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46. CODAS syndrome is associated with mutations of LONP1, encoding mitochondrial AAA+ Lon protease. Strauss KA; Jinks RN; Puffenberger EG; Venkatesh S; Singh K; Cheng I; Mikita N; Thilagavathi J; Lee J; Sarafianos S; Benkert A; Koehler A; Zhu A; Trovillion V; McGlincy M; Morlet T; Deardorff M; Innes AM; Prasad C; Chudley AE; Lee IN; Suzuki CK Am J Hum Genet; 2015 Jan; 96(1):121-35. PubMed ID: 25574826 [TBL] [Abstract][Full Text] [Related]
47. Substitution of PIM1 protease in mitochondria by Escherichia coli Lon protease. Teichmann U; van Dyck L; Guiard B; Fischer H; Glockshuber R; Neupert W; Langer T J Biol Chem; 1996 Apr; 271(17):10137-42. PubMed ID: 8626573 [TBL] [Abstract][Full Text] [Related]
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49. The role of Lon-mediated proteolysis in the dynamics of mitochondrial nucleic acid-protein complexes. Kunová N; Ondrovičová G; Bauer JA; Bellová J; Ambro Ľ; Martináková L; Kotrasová V; Kutejová E; Pevala V Sci Rep; 2017 Apr; 7(1):631. PubMed ID: 28377575 [TBL] [Abstract][Full Text] [Related]
50. Lon protease preferentially degrades oxidized mitochondrial aconitase by an ATP-stimulated mechanism. Bota DA; Davies KJ Nat Cell Biol; 2002 Sep; 4(9):674-80. PubMed ID: 12198491 [TBL] [Abstract][Full Text] [Related]
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58. Diphenylarsinic acid promotes degradation of glutaminase C by mitochondrial Lon protease. Kita K; Suzuki T; Ochi T J Biol Chem; 2012 May; 287(22):18163-72. PubMed ID: 22493432 [TBL] [Abstract][Full Text] [Related]
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