These tools will no longer be maintained as of December 31, 2024. Archived website can be found here. PubMed4Hh GitHub repository can be found here. Contact NLM Customer Service if you have questions.
256 related articles for article (PubMed ID: 31756517)
1. Cell stress management by the mitochondrial LonP1 protease - Insights into mitigating developmental, oncogenic and cardiac stress. Venkatesh S; Suzuki CK Mitochondrion; 2020 Mar; 51():46-61. PubMed ID: 31756517 [TBL] [Abstract][Full Text] [Related]
2. LONP1 Is Required for Maturation of a Subset of Mitochondrial Proteins, and Its Loss Elicits an Integrated Stress Response. Zurita Rendón O; Shoubridge EA Mol Cell Biol; 2018 Oct; 38(20):. PubMed ID: 30061372 [TBL] [Abstract][Full Text] [Related]
3. CODAS syndrome is associated with mutations of LONP1, encoding mitochondrial AAA+ Lon protease. Strauss KA; Jinks RN; Puffenberger EG; Venkatesh S; Singh K; Cheng I; Mikita N; Thilagavathi J; Lee J; Sarafianos S; Benkert A; Koehler A; Zhu A; Trovillion V; McGlincy M; Morlet T; Deardorff M; Innes AM; Prasad C; Chudley AE; Lee IN; Suzuki CK Am J Hum Genet; 2015 Jan; 96(1):121-35. PubMed ID: 25574826 [TBL] [Abstract][Full Text] [Related]
4. Proteomic analysis demonstrates the role of the quality control protease LONP1 in mitochondrial protein aggregation. Pollecker K; Sylvester M; Voos W J Biol Chem; 2021 Oct; 297(4):101134. PubMed ID: 34461102 [TBL] [Abstract][Full Text] [Related]
5. Bi-allelic mutations of LONP1 encoding the mitochondrial LonP1 protease cause pyruvate dehydrogenase deficiency and profound neurodegeneration with progressive cerebellar atrophy. Nimmo GAM; Venkatesh S; Pandey AK; Marshall CR; Hazrati LN; Blaser S; Ahmed S; Cameron J; Singh K; Ray PN; Suzuki CK; Yoon G Hum Mol Genet; 2019 Jan; 28(2):290-306. PubMed ID: 30304514 [TBL] [Abstract][Full Text] [Related]
6. Mitochondrial LonP1 protects cardiomyocytes from ischemia/reperfusion injury in vivo. Venkatesh S; Li M; Saito T; Tong M; Rashed E; Mareedu S; Zhai P; Bárcena C; López-Otín C; Yehia G; Sadoshima J; Suzuki CK J Mol Cell Cardiol; 2019 Mar; 128():38-50. PubMed ID: 30625302 [TBL] [Abstract][Full Text] [Related]
7. Defective mitochondrial protease LonP1 can cause classical mitochondrial disease. Peter B; Waddington CL; Oláhová M; Sommerville EW; Hopton S; Pyle A; Champion M; Ohlson M; Siibak T; Chrzanowska-Lightowlers ZMA; Taylor RW; Falkenberg M; Lightowlers RN Hum Mol Genet; 2018 May; 27(10):1743-1753. PubMed ID: 29518248 [TBL] [Abstract][Full Text] [Related]
8. Structures of the human LONP1 protease reveal regulatory steps involved in protease activation. Shin M; Watson ER; Song AS; Mindrebo JT; Novick SJ; Griffin PR; Wiseman RL; Lander GC Nat Commun; 2021 May; 12(1):3239. PubMed ID: 34050165 [TBL] [Abstract][Full Text] [Related]
9. Chronic hyperglycemia impairs mitochondrial unfolded protein response and precipitates proteotoxicity in experimental diabetic neuropathy: focus on LonP1 mediated mitochondrial regulation. Kalvala AK; Yerra VG; Sherkhane B; Gundu C; Arruri V; Kumar R; Kumar A Pharmacol Rep; 2020 Dec; 72(6):1627-1644. PubMed ID: 32720218 [TBL] [Abstract][Full Text] [Related]
