166 related articles for article (PubMed ID: 32157564)
1. Low Level of Expression of C-Terminally Truncated Human FUS Causes Extensive Changes in the Spinal Cord Transcriptome of Asymptomatic Transgenic Mice.
Lysikova EA; Funikov S; Rezvykh AP; Chaprov KD; Kukharsky MS; Ustyugov A; Deykin AV; Flyamer IM; Boyle S; Bachurin SO; Ninkina N; Buchman VL
Neurochem Res; 2020 May; 45(5):1168-1179. PubMed ID: 32157564
[TBL] [Abstract][Full Text] [Related]
2. Fused in sarcoma (FUS) protein lacking nuclear localization signal (NLS) and major RNA binding motifs triggers proteinopathy and severe motor phenotype in transgenic mice.
Shelkovnikova TA; Peters OM; Deykin AV; Connor-Robson N; Robinson H; Ustyugov AA; Bachurin SO; Ermolkevich TG; Goldman IL; Sadchikova ER; Kovrazhkina EA; Skvortsova VI; Ling SC; Da Cruz S; Parone PA; Buchman VL; Ninkina NN
J Biol Chem; 2013 Aug; 288(35):25266-25274. PubMed ID: 23867462
[TBL] [Abstract][Full Text] [Related]
3. FUS(1-359) transgenic mice as a model of ALS: pathophysiological and molecular aspects of the proteinopathy.
Funikov SY; Rezvykh AP; Mazin PV; Morozov AV; Maltsev AV; Chicheva MM; Vikhareva EA; Evgen'ev MB; Ustyugov AA
Neurogenetics; 2018 Aug; 19(3):189-204. PubMed ID: 29982879
[TBL] [Abstract][Full Text] [Related]
4. [A mice model of amyotrophic lateral sclerosis expressing mutant human FUS protein].
Deĭkin AV; Kovrazhkina EA; Ovchinnikov RK; Bronovitskiĭ EV; Razinskaia OD; Smirnov AP; Ermolkevich TG; Eliakov AB; Popov AN; Fedorov EN; Lytkina OA; Kukharskiĭ MS; Tarasova TV; Shelkovnikova TA; Ustiugov AA; Ninkina NN; Gol'dman IL; Sadchikova ER; Bachurin SO; Skvortsova VI
Zh Nevrol Psikhiatr Im S S Korsakova; 2014; 114(8):62-9. PubMed ID: 25345633
[TBL] [Abstract][Full Text] [Related]
5. A Regulatory Circuitry Between Gria2, miR-409, and miR-495 Is Affected by ALS FUS Mutation in ESC-Derived Motor Neurons.
Capauto D; Colantoni A; Lu L; Santini T; Peruzzi G; Biscarini S; Morlando M; Shneider NA; Caffarelli E; Laneve P; Bozzoni I
Mol Neurobiol; 2018 Oct; 55(10):7635-7651. PubMed ID: 29430619
[TBL] [Abstract][Full Text] [Related]
6. Wild-Type and Mutant FUS Expression Reduce Proliferation and Neuronal Differentiation Properties of Neural Stem Progenitor Cells.
Stronati E; Biagioni S; Fiore M; Giorgi M; Poiana G; Toselli C; Cacci E
Int J Mol Sci; 2021 Jul; 22(14):. PubMed ID: 34299185
[TBL] [Abstract][Full Text] [Related]
7. Human TDP-43 and FUS selectively affect motor neuron maturation and survival in a murine cell model of ALS by non-cell-autonomous mechanisms.
Wächter N; Storch A; Hermann A
Amyotroph Lateral Scler Frontotemporal Degener; 2015; 16(7-8):431-41. PubMed ID: 26174443
[TBL] [Abstract][Full Text] [Related]
8. Changes in the Expression of FUS/TLS in Spinal Cords of SOD1 G93A Transgenic Mice and Correlation with Motor-Neuron Degeneration.
Li J; Lu Y; Liang H; Tang C; Zhu L; Zhang J; Xu R
Int J Biol Sci; 2016; 12(10):1181-1190. PubMed ID: 27766033
[TBL] [Abstract][Full Text] [Related]
9. Frameshift peptides alter the properties of truncated FUS proteins in ALS-FUS.
An H; Rabesahala de Meritens C; Buchman VL; Shelkovnikova TA
Mol Brain; 2020 May; 13(1):77. PubMed ID: 32404191
[TBL] [Abstract][Full Text] [Related]
10. Astrocytes expressing ALS-linked mutant FUS induce motor neuron death through release of tumor necrosis factor-alpha.
