320 related articles for article (PubMed ID: 32005289)
21. Motor neuron disease-associated loss of nuclear TDP-43 is linked to DNA double-strand break repair defects.
Mitra J; Guerrero EN; Hegde PM; Liachko NF; Wang H; Vasquez V; Gao J; Pandey A; Taylor JP; Kraemer BC; Wu P; Boldogh I; Garruto RM; Mitra S; Rao KS; Hegde ML
Proc Natl Acad Sci U S A; 2019 Mar; 116(10):4696-4705. PubMed ID: 30770445
[TBL] [Abstract][Full Text] [Related]
22. Morpholino-mediated SOD1 reduction ameliorates an amyotrophic lateral sclerosis disease phenotype.
Nizzardo M; Simone C; Rizzo F; Ulzi G; Ramirez A; Rizzuti M; Bordoni A; Bucchia M; Gatti S; Bresolin N; Comi GP; Corti S
Sci Rep; 2016 Feb; 6():21301. PubMed ID: 26878886
[TBL] [Abstract][Full Text] [Related]
23. Co-deposition of SOD1, TDP-43 and p62 proteinopathies in ALS: evidence for multifaceted pathways underlying neurodegeneration.
Trist BG; Fifita JA; Hogan A; Grima N; Smith B; Troakes C; Vance C; Shaw C; Al-Sarraj S; Blair IP; Double KL
Acta Neuropathol Commun; 2022 Aug; 10(1):122. PubMed ID: 36008843
[TBL] [Abstract][Full Text] [Related]
24. Spy1, a unique cell cycle regulator, alters viability in ALS motor neurons and cell lines in response to mutant SOD1-induced DNA damage.
Wang XD; Zhu MW; Shan D; Wang SY; Yin X; Yang YQ; Wang TH; Zhang CT; Wang Y; Liang WW; Zhang J; Jiang HZ; Dong GT; Jiang HQ; Qi Y; Feng HL
DNA Repair (Amst); 2019 Feb; 74():51-62. PubMed ID: 30630676
[TBL] [Abstract][Full Text] [Related]
25. Distinct responses of neurons and astrocytes to TDP-43 proteinopathy in amyotrophic lateral sclerosis.
Smethurst P; Risse E; Tyzack GE; Mitchell JS; Taha DM; Chen YR; Newcombe J; Collinge J; Sidle K; Patani R
Brain; 2020 Feb; 143(2):430-440. PubMed ID: 32040555
[TBL] [Abstract][Full Text] [Related]
26. Coactivation of GSK3β and IGF-1 Attenuates Amyotrophic Lateral Sclerosis Nerve Fiber Cytopathies in SOD1 Mutant Patient-Derived Motor Neurons.
Ting HC; Yang HI; Harn HJ; Chiu IM; Su HL; Li X; Chen MF; Ho TJ; Liu CA; Tsai YJ; Chiou TW; Lin SZ; Chang CY
Cells; 2021 Oct; 10(10):. PubMed ID: 34685754
[TBL] [Abstract][Full Text] [Related]
27. Nonoxidative protein glycation is implicated in familial amyotrophic lateral sclerosis with superoxide dismutase-1 mutation.
Shibata N; Nagai R; Miyata S; Jono T; Horiuchi S; Hirano A; Kato S; Sasaki S; Asayama K; Kobayashi M
Acta Neuropathol; 2000 Sep; 100(3):275-84. PubMed ID: 10965797
[TBL] [Abstract][Full Text] [Related]
28. Comparing effects of microgravity and amyotrophic lateral sclerosis in the mouse ventral lumbar spinal cord.
Yoshikawa M; Ishikawa C; Li H; Kudo T; Shiba D; Shirakawa M; Muratani M; Takahashi S; Aizawa S; Shiga T
Mol Cell Neurosci; 2022 Jul; 121():103745. PubMed ID: 35660087
[TBL] [Abstract][Full Text] [Related]
29. Impairment of mitochondrial DNA repair enzymes against accumulation of 8-oxo-guanine in the spinal motor neurons of amyotrophic lateral sclerosis.
Kikuchi H; Furuta A; Nishioka K; Suzuki SO; Nakabeppu Y; Iwaki T
Acta Neuropathol; 2002 Apr; 103(4):408-14. PubMed ID: 11904761
[TBL] [Abstract][Full Text] [Related]
30. Single-cell transcriptomics identifies master regulators of neurodegeneration in SOD1 ALS iPSC-derived motor neurons.
Namboori SC; Thomas P; Ames R; Hawkins S; Garrett LO; Willis CRG; Rosa A; Stanton LW; Bhinge A
Stem Cell Reports; 2021 Dec; 16(12):3020-3035. PubMed ID: 34767750
[TBL] [Abstract][Full Text] [Related]
31. Neuroprotective effects of the Sigma-1 receptor (S1R) agonist PRE-084, in a mouse model of motor neuron disease not linked to SOD1 mutation.