10. Disuse-associated loss of the protease LONP1 in muscle impairs mitochondrial function and causes reduced skeletal muscle mass and strength. Xu Z; Fu T; Guo Q; Zhou D; Sun W; Zhou Z; Chen X; Zhang J; Liu L; Xiao L; Yin Y; Jia Y; Pang E; Chen Y; Pan X; Fang L; Zhu MS; Fei W; Lu B; Gan Z Nat Commun; 2022 Feb; 13(1):894. PubMed ID: 35173176 [TBL] [Abstract][Full Text] [Related]
11. Intraneuronal β-amyloid impaired mitochondrial proteostasis through the impact on LONP1. Wang W; Ma X; Bhatta S; Shao C; Zhao F; Fujioka H; Torres S; Wu F; Zhu X Proc Natl Acad Sci U S A; 2023 Dec; 120(51):e2316823120. PubMed ID: 38091289 [TBL] [Abstract][Full Text] [Related]
12. Roles of LonP1 in Oral-Maxillofacial Developmental Defects and Tumors: A Novel Insight. Ma H; Chen W; Fan W; He H; Huang F Int J Mol Sci; 2022 Nov; 23(21):. PubMed ID: 36362158 [TBL] [Abstract][Full Text] [Related]
13. Inhibition of Lonp1 induces mitochondrial remodeling and autophagy suppression in cervical cancer cells. Wang X; Xu X; Zhao Y; Qi L; Ge H Acta Histochem; 2023 Jan; 125(1):151986. PubMed ID: 36508908 [TBL] [Abstract][Full Text] [Related]
14. ATP-Dependent Lon Protease Contributes to Helicobacter pylori-Induced Gastric Carcinogenesis. Luo B; Wang M; Hou N; Hu X; Jia G; Qin X; Zuo X; Liu Y; Luo K; Song W; Wang K; Pang M Neoplasia; 2016 Apr; 18(4):242-52. PubMed ID: 27108387 [TBL] [Abstract][Full Text] [Related]
15. Acute increases in Wright JN; Benavides GA; Johnson MS; Wani W; Ouyang X; Zou L; Collins HE; Zhang J; Darley-Usmar V; Chatham JC Am J Physiol Cell Physiol; 2019 Jun; 316(6):C862-C875. PubMed ID: 30865517 [TBL] [Abstract][Full Text] [Related]
16. Readdressing the Localization of Apolipoprotein E (APOE) in Mitochondria-Associated Endoplasmic Reticulum (ER) Membranes (MAMs): An Investigation of the Hepatic Protein-Protein Interactions of APOE with the Mitochondrial Proteins Lon Protease (LONP1), Mitochondrial Import Receptor Subunit TOM40 (TOMM40) and Voltage-Dependent Anion-Selective Channel 1 (VDAC1). Rueter J; Rimbach G; Bilke S; Tholey A; Huebbe P Int J Mol Sci; 2024 Oct; 25(19):. PubMed ID: 39408926 [TBL] [Abstract][Full Text] [Related]
17. TDP-43 induces mitochondrial damage and activates the mitochondrial unfolded protein response. Wang P; Deng J; Dong J; Liu J; Bigio EH; Mesulam M; Wang T; Sun L; Wang L; Lee AY; McGee WA; Chen X; Fushimi K; Zhu L; Wu JY PLoS Genet; 2019 May; 15(5):e1007947. PubMed ID: 31100073 [TBL] [Abstract][Full Text] [Related]
18. Mitochondrial Lon protease is a gatekeeper for proteins newly imported into the matrix. Matsushima Y; Takahashi K; Yue S; Fujiyoshi Y; Yoshioka H; Aihara M; Setoyama D; Uchiumi T; Fukuchi S; Kang D Commun Biol; 2021 Aug; 4(1):974. PubMed ID: 34400774 [TBL] [Abstract][Full Text] [Related]
19. Evidence for mitochondrial Lonp1 expression in the nucleus. Gibellini L; Borella R; De Gaetano A; Zanini G; Tartaro DL; Carnevale G; Beretti F; Losi L; De Biasi S; Nasi M; Forcato M; Cossarizza A; Pinti M Sci Rep; 2022 Jun; 12(1):10877. PubMed ID: 35760833 [TBL] [Abstract][Full Text] [Related]
20. A mitochondrial FUNDC1/HSC70 interaction organizes the proteostatic stress response at the risk of cell morbidity. Li Y; Xue Y; Xu X; Wang G; Liu Y; Wu H; Li W; Wang Y; Chen Z; Zhang W; Zhu Y; Ji W; Xu T; Liu L; Chen Q EMBO J; 2019 Feb; 38(3):. PubMed ID: 30591555 [TBL] [Abstract][Full Text] [Related] [Next] [New Search]