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5. Novel dominant-negative NR2F1 frameshift mutation and a phenotypic expansion of the Bosch-Boonstra-Schaaf optic atrophy syndrome. Walsh S; Gösswein SS; Rump A; von der Hagen M; Hackmann K; Schröck E; Di Donato N; Kahlert AK Eur J Med Genet; 2020 Oct; 63(10):104019. PubMed ID: 32712214 [TBL] [Abstract][Full Text] [Related]
6. Commentary on "Bosch-Boonstra-Schaaf Optic Atrophy Syndrome Presenting as New-Onset Psychosis in a 32-Year-Old Man: A Case Report and Literature Review". Kahn DA J Psychiatr Pract; 2020 Jan; 26(1):58-62. PubMed ID: 31913972 [TBL] [Abstract][Full Text] [Related]
7. Two siblings with Bosch-Boonstra-Schaaf optic atrophy syndrome due to parental gonadal mosaicism. van Renterghem V; Vilain C; Devriendt K; Casteels I; Smits G; Soblet J; Balikova I Eur J Med Genet; 2023 Apr; 66(4):104729. PubMed ID: 36775012 [TBL] [Abstract][Full Text] [Related]
8. A severe case of Bosch-Boonstra-Schaaf optic atrophy syndrome with a novel description of coloboma and septo-optic dysplasia, owing to a start codon variant in the NR2F1 gene. Gazdagh G; Mawby R; Self JE; Baralle D; Am J Med Genet A; 2022 Mar; 188(3):900-906. PubMed ID: 34787370 [TBL] [Abstract][Full Text] [Related]
9. Bosch-Boonstra-Schaaf Optic Atrophy Syndrome Presenting as New-Onset Psychosis in a 32-Year-Old Man: A Case Report and Literature Review. Hobbs MM; Wolters WC; Rayapati AO J Psychiatr Pract; 2020 Jan; 26(1):58-62. PubMed ID: 31913971 [TBL] [Abstract][Full Text] [Related]
10. Targeted panel sequencing identifies a novel Park SE; Lee JS; Lee ST; Kim HY; Han SH; Han J Ophthalmic Genet; 2019 Aug; 40(4):359-361. PubMed ID: 31393201 [No Abstract] [Full Text] [Related]
11. Phenotypic expansion of Bosch-Boonstra-Schaaf optic atrophy syndrome and further evidence for genotype-phenotype correlations. Rech ME; McCarthy JM; Chen CA; Edmond JC; Shah VS; Bosch DGM; Berry GT; Williams L; Madan-Khetarpal S; Niyazov D; Shaw-Smith C; Kovar EM; Lupo PJ; Schaaf CP Am J Med Genet A; 2020 Jun; 182(6):1426-1437. PubMed ID: 32275123 [TBL] [Abstract][Full Text] [Related]
12. ALG6-CDG: a recognizable phenotype with epilepsy, proximal muscle weakness, ataxia and behavioral and limb anomalies. Morava E; Tiemes V; Thiel C; Seta N; de Lonlay P; de Klerk H; Mulder M; Rubio-Gozalbo E; Visser G; van Hasselt P; Horovitz DDG; de Souza CFM; Schwartz IVD; Green A; Al-Owain M; Uziel G; Sigaudy S; Chabrol B; van Spronsen FJ; Steinert M; Komini E; Wurm D; Bevot A; Ayadi A; Huijben K; Dercksen M; Witters P; Jaeken J; Matthijs G; Lefeber DJ; Wevers RA J Inherit Metab Dis; 2016 Sep; 39(5):713-723. PubMed ID: 27287710 [TBL] [Abstract][Full Text] [Related]
13. NR2F1 database: 112 variants and 84 patients support refining the clinical synopsis of Bosch-Boonstra-Schaaf optic atrophy syndrome. Billiet B; Amati-Bonneau P; Desquiret-Dumas V; Guehlouz K; Milea D; Gohier P; Lenaers G; Mirebeau-Prunier D; den Dunnen JT; Reynier P; Ferré M Hum Mutat; 2022 Feb; 43(2):128-142. PubMed ID: 34837429 [TBL] [Abstract][Full Text] [Related]
14. The expanding clinical phenotype of Bosch-Boonstra-Schaaf optic atrophy syndrome: 20 new cases and possible genotype-phenotype correlations. Chen CA; Bosch DG; Cho MT; Rosenfeld JA; Shinawi M; Lewis RA; Mann J; Jayakar P; Payne K; Walsh L; Moss T; Schreiber A; Schoonveld C; Monaghan KG; Elmslie F; Douglas G; Boonstra FN; Millan F; Cremers FP; McKnight D; Richard G; Juusola J; Kendall F; Ramsey K; Anyane-Yeboa K; Malkin E; Chung WK; Niyazov D; Pascual JM; Walkiewicz M; Veluchamy V; Li C; Hisama FM; de Vries BB; Schaaf C Genet Med; 2016 Nov; 18(11):1143-1150. PubMed ID: 26986877 [TBL] [Abstract][Full Text] [Related]
15. Mitochondrial involvement in a Bosch-Boonstra-Schaaf optic atrophy syndrome patient with a novel de novo NR2F1 gene mutation. Martín-Hernández E; Rodríguez-García ME; Chen CA; Cotrina-Vinagre FJ; Carnicero-Rodríguez P; Bellusci M; Schaaf CP; Martínez-Azorín F J Hum Genet; 2018 Apr; 63(4):525-528. PubMed ID: 29410510 [TBL] [Abstract][Full Text] [Related]
16. Bosch-Boonstra-Schaaf optic atrophy syndrome mimicking septo-optic dysplasia in a 10-year-old child. Kingrey B; Phornphutkul C; Chen W J AAPOS; 2021 Oct; 25(5):314-316. PubMed ID: 34425235 [TBL] [Abstract][Full Text] [Related]
17. A fetus with Bosch-Boonstra-Schaaf optic atrophy syndrome characterized by bilateral ventricle widening: A case report and related literature review. Sun Y; Guo L; Sha J; Tao H; Wang X; Liu Y; Zhai J; Wu J; Zhao Y Medicine (Baltimore); 2022 Oct; 101(40):e30558. PubMed ID: 36221391 [TBL] [Abstract][Full Text] [Related]
18. A novel mutation and first report of dilated cardiomyopathy in ALG6-CDG (CDG-Ic): a case report. Al-Owain M; Mohamed S; Kaya N; Zagal A; Matthijs G; Jaeken J Orphanet J Rare Dis; 2010 Apr; 5():7. PubMed ID: 20398363 [TBL] [Abstract][Full Text] [Related]
19. ALG12-CDG: An unusual patient without intellectual disability and facial dysmorphism, and with a novel variant. de la Morena-Barrio ME; Sabater M; de la Morena-Barrio B; Ruhaak RL; Miñano A; Padilla J; Toderici M; Roldán V; Gimeno JR; Vicente V; Corral J Mol Genet Genomic Med; 2020 Aug; 8(8):e1304. PubMed ID: 32530140 [TBL] [Abstract][Full Text] [Related]
20. Pathophysiological Heterogeneity of the BBSOA Neurodevelopmental Syndrome. Bertacchi M; Tocco C; Schaaf CP; Studer M Cells; 2022 Apr; 11(8):. PubMed ID: 35455940 [TBL] [Abstract][Full Text] [Related] [Next] [New Search]