157 related articles for article (PubMed ID: 31778232)
1. Therapeutic potential of triheptanoin in metabolic and neurodegenerative diseases.
Wehbe Z; Tucci S
J Inherit Metab Dis; 2020 May; 43(3):385-391. PubMed ID: 31778232
[TBL] [Abstract][Full Text] [Related]
2. Triheptanoin for the treatment of brain energy deficit: A 14-year experience.
Mochel F
J Neurosci Res; 2017 Nov; 95(11):2236-2243. PubMed ID: 28688166
[TBL] [Abstract][Full Text] [Related]
3. Triheptanoin--a medium chain triglyceride with odd chain fatty acids: a new anaplerotic anticonvulsant treatment?
Borges K; Sonnewald U
Epilepsy Res; 2012 Jul; 100(3):239-44. PubMed ID: 21855298
[TBL] [Abstract][Full Text] [Related]
4. The Pharmacokinetics of Triheptanoin and Its Metabolites in Healthy Subjects and Patients With Long-Chain Fatty Acid Oxidation Disorders.
Lee SK; Gupta M; Shi J; McKeever K
Clin Pharmacol Drug Dev; 2021 Nov; 10(11):1325-1334. PubMed ID: 33789001
[TBL] [Abstract][Full Text] [Related]
5. Parenteral and enteral metabolism of anaplerotic triheptanoin in normal rats. II. Effects on lipolysis, glucose production, and liver acyl-CoA profile.
Gu L; Zhang GF; Kombu RS; Allen F; Kutz G; Brewer WU; Roe CR; Brunengraber H
Am J Physiol Endocrinol Metab; 2010 Feb; 298(2):E362-71. PubMed ID: 19903863
[TBL] [Abstract][Full Text] [Related]
6. Long-term major clinical outcomes in patients with long chain fatty acid oxidation disorders before and after transition to triheptanoin treatment--A retrospective chart review.
Vockley J; Marsden D; McCracken E; DeWard S; Barone A; Hsu K; Kakkis E
Mol Genet Metab; 2015; 116(1-2):53-60. PubMed ID: 26116311
[TBL] [Abstract][Full Text] [Related]
7. Triheptanoin treatment in patients with pediatric cardiomyopathy associated with long chain-fatty acid oxidation disorders.
Vockley J; Charrow J; Ganesh J; Eswara M; Diaz GA; McCracken E; Conway R; Enns GM; Starr J; Wang R; Abdenur JE; Sanchez-de-Toledo J; Marsden DL
Mol Genet Metab; 2016 Nov; 119(3):223-231. PubMed ID: 27590926
[TBL] [Abstract][Full Text] [Related]
8. Tutorial: Triheptanoin and Nutrition Management for Treatment of Long-Chain Fatty Acid Oxidation Disorders.
Norris MK; Scott AI; Sullivan S; Chang IJ; Lam C; Sun A; Hahn S; Thies JM; Gunnarson M; McKean KN; Merritt JL
JPEN J Parenter Enteral Nutr; 2021 Feb; 45(2):230-238. PubMed ID: 33085788
[TBL] [Abstract][Full Text] [Related]
9. Reduced severity of ischemic stroke and improvement of mitochondrial function after dietary treatment with the anaplerotic substance triheptanoin.
Schwarzkopf TM; Koch K; Klein J
Neuroscience; 2015 Aug; 300():201-9. PubMed ID: 25982559
[TBL] [Abstract][Full Text] [Related]
10. Triheptanoin Mitigates Brain ATP Depletion and Mitochondrial Dysfunction in a Mouse Model of Alzheimer's Disease.
Yuan X; Wang L; Tandon N; Sun H; Tian J; Du H; Pascual JM; Guo L
J Alzheimers Dis; 2020; 78(1):425-437. PubMed ID: 33016909
[TBL] [Abstract][Full Text] [Related]
11. Triheptanoin: long-term effects in the very long-chain acyl-CoA dehydrogenase-deficient mouse.
Tucci S; Floegel U; Beermann F; Behringer S; Spiekerkoetter U
J Lipid Res; 2017 Jan; 58(1):196-207. PubMed ID: 27884962
[TBL] [Abstract][Full Text] [Related]
12. Alternative Fuels in Epilepsy and Amyotrophic Lateral Sclerosis.
Tefera TW; Tan KN; McDonald TS; Borges K
Neurochem Res; 2017 Jun; 42(6):1610-1620. PubMed ID: 27868154
[TBL] [Abstract][Full Text] [Related]
13. Triheptanoin for the treatment of long-chain fatty acid oxidation disorders: Final results of an open-label, long-term extension study.
