenylketonuria.
Scala I; Concolino D; Nastasi A; Esposito G; Crisci D; Sestito S; Ferraro S; Albano L; Ruoppolo M; Parenti G; Strisciuglio P
Nutrients; 2021 Nov; 13(11):. PubMed ID: 34836270
[TBL] [Abstract][Full Text] [Related]
5. Future role of large neutral amino acids in transport of phenylalanine into the brain.
Matalon R; Surendran S; Matalon KM; Tyring S; Quast M; Jinga W; Ezell E; Szucs S
Pediatrics; 2003 Dec; 112(6 Pt 2):1570-4. PubMed ID: 14654667
[TBL] [Abstract][Full Text] [Related]
6. Therapeutic brain modulation with targeted large neutral amino acid supplements in the Pah-enu2 phenylketonuria mouse model.
van Vliet D; Bruinenberg VM; Mazzola PN; van Faassen MH; de Blaauw P; Pascucci T; Puglisi-Allegra S; Kema IP; Heiner-Fokkema MR; van der Zee EA; van Spronsen FJ
Am J Clin Nutr; 2016 Nov; 104(5):1292-1300. PubMed ID: 27655443
[TBL] [Abstract][Full Text] [Related]
7. The effect of casein glycomacropeptide versus free synthetic amino acids for early treatment of phenylketonuria in a mice model.
Ahring KK; Dagnæs-Hansen F; Brüel A; Christensen M; Jensen E; Jensen TG; Johannsen M; Johansen KS; Lund AM; Madsen JG; Brøndum-Nielsen K; Pedersen M; Sørensen LK; Kjolby M; Møller LB
PLoS One; 2022; 17(1):e0261150. PubMed ID: 35015767
[TBL] [Abstract][Full Text] [Related]
8. Large Neutral Amino Acid Supplementation Exerts Its Effect through Three Synergistic Mechanisms: Proof of Principle in Phenylketonuria Mice.
van Vliet D; Bruinenberg VM; Mazzola PN; van Faassen MH; de Blaauw P; Kema IP; Heiner-Fokkema MR; van Anholt RD; van der Zee EA; van Spronsen FJ
PLoS One; 2015; 10(12):e0143833. PubMed ID: 26624009
[TBL] [Abstract][Full Text] [Related]
9. Evaluation of Tetrahydrobiopterin Therapy with Large Neutral Amino Acid Supplementation in Phenylketonuria: Effects on Potential Peripheral Biomarkers, Melatonin and Dopamine, for Brain Monoamine Neurotransmitters.
Yano S; Moseley K; Fu X; Azen C
PLoS One; 2016; 11(8):e0160892. PubMed ID: 27513937
[TBL] [Abstract][Full Text] [Related]
10. Phenylketonuria: tyrosine beyond the phenylalanine-restricted diet.
van Spronsen FJ; Smit PG; Koch R
J Inherit Metab Dis; 2001 Feb; 24(1):1-4. PubMed ID: 11286377
[TBL] [Abstract][Full Text] [Related]
11. Melatonin and dopamine as biomarkers to optimize treatment in phenylketonuria: effects of tryptophan and tyrosine supplementation.
Yano S; Moseley K; Azen C
J Pediatr; 2014 Jul; 165(1):184-189.e1. PubMed ID: 24857519
[TBL] [Abstract][Full Text] [Related]
12. The Benefit of Large Neutral Amino Acid Supplementation to a Liberalized Phenylalanine-Restricted Diet in Adult Phenylketonuria Patients: Evidence from Adult
van Vliet D; van der Goot E; van Ginkel WG; van Faassen MHJR; de Blaauw P; Kema IP; Martinez A; Heiner-Fokkema MR; van der Zee EA; van Spronsen FJ
Nutrients; 2019 Sep; 11(9):. PubMed ID: 31546852
[TBL] [Abstract][Full Text] [Related]
13. Double blind placebo control trial of large neutral amino acids in treatment of PKU: effect on blood phenylalanine.
Matalon R; Michals-Matalon K; Bhatia G; Burlina AB; Burlina AP; Braga C; Fiori L; Giovannini M; Grechanina E; Novikov P; Grady J; Tyring SK; Guttler F
J Inherit Metab Dis; 2007 Apr; 30(2):153-8. PubMed ID: 17334706
[TBL] [Abstract][Full Text] [Related]
14. Characterization of 2-(methylamino)alkanoic acid capacity to restrict blood-brain phenylalanine transport in Pah enu2 mice: preliminary findings.
Vogel KR; Arning E; Wasek BL; Bottiglieri T; Gibson KM
Mol Genet Metab; 2013; 110 Suppl(0):S71-8. PubMed ID: 23999161
[TBL] [Abstract][Full Text] [Related]
15. The increasing importance of LNAA supplementation in phenylketonuria at higher plasma phenylalanine concentrations.
van Vliet D; van der Goot E; van Ginkel WG; van Faassen HJR; de Blaauw P; Kema IP; Heiner-Fokkema MR; van der Zee EA; van Spronsen FJ
Mol Genet Metab; 2022 Jan; 135(1):27-34. PubMed ID: 34974973
[TBL] [Abstract][Full Text] [Related]
16. Large neutral amino acids in the treatment of PKU: from theory to practice.
van Spronsen FJ; de Groot MJ; Hoeksma M; Reijngoud DJ; van Rijn M
J Inherit Metab Dis; 2010 Dec; 33(6):671-6. PubMed ID: 20976625
[TBL] [Abstract][Full Text] [Related]
17. Large neutral amino acid supplementation increases melatonin synthesis in phenylketonuria: a new biomarker.
Yano S; Moseley K; Azen C
J Pediatr; 2013 May; 162(5):999-1003. PubMed ID: 23164313
[TBL] [Abstract][Full Text] [Related]
18. Tyrosine metabolism in health and disease: slow-release amino acids therapy improves tyrosine homeostasis in phenylketonuria.
Porta F; Giorda S; Ponzone A; Spada M
J Pediatr Endocrinol Metab; 2020 Dec; 33(12):1519-1523. PubMed ID: 33581706
[TBL] [Abstract][Full Text] [Related]
19. Advances in the nutritional and pharmacological management of phenylketonuria.
Ney DM; Blank RD; Hansen KE
Curr Opin Clin Nutr Metab Care; 2014 Jan; 17(1):61-8. PubMed ID: 24136088
[TBL] [Abstract][Full Text] [Related]
20. Optimising amino acid absorption: essential to improve nitrogen balance and metabolic control in phenylketonuria.
MacDonald A; Singh RH; Rocha JC; van Spronsen FJ
Nutr Res Rev; 2019 Jun; 32(1):70-78. PubMed ID: 30284526
[TBL] [Abstract][Full Text] [Related]
[Next] [New Search]
