These tools will no longer be maintained as of December 31, 2024. Archived website can be found here. PubMed4Hh GitHub repository can be found here. Contact NLM Customer Service if you have questions.
89 related articles for article (PubMed ID: 32707090)
1. Relationship between activity and stability: Design and characterization of stable variants of human frataxin. Castro IH; Bringas M; Doni D; Noguera ME; Capece L; Aran M; Blaustein M; Costantini P; Santos J Arch Biochem Biophys; 2020 Sep; 691():108491. PubMed ID: 32707090 [TBL] [Abstract][Full Text] [Related]
2. Structure-function analysis of Friedreich's ataxia mutants reveals determinants of frataxin binding and activation of the Fe-S assembly complex. Bridwell-Rabb J; Winn AM; Barondeau DP Biochemistry; 2011 Aug; 50(33):7265-74. PubMed ID: 21776984 [TBL] [Abstract][Full Text] [Related]
3. The alteration of the C-terminal region of human frataxin distorts its structural dynamics and function. Faraj SE; Roman EA; Aran M; Gallo M; Santos J FEBS J; 2014 Aug; 281(15):3397-419. PubMed ID: 24920569 [TBL] [Abstract][Full Text] [Related]
4. A Highly Conserved Iron-Sulfur Cluster Assembly Machinery between Humans and Amoeba Olmos J; Pignataro MF; Benítez Dos Santos AB; Bringas M; Klinke S; Kamenetzky L; Velazquez F; Santos J Int J Mol Sci; 2020 Sep; 21(18):. PubMed ID: 32957566 [TBL] [Abstract][Full Text] [Related]
5. Insights on the conformational dynamics of human frataxin through modifications of loop-1. Noguera ME; Aran M; Smal C; Vazquez DS; Herrera MG; Roman EA; Alaimo N; Gallo M; Santos J Arch Biochem Biophys; 2017 Dec; 636():123-137. PubMed ID: 29097312 [TBL] [Abstract][Full Text] [Related]
6. Conformational stability, dynamics and function of human frataxin: Tryptophan side chain interplay. Espeche LD; Sewell KE; Castro IH; Capece L; Pignataro MF; Dain L; Santos J Arch Biochem Biophys; 2022 Jan; 715():109086. PubMed ID: 34801473 [TBL] [Abstract][Full Text] [Related]
9. Mechanism of frataxin "bypass" in human iron-sulfur cluster biosynthesis with implications for Friedreich's ataxia. Das D; Patra S; Bridwell-Rabb J; Barondeau DP J Biol Chem; 2019 Jun; 294(23):9276-9284. PubMed ID: 30975898 [TBL] [Abstract][Full Text] [Related]
10. Mechanism of activation of the human cysteine desulfurase complex by frataxin. Patra S; Barondeau DP Proc Natl Acad Sci U S A; 2019 Sep; 116(39):19421-19430. PubMed ID: 31511419 [TBL] [Abstract][Full Text] [Related]
11. Selection of synthetic proteins to modulate the human frataxin function. Pignataro MF; Herrera MG; Fernández NB; Aran M; Gentili HG; Battaglini F; Santos J Biotechnol Bioeng; 2023 Feb; 120(2):409-425. PubMed ID: 36225115 [TBL] [Abstract][Full Text] [Related]
13. Characterization of human frataxin missense variants in cancer tissues. Petrosino M; Pasquo A; Novak L; Toto A; Gianni S; Mantuano E; Veneziano L; Minicozzi V; Pastore A; Puglisi R; Capriotti E; Chiaraluce R; Consalvi V Hum Mutat; 2019 Sep; 40(9):1400-1413. PubMed ID: 31074541 [TBL] [Abstract][Full Text] [Related]
14. Direct Cysteine Desulfurase Activity Determination by NMR and the Study of the Functional Role of Key Structural Elements of Human NFS1. Sewell KE; Gola GF; Pignataro MF; Herrera MG; Noguera ME; Olmos J; Ramírez JA; Capece L; Aran M; Santos J ACS Chem Biol; 2023 Jul; 18(7):1534-1547. PubMed ID: 37410592 [TBL] [Abstract][Full Text] [Related]
15. ISCU(M108I) and ISCU(D39V) Differ from Wild-Type ISCU in Their Failure To Form Cysteine Desulfurase Complexes Containing Both Frataxin and Ferredoxin. Cai K; Frederick RO; Tonelli M; Markley JL Biochemistry; 2018 Mar; 57(9):1491-1500. PubMed ID: 29406711 [TBL] [Abstract][Full Text] [Related]
16. Frataxin mRNA isoforms in FRDA patients and normal subjects: effect of tocotrienol supplementation. Abruzzo PM; Marini M; Bolotta A; Malisardi G; Manfredini S; Ghezzo A; Pini A; Tasco G; Casadio R Biomed Res Int; 2013; 2013():276808. PubMed ID: 24175286 [TBL] [Abstract][Full Text] [Related]
17. Probing the kinetic stabilities of Friedreich's ataxia clinical variants using a solid phase GroEL chaperonin capture platform. Correia AR; Naik S; Fisher MT; Gomes CM Biomolecules; 2014 Oct; 4(4):956-79. PubMed ID: 25333765 [TBL] [Abstract][Full Text] [Related]
18. Zinc(II) binding on human wild-type ISCU and Met140 variants modulates NFS1 desulfurase activity. Fox NG; Martelli A; Nabhan JF; Janz J; Borkowska O; Bulawa C; Yue WW Biochimie; 2018 Sep; 152():211-218. PubMed ID: 30031876 [TBL] [Abstract][Full Text] [Related]
19. Human frataxin maintains mitochondrial iron homeostasis in Saccharomyces cerevisiae. Cavadini P; Gellera C; Patel PI; Isaya G Hum Mol Genet; 2000 Oct; 9(17):2523-30. PubMed ID: 11030757 [TBL] [Abstract][Full Text] [Related]
20. Mitochondrial frataxin interacts with ISD11 of the NFS1/ISCU complex and multiple mitochondrial chaperones. Shan Y; Napoli E; Cortopassi G Hum Mol Genet; 2007 Apr; 16(8):929-41. PubMed ID: 17331979 [TBL] [Abstract][Full Text] [Related] [Next] [New Search]