These tools will no longer be maintained as of December 31, 2024. Archived website can be found here. PubMed4Hh GitHub repository can be found here. Contact NLM Customer Service if you have questions.
123 related articles for article (PubMed ID: 31943253)
41. Cyclodextrins: Assessing the Impact of Cavity Size, Occupancy, and Substitutions on Cytotoxicity and Cholesterol Homeostasis. Szente L; Singhal A; Domokos A; Song B Molecules; 2018 May; 23(5):. PubMed ID: 29783784 [TBL] [Abstract][Full Text] [Related]
42. Expanded access with intravenous hydroxypropyl-β-cyclodextrin to treat children and young adults with Niemann-Pick disease type C1: a case report analysis. Hastings C; Vieira C; Liu B; Bascon C; Gao C; Wang RY; Casey A; Hrynkow S Orphanet J Rare Dis; 2019 Oct; 14(1):228. PubMed ID: 31639011 [TBL] [Abstract][Full Text] [Related]
43. Pharmacokinetics and distribution of 2-hydroxypropyl-β-cyclodextrin following a single intrathecal dose to cats. Kao ML; Stellar S; Solon E; Lordi A; Kasica N; Swain G; Bagel JH; Gurda BL; Vite CH J Inherit Metab Dis; 2020 May; 43(3):618-634. PubMed ID: 31707730 [TBL] [Abstract][Full Text] [Related]
44. Impact of Mixed β-Cyclodextrin Ratios on Pluronic Rotaxanation Efficiency and Product Solubility. Mondjinou YA; Hyun SH; Xiong M; Collins CJ; Thong PL; Thompson DH ACS Appl Mater Interfaces; 2015 Nov; 7(43):23831-6. PubMed ID: 26502827 [TBL] [Abstract][Full Text] [Related]
45. Cholesterol in Niemann-Pick Type C disease. Bi X; Liao G Subcell Biochem; 2010; 51():319-35. PubMed ID: 20213549 [TBL] [Abstract][Full Text] [Related]
46. 2-Hydroxypropyl-gamma-cyclodextrin overcomes NPC1 deficiency by enhancing lysosome-ER association and autophagy. Singhal A; Krystofiak ES; Jerome WG; Song B Sci Rep; 2020 May; 10(1):8663. PubMed ID: 32457374 [TBL] [Abstract][Full Text] [Related]
47. Dynamics of lysosomal cholesterol in Niemann-Pick type C and normal human fibroblasts. Lange Y; Ye J; Rigney M; Steck TL J Lipid Res; 2002 Feb; 43(2):198-204. PubMed ID: 11861661 [TBL] [Abstract][Full Text] [Related]
52. Induced Pluripotent Stem Cells for Disease Modeling and Evaluation of Therapeutics for Niemann-Pick Disease Type A. Long Y; Xu M; Li R; Dai S; Beers J; Chen G; Soheilian F; Baxa U; Wang M; Marugan JJ; Muro S; Li Z; Brady R; Zheng W Stem Cells Transl Med; 2016 Dec; 5(12):1644-1655. PubMed ID: 27484861 [TBL] [Abstract][Full Text] [Related]
54. Endosomal accumulation of Toll-like receptor 4 causes constitutive secretion of cytokines and activation of signal transducers and activators of transcription in Niemann-Pick disease type C (NPC) fibroblasts: a potential basis for glial cell activation in the NPC brain. Suzuki M; Sugimoto Y; Ohsaki Y; Ueno M; Kato S; Kitamura Y; Hosokawa H; Davies JP; Ioannou YA; Vanier MT; Ohno K; Ninomiya H J Neurosci; 2007 Feb; 27(8):1879-91. PubMed ID: 17314284 [TBL] [Abstract][Full Text] [Related]
55. Use of 2 hydroxypropyl-beta-cyclodextrin therapy in two adult Niemann Pick Type C patients. García-Robles AA; Company-Albir MJ; Megías-Vericat JE; Fernández-Megía MJ; Pérez-Miralles FC; López-Briz E; Alcalá-Vicente C; Galeano I; Casanova B; Poveda JL J Neurol Sci; 2016 Jul; 366():65-67. PubMed ID: 27288778 [No Abstract] [Full Text] [Related]
56. Mutant human APP exacerbates pathology in a mouse model of NPC and its reversal by a β-cyclodextrin. Maulik M; Ghoshal B; Kim J; Wang Y; Yang J; Westaway D; Kar S Hum Mol Genet; 2012 Nov; 21(22):4857-75. PubMed ID: 22869680 [TBL] [Abstract][Full Text] [Related]
57. 2-hydroxypropyl-beta-cyclodextrin raises hearing threshold in normal cats and in cats with Niemann-Pick type C disease. Ward S; O'Donnell P; Fernandez S; Vite CH Pediatr Res; 2010 Jul; 68(1):52-6. PubMed ID: 20357695 [TBL] [Abstract][Full Text] [Related]
58. High-content screen for modifiers of Niemann-Pick type C disease in patient cells. Pugach EK; Feltes M; Kaufman RJ; Ory DS; Bang AG Hum Mol Genet; 2018 Jun; 27(12):2101-2112. PubMed ID: 29659804 [TBL] [Abstract][Full Text] [Related]
59. Characterization of cholesterol homeostasis in sphingosine-1-phosphate lyase-deficient fibroblasts reveals a Niemann-Pick disease type C-like phenotype with enhanced lysosomal Ca Vienken H; Mabrouki N; Grabau K; Claas RF; Rudowski A; Schömel N; Pfeilschifter J; Lütjohann D; van Echten-Deckert G; Meyer Zu Heringdorf D Sci Rep; 2017 Mar; 7():43575. PubMed ID: 28262793 [TBL] [Abstract][Full Text] [Related]
60. Cyclodextrin triggers MCOLN1-dependent endo-lysosome secretion in Niemann-Pick type C cells. Vacca F; Vossio S; Mercier V; Moreau D; Johnson S; Scott CC; Montoya JP; Moniatte M; Gruenberg J J Lipid Res; 2019 Apr; 60(4):832-843. PubMed ID: 30709900 [TBL] [Abstract][Full Text] [Related] [Previous] [Next] [New Search]