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4. Targeted next generation sequencing of a panel of autism-related genes identifies an EHMT1 mutation in a Kleefstra syndrome patient with autism and normal intellectual performance. Bock I; Németh K; Pentelényi K; Balicza P; Balázs A; Molnár MJ; Román V; Nagy J; Lévay G; Kobolák J; Dinnyés A Gene; 2016 Dec; 595(2):131-141. PubMed ID: 27651234 [TBL] [Abstract][Full Text] [Related]
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7. Altered neurite morphology and cholinergic function of induced pluripotent stem cell-derived neurons from a patient with Kleefstra syndrome and autism. Nagy J; Kobolák J; Berzsenyi S; Ábrahám Z; Avci HX; Bock I; Bekes Z; Hodoscsek B; Chandrasekaran A; Téglási A; Dezső P; Koványi B; Vörös ET; Fodor L; Szél T; Németh K; Balázs A; Dinnyés A; Lendvai B; Lévay G; Román V Transl Psychiatry; 2017 Jul; 7(7):e1179. PubMed ID: 28742076 [TBL] [Abstract][Full Text] [Related]
8. Comprehensive EHMT1 variants analysis broadens genotype-phenotype associations and molecular mechanisms in Kleefstra syndrome. Rots D; Bouman A; Yamada A; Levy M; Dingemans AJM; de Vries BBA; Ruiterkamp-Versteeg M; de Leeuw N; Ockeloen CW; Pfundt R; de Boer E; Kummeling J; van Bon B; van Bokhoven H; Kasri NN; Venselaar H; Alders M; Kerkhof J; McConkey H; Kuechler A; Elffers B; van Beeck Calkoen R; Hofman S; Smith A; Valenzuela MI; Srivastava S; Frazier Z; Maystadt I; Piscopo C; Merla G; Balasubramanian M; Santen GWE; Metcalfe K; Park SM; Pasquier L; Banka S; Donnai D; Weisberg D; Strobl-Wildemann G; Wagemans A; Vreeburg M; Baralle D; Foulds N; Scurr I; Brunetti-Pierri N; van Hagen JM; Bijlsma EK; Hakonen AH; Courage C; Genevieve D; Pinson L; Forzano F; Deshpande C; Kluskens ML; Welling L; Plomp AS; Vanhoutte EK; Kalsner L; Hol JA; Putoux A; Lazier J; Vasudevan P; Ames E; O'Shea J; Lederer D; Fleischer J; O'Connor M; Pauly M; Vasileiou G; Reis A; Kiraly-Borri C; Bouman A; Barnett C; Nezarati M; Borch L; Beunders G; Özcan K; Miot S; Volker-Touw CML; van Gassen KLI; Cappuccio G; Janssens K; Mor N; Shomer I; Dominissini D; Tedder ML; Muir AM; Sadikovic B; Brunner HG; Vissers LELM; Shinkai Y; Kleefstra T Am J Hum Genet; 2024 Aug; 111(8):1605-1625. PubMed ID: 39013458 [TBL] [Abstract][Full Text] [Related]
9. A Novel Kleefstra Syndrome-associated Variant That Affects the Conserved TPL Blackburn PR; Tischer A; Zimmermann MT; Kemppainen JL; Sastry S; Knight Johnson AE; Cousin MA; Boczek NJ; Oliver G; Misra VK; Gavrilova RH; Lomberk G; Auton M; Urrutia R; Klee EW J Biol Chem; 2017 Mar; 292(9):3866-3876. PubMed ID: 28057753 [TBL] [Abstract][Full Text] [Related]
10. Clinical phenotypes and molecular findings in ten Chinese patients with Kleefstra Syndrome Type 1 due to EHMT1 defects. Huang Q; Xiong H; Tao Z; Yue F; Xiao N Eur J Med Genet; 2021 Sep; 64(9):104289. PubMed ID: 34265435 [TBL] [Abstract][Full Text] [Related]
11. Biochemical validation of EHMT1 missense mutations in Kleefstra syndrome. Yamada A; Shimura C; Shinkai Y J Hum Genet; 2018 May; 63(5):555-562. PubMed ID: 29459631 [TBL] [Abstract][Full Text] [Related]
12. Transcriptomic dysregulation and autistic-like behaviors in Kmt2c haploinsufficient mice rescued by an LSD1 inhibitor. Nakamura T; Yoshihara T; Tanegashima C; Kadota M; Kobayashi Y; Honda K; Ishiwata M; Ueda J; Hara T; Nakanishi M; Takumi T; Itohara S; Kuraku S; Asano M; Kasahara T; Nakajima K; Tsuboi T; Takata A; Kato T Mol Psychiatry; 2024 Sep; 29(9):2888-2904. PubMed ID: 38528071 [TBL] [Abstract][Full Text] [Related]
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18. Disruption of an EHMT1-associated chromatin-modification module causes intellectual disability. Kleefstra T; Kramer JM; Neveling K; Willemsen MH; Koemans TS; Vissers LE; Wissink-Lindhout W; Fenckova M; van den Akker WM; Kasri NN; Nillesen WM; Prescott T; Clark RD; Devriendt K; van Reeuwijk J; de Brouwer AP; Gilissen C; Zhou H; Brunner HG; Veltman JA; Schenck A; van Bokhoven H Am J Hum Genet; 2012 Jul; 91(1):73-82. PubMed ID: 22726846 [TBL] [Abstract][Full Text] [Related]
19. Haploinsufficiency of EHMT1 improves pattern separation and increases hippocampal cell proliferation. Benevento M; Oomen CA; Horner AE; Amiri H; Jacobs T; Pauwels C; Frega M; Kleefstra T; Kopanitsa MV; Grant SG; Bussey TJ; Saksida LM; Van der Zee CE; van Bokhoven H; Glennon JC; Kasri NN Sci Rep; 2017 Jan; 7():40284. PubMed ID: 28071689 [TBL] [Abstract][Full Text] [Related]
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