497 related articles for article (PubMed ID: 32639008)
1. Arginine-rich dipeptide-repeat proteins as phase disruptors in C9-ALS/FTD.
Odeh HM; Shorter J
Emerg Top Life Sci; 2020 Dec; 4(3):293-305. PubMed ID: 32639008
[TBL] [Abstract][Full Text] [Related]
2. Therapeutic reduction of GGGGCC repeat RNA levels by hnRNPA3 suppresses neurodegeneration in Drosophila models of C9orf72-linked ALS/FTD.
Taminato T; Takeuchi T; Ueyama M; Mori K; Ikeda M; Mochizuki H; Nagai Y
Hum Mol Genet; 2023 May; 32(10):1673-1682. PubMed ID: 36611007
[TBL] [Abstract][Full Text] [Related]
3. Modelling C9ORF72 hexanucleotide repeat expansion in amyotrophic lateral sclerosis and frontotemporal dementia.
Stepto A; Gallo JM; Shaw CE; Hirth F
Acta Neuropathol; 2014 Mar; 127(3):377-89. PubMed ID: 24366528
[TBL] [Abstract][Full Text] [Related]
4. FUS regulates RAN translation through modulating the G-quadruplex structure of GGGGCC repeat RNA in
Fujino Y; Ueyama M; Ishiguro T; Ozawa D; Ito H; Sugiki T; Murata A; Ishiguro A; Gendron T; Mori K; Tokuda E; Taminato T; Konno T; Koyama A; Kawabe Y; Takeuchi T; Furukawa Y; Fujiwara T; Ikeda M; Mizuno T; Mochizuki H; Mizusawa H; Wada K; Ishikawa K; Onodera O; Nakatani K; Petrucelli L; Taguchi H; Nagai Y
Elife; 2023 Jul; 12():. PubMed ID: 37461319
[TBL] [Abstract][Full Text] [Related]
5. Chimeric Peptide Species Contribute to Divergent Dipeptide Repeat Pathology in c9ALS/FTD and SCA36.
McEachin ZT; Gendron TF; Raj N; García-Murias M; Banerjee A; Purcell RH; Ward PJ; Todd TW; Merritt-Garza ME; Jansen-West K; Hales CM; García-Sobrino T; Quintáns B; Holler CJ; Taylor G; San Millán B; Teijeira S; Yamashita T; Ohkubo R; Boulis NM; Xu C; Wen Z; Streichenberger N; ; Fogel BL; Kukar T; Abe K; Dickson DW; Arias M; Glass JD; Jiang J; Tansey MG; Sobrido MJ; Petrucelli L; Rossoll W; Bassell GJ
Neuron; 2020 Jul; 107(2):292-305.e6. PubMed ID: 32375063
[TBL] [Abstract][Full Text] [Related]
6. C9orf72 ALS-FTD: recent evidence for dysregulation of the autophagy-lysosome pathway at multiple levels.
Beckers J; Tharkeshwar AK; Van Damme P
Autophagy; 2021 Nov; 17(11):3306-3322. PubMed ID: 33632058
[TBL] [Abstract][Full Text] [Related]
7. The carboxyl termini of RAN translated GGGGCC nucleotide repeat expansions modulate toxicity in models of ALS/FTD.
He F; Flores BN; Krans A; Frazer M; Natla S; Niraula S; Adefioye O; Barmada SJ; Todd PK
Acta Neuropathol Commun; 2020 Aug; 8(1):122. PubMed ID: 32753055
[TBL] [Abstract][Full Text] [Related]
8. Inflammasome-Mediated Neuronal-Microglial Crosstalk: a Therapeutic Substrate for the Familial C9orf72 Variant of Frontotemporal Dementia/Amyotrophic Lateral Sclerosis.
Trageser KJ; Yang EJ; Smith C; Iban-Arias R; Oguchi T; Sebastian-Valverde M; Iqbal UH; Wu H; Estill M; Al Rahim M; Raval U; Herman FJ; Zhang YJ; Petrucelli L; Pasinetti GM
Mol Neurobiol; 2023 Jul; 60(7):4004-4016. PubMed ID: 37010807
[TBL] [Abstract][Full Text] [Related]
9. Senataxin helicase, the causal gene defect in ALS4, is a significant modifier of C9orf72 ALS G4C2 and arginine-containing dipeptide repeat toxicity.
Bennett CL; Dastidar S; Arnold FJ; McKinstry SU; Stockford C; Freibaum BD; Sopher BL; Wu M; Seidner G; Joiner W; Taylor JP; West RJH; La Spada AR
Acta Neuropathol Commun; 2023 Oct; 11(1):164. PubMed ID: 37845749
[TBL] [Abstract][Full Text] [Related]
10. C9orf72 Dipeptide Repeats Cause Selective Neurodegeneration and Cell-Autonomous Excitotoxicity in
Xu W; Xu J
J Neurosci; 2018 Aug; 38(35):7741-7752. PubMed ID: 30037833
[TBL] [Abstract][Full Text] [Related]
11. C9orf72-associated dipeptide protein repeats form A11-positive oligomers in amyotrophic lateral sclerosis and frontotemporal dementia.