Peviani M; Salvaneschi E; Bontempi L; Petese A; Manzo A; Rossi D; Salmona M; Collina S; Bigini P; Curti D
Neurobiol Dis; 2014 Feb; 62():218-32. PubMed ID: 24141020
[TBL] [Abstract][Full Text] [Related]
32. Characterizing the multiple roles of FGF-2 in SOD1
Kefalakes E; Böselt S; Sarikidi A; Ettcheto M; Bursch F; Naujock M; Stanslowsky N; Schmuck M; Barenys M; Wegner F; Grothe C; Petri S
J Cell Physiol; 2019 May; 234(5):7395-7410. PubMed ID: 30370540
[TBL] [Abstract][Full Text] [Related]
33. Alterations in lipid metabolism of spinal cord linked to amyotrophic lateral sclerosis.
Chaves-Filho AB; Pinto IFD; Dantas LS; Xavier AM; Inague A; Faria RL; Medeiros MHG; Glezer I; Yoshinaga MY; Miyamoto S
Sci Rep; 2019 Aug; 9(1):11642. PubMed ID: 31406145
[TBL] [Abstract][Full Text] [Related]
34. Analysis of proteome-wide degradation dynamics in ALS SOD1 iPSC-derived patient neurons reveals disrupted VCP homeostasis.
Tsioras K; Smith KC; Edassery SL; Garjani M; Li Y; Williams C; McKenna ED; Guo W; Wilen AP; Hark TJ; Marklund SL; Ostrow LW; Gilthorpe JD; Ichida JK; Kalb RG; Savas JN; Kiskinis E
Cell Rep; 2023 Oct; 42(10):113160. PubMed ID: 37776851
[TBL] [Abstract][Full Text] [Related]
35. Misfolded SOD1 inclusions in patients with mutations in
Forsberg K; Graffmo K; Pakkenberg B; Weber M; Nielsen M; Marklund S; Brännström T; Andersen PM
J Neurol Neurosurg Psychiatry; 2019 Aug; 90(8):861-869. PubMed ID: 30992335
[TBL] [Abstract][Full Text] [Related]
36. Cytoplasmic Restriction of Mutated SOD1 Impairs the DNA Repair Process in Spinal Cord Neurons.
Li J; Song M; Moh S; Kim H; Kim DH
Cells; 2019 Nov; 8(12):. PubMed ID: 31771229
[TBL] [Abstract][Full Text] [Related]
37. Protein-bound crotonaldehyde accumulates in the spinal cord of superoxide dismutase-1 mutation-associated familial amyotrophic lateral sclerosis and its transgenic mouse model.
Shibata N; Kawaguchi M; Uchida K; Kakita A; Takahashi H; Nakano R; Fujimura H; Sakoda S; Ihara Y; Nobukuni K; Takehisa Y; Kuroda S; Kokubo Y; Kuzuhara S; Honma T; Mochizuki Y; Mizutani T; Yamada S; Toi S; Sasaki S; Iwata M; Hirano A; Yamamoto T; Kato Y; Sawada T; Kobayashi M
Neuropathology; 2007 Feb; 27(1):49-61. PubMed ID: 17319283
[TBL] [Abstract][Full Text] [Related]
38. Delayed disease onset and extended survival in the SOD1G93A rat model of amyotrophic lateral sclerosis after suppression of mutant SOD1 in the motor cortex.
Thomsen GM; Gowing G; Latter J; Chen M; Vit JP; Staggenborg K; Avalos P; Alkaslasi M; Ferraiuolo L; Likhite S; Kaspar BK; Svendsen CN
J Neurosci; 2014 Nov; 34(47):15587-600. PubMed ID: 25411487
[TBL] [Abstract][Full Text] [Related]
39. Overexpression of metallothionein-I, a copper-regulating protein, attenuates intracellular copper dyshomeostasis and extends lifespan in a mouse model of amyotrophic lateral sclerosis caused by mutant superoxide dismutase-1.
Tokuda E; Okawa E; Watanabe S; Ono S
Hum Mol Genet; 2014 Mar; 23(5):1271-85. PubMed ID: 24163136
[TBL] [Abstract][Full Text] [Related]
40. p53 is abnormally elevated and active in the CNS of patients with amyotrophic lateral sclerosis.
Martin LJ
Neurobiol Dis; 2000 Dec; 7(6 Pt B):613-22. PubMed ID: 11114260
[TBL] [Abstract][Full Text] [Related]
[Previous] [Next] [New Search]