Kia A; McAvoy K; Krishnamurthy K; Trotti D; Pasinelli P
Glia; 2018 May; 66(5):1016-1033. PubMed ID: 29380416
[TBL] [Abstract][Full Text] [Related]
11. ALS-associated mutant FUS induces selective motor neuron degeneration through toxic gain of function.
Sharma A; Lyashchenko AK; Lu L; Nasrabady SE; Elmaleh M; Mendelsohn M; Nemes A; Tapia JC; Mentis GZ; Shneider NA
Nat Commun; 2016 Feb; 7():10465. PubMed ID: 26842965
[TBL] [Abstract][Full Text] [Related]
12. Mutations in the FUS/TLS gene on chromosome 16 cause familial amyotrophic lateral sclerosis.
Kwiatkowski TJ; Bosco DA; Leclerc AL; Tamrazian E; Vanderburg CR; Russ C; Davis A; Gilchrist J; Kasarskis EJ; Munsat T; Valdmanis P; Rouleau GA; Hosler BA; Cortelli P; de Jong PJ; Yoshinaga Y; Haines JL; Pericak-Vance MA; Yan J; Ticozzi N; Siddique T; McKenna-Yasek D; Sapp PC; Horvitz HR; Landers JE; Brown RH
Science; 2009 Feb; 323(5918):1205-8. PubMed ID: 19251627
[TBL] [Abstract][Full Text] [Related]
13. Humanized mutant FUS drives progressive motor neuron degeneration without aggregation in 'FUSDelta14' knockin mice.
Devoy A; Kalmar B; Stewart M; Park H; Burke B; Noy SJ; Redhead Y; Humphrey J; Lo K; Jaeger J; Mejia Maza A; Sivakumar P; Bertolin C; Soraru G; Plagnol V; Greensmith L; Acevedo Arozena A; Isaacs AM; Davies B; Fratta P; Fisher EMC
Brain; 2017 Nov; 140(11):2797-2805. PubMed ID: 29053787
[TBL] [Abstract][Full Text] [Related]
14. Ataxin-2 interacts with FUS and intermediate-length polyglutamine expansions enhance FUS-related pathology in amyotrophic lateral sclerosis.
Farg MA; Soo KY; Warraich ST; Sundaramoorthy V; Blair IP; Atkin JD
Hum Mol Genet; 2013 Feb; 22(4):717-28. PubMed ID: 23172909
[TBL] [Abstract][Full Text] [Related]
15. Stepwise acquirement of hallmark neuropathology in FUS-ALS iPSC models depends on mutation type and neuronal aging.
Japtok J; Lojewski X; Naumann M; Klingenstein M; Reinhardt P; Sterneckert J; Putz S; Demestre M; Boeckers TM; Ludolph AC; Liebau S; Storch A; Hermann A
Neurobiol Dis; 2015 Oct; 82():420-429. PubMed ID: 26253605
[TBL] [Abstract][Full Text] [Related]
16. ALS-associated mutation FUS-R521C causes DNA damage and RNA splicing defects.
Qiu H; Lee S; Shang Y; Wang WY; Au KF; Kamiya S; Barmada SJ; Finkbeiner S; Lui H; Carlton CE; Tang AA; Oldham MC; Wang H; Shorter J; Filiano AJ; Roberson ED; Tourtellotte WG; Chen B; Tsai LH; Huang EJ
J Clin Invest; 2014 Mar; 124(3):981-99. PubMed ID: 24509083
[TBL] [Abstract][Full Text] [Related]
17. A bioisostere of Dimebon/Latrepirdine delays the onset and slows the progression of pathology in FUS transgenic mice.
Chaprov K; Rezvykh A; Funikov S; Ivanova TA; Lysikova EA; Deykin AV; Kukharsky MS; Yu Aksinenko A; Bachurin SO; Ninkina N; Buchman VL
CNS Neurosci Ther; 2021 Jul; 27(7):765-775. PubMed ID: 33754495
[TBL] [Abstract][Full Text] [Related]
18. Arginine methylation by PRMT1 regulates nuclear-cytoplasmic localization and toxicity of FUS/TLS harbouring ALS-linked mutations.
Tradewell ML; Yu Z; Tibshirani M; Boulanger MC; Durham HD; Richard S
Hum Mol Genet; 2012 Jan; 21(1):136-49. PubMed ID: 21965298
[TBL] [Abstract][Full Text] [Related]
19. Novel FUS deletion in a patient with juvenile amyotrophic lateral sclerosis.
Belzil VV; Langlais JS; Daoud H; Dion PA; Brais B; Rouleau GA
Arch Neurol; 2012 May; 69(5):653-6. PubMed ID: 22248478
[TBL] [Abstract][Full Text] [Related]
20. Cytoplasmic sequestration of FUS/TLS associated with ALS alters histone marks through loss of nuclear protein arginine methyltransferase 1.
Tibshirani M; Tradewell ML; Mattina KR; Minotti S; Yang W; Zhou H; Strong MJ; Hayward LJ; Durham HD
Hum Mol Genet; 2015 Feb; 24(3):773-86. PubMed ID: 25274782
[TBL] [Abstract][Full Text] [Related]
[Next] [New Search]