Vockley J; Burton BK; Berry G; Longo N; Phillips J; Sanchez-Valle A; Chapman KA; Tanpaiboon P; Grunewald S; Murphy E; Lu X; Rahman S; Ray K; Reineking B; Pisani L; Ramirez AN
J Inherit Metab Dis; 2023 Sep; 46(5):943-955. PubMed ID: 37276053
[TBL] [Abstract][Full Text] [Related]
14. Triheptanoin versus trioctanoin for long-chain fatty acid oxidation disorders: a double blinded, randomized controlled trial.
Gillingham MB; Heitner SB; Martin J; Rose S; Goldstein A; El-Gharbawy AH; Deward S; Lasarev MR; Pollaro J; DeLany JP; Burchill LJ; Goodpaster B; Shoemaker J; Matern D; Harding CO; Vockley J
J Inherit Metab Dis; 2017 Nov; 40(6):831-843. PubMed ID: 28871440
[TBL] [Abstract][Full Text] [Related]
15. Clinical outcomes in a series of 18 patients with long chain fatty acids oxidation disorders treated with triheptanoin for a median duration of 22 months.
Guffon N; Mochel F; Schiff M; De Lonlay P; Douillard C; Vianey-Saban C
Mol Genet Metab; 2021 Apr; 132(4):227-233. PubMed ID: 33610471
[TBL] [Abstract][Full Text] [Related]
16. Physiological Perspectives on the Use of Triheptanoin as Anaplerotic Therapy for Long Chain Fatty Acid Oxidation Disorders.
Sklirou E; Alodaib AN; Dobrowolski SF; Mohsen AA; Vockley J
Front Genet; 2020; 11():598760. PubMed ID: 33584796
[TBL] [Abstract][Full Text] [Related]
17. Triheptanoin alters [U-
McDonald T; Hodson MP; Bederman I; Puchowicz M; Borges K
J Cereb Blood Flow Metab; 2020 Mar; 40(3):678-691. PubMed ID: 30890077
[TBL] [Abstract][Full Text] [Related]
18. Triheptanoin for glucose transporter type I deficiency (G1D): modulation of human ictogenesis, cerebral metabolic rate, and cognitive indices by a food supplement.
Pascual JM; Liu P; Mao D; Kelly DI; Hernandez A; Sheng M; Good LB; Ma Q; Marin-Valencia I; Zhang X; Park JY; Hynan LS; Stavinoha P; Roe CR; Lu H
JAMA Neurol; 2014 Oct; 71(10):1255-65. PubMed ID: 25110966
[TBL] [Abstract][Full Text] [Related]
19. Triheptanoin reduces seizure susceptibility in a syndrome-specific mouse model of generalized epilepsy.
Kim TH; Borges K; Petrou S; Reid CA
Epilepsy Res; 2013 Jan; 103(1):101-5. PubMed ID: 23196212
[TBL] [Abstract][Full Text] [Related]
20. UX007 for the treatment of long chain-fatty acid oxidation disorders: Safety and efficacy in children and adults following 24weeks of treatment.
Vockley J; Burton B; Berry GT; Longo N; Phillips J; Sanchez-Valle A; Tanpaiboon P; Grunewald S; Murphy E; Humphrey R; Mayhew J; Bowden A; Zhang L; Cataldo J; Marsden DL; Kakkis E
Mol Genet Metab; 2017 Apr; 120(4):370-377. PubMed ID: 28189603
[TBL] [Abstract][Full Text] [Related]
[Next] [New Search]