Bhatt N; Puangmalai N; Sengupta U; Jerez C; Kidd M; Gandhi S; Kayed R
J Biol Chem; 2024 Feb; 300(2):105628. PubMed ID: 38295729
[TBL] [Abstract][Full Text] [Related]
12. Dipeptide repeat proteins inhibit homology-directed DNA double strand break repair in C9ORF72 ALS/FTD.
Andrade NS; Ramic M; Esanov R; Liu W; Rybin MJ; Gaidosh G; Abdallah A; Del'Olio S; Huff TC; Chee NT; Anatha S; Gendron TF; Wahlestedt C; Zhang Y; Benatar M; Mueller C; Zeier Z
Mol Neurodegener; 2020 Feb; 15(1):13. PubMed ID: 32093728
[TBL] [Abstract][Full Text] [Related]
13. DDX3X overexpression decreases dipeptide repeat proteins in a mouse model of C9ORF72-ALS/FTD.
Fu X; Zhang Z; Hayes LR; Wright N; Asbury J; Li S; Ye Y; Sun S
Exp Neurol; 2024 Jun; 376():114768. PubMed ID: 38556190
[TBL] [Abstract][Full Text] [Related]
14. C9orf72 arginine-rich dipeptide proteins interact with ribosomal proteins in vivo to induce a toxic translational arrest that is rescued by eIF1A.
Moens TG; Niccoli T; Wilson KM; Atilano ML; Birsa N; Gittings LM; Holbling BV; Dyson MC; Thoeng A; Neeves J; Glaria I; Yu L; Bussmann J; Storkebaum E; Pardo M; Choudhary JS; Fratta P; Partridge L; Isaacs AM
Acta Neuropathol; 2019 Mar; 137(3):487-500. PubMed ID: 30604225
[TBL] [Abstract][Full Text] [Related]
15. Sense-encoded poly-GR dipeptide repeat proteins correlate to neurodegeneration and uniquely co-localize with TDP-43 in dendrites of repeat-expanded C9orf72 amyotrophic lateral sclerosis.
Saberi S; Stauffer JE; Jiang J; Garcia SD; Taylor AE; Schulte D; Ohkubo T; Schloffman CL; Maldonado M; Baughn M; Rodriguez MJ; Pizzo D; Cleveland D; Ravits J
Acta Neuropathol; 2018 Mar; 135(3):459-474. PubMed ID: 29196813
[TBL] [Abstract][Full Text] [Related]
16. Molecular Mechanisms of Neurodegeneration Related to
Babić Leko M; Župunski V; Kirincich J; Smilović D; Hortobágyi T; Hof PR; Šimić G
Behav Neurol; 2019; 2019():2909168. PubMed ID: 30774737
[TBL] [Abstract][Full Text] [Related]
17. C9orf72 Dipeptide Repeats Impair the Assembly, Dynamics, and Function of Membrane-Less Organelles.
Lee KH; Zhang P; Kim HJ; Mitrea DM; Sarkar M; Freibaum BD; Cika J; Coughlin M; Messing J; Molliex A; Maxwell BA; Kim NC; Temirov J; Moore J; Kolaitis RM; Shaw TI; Bai B; Peng J; Kriwacki RW; Taylor JP
Cell; 2016 Oct; 167(3):774-788.e17. PubMed ID: 27768896
[TBL] [Abstract][Full Text] [Related]
18. Emerging Perspectives on Dipeptide Repeat Proteins in C9ORF72 ALS/FTD.
Schmitz A; Pinheiro Marques J; Oertig I; Maharjan N; Saxena S
Front Cell Neurosci; 2021; 15():637548. PubMed ID: 33679328
[TBL] [Abstract][Full Text] [Related]
19. Proline-arginine poly-dipeptide encoded by the C9orf72 repeat expansion inhibits adenosine deaminase acting on RNA.
Suzuki H; Matsuoka M
J Neurochem; 2021 Aug; 158(3):753-765. PubMed ID: 34081786
[TBL] [Abstract][Full Text] [Related]
20. Poly(ADP-ribose) promotes toxicity of
Gao J; Mewborne QT; Girdhar A; Sheth U; Coyne AN; Punathil R; Kang BG; Dasovich M; Veire A; DeJesus Hernandez M; Liu S; Shi Z; Dafinca R; Fouquerel E; Talbot K; Kam TI; Zhang YJ; Dickson D; Petrucelli L; van Blitterswijk M; Guo L; Dawson TM; Dawson VL; Leung AKL; Lloyd TE; Gendron TF; Rothstein JD; Zhang K
Sci Transl Med; 2022 Sep; 14(662):eabq3215. PubMed ID: 36103513
[TBL] [Abstract][Full Text] [Related]
[Next] [New Search]